Mitochondrial Dysfunction in Repeat Expansion Diseases

Mitochondrial Dysfunction in Repeat Expansion Diseases

Repeat expansion diseases are a group of neuromuscular and neurodegenerative disorders characterized by expansions of several successive repeated DNA sequences. Currently, more than 50 repeat expansion diseases have been described. These disorders involve diverse pathogenic mechanisms, including los...

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Bibliographic Details
Main Authors:	Alberto Giménez-Bejarano, Eva Alegre-Cortés, Sokhna M. S. Yakhine-Diop, Patricia Gómez-Suaga, José M. Fuentes
Format:	Article
Language:	English
Published:	MDPI AG 2023-08-01
Series:	Antioxidants
Subjects:	Huntington disease <i>C9orf72</i> myotonic dystrophy type 1 Ca<sup>2+</sup>, mitophagy apoptosis ROS
Online Access:	https://www.mdpi.com/2076-3921/12/8/1593

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