Pathophysiology of Lung Disease and Wound Repair in Cystic Fibrosis
Cystic fibrosis (CF) is an autosomal recessive, life-threatening condition affecting many organs and tissues, the lung disease being the chief cause of morbidity and mortality. Mutations affecting the <i>CF Transmembrane Conductance Regulator</i> (<i>CFTR</i>) gene determine...
Principais autores: | Massimo Conese, Sante Di Gioia |
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Formato: | Artigo |
Idioma: | English |
Publicado em: |
MDPI AG
2021-03-01
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coleção: | Pathophysiology |
Assuntos: | |
Acesso em linha: | https://www.mdpi.com/1873-149X/28/1/11 |
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