Recurrent Dermatofibrosarcoma Protuberans with Pigmentation and Myoid Differentiation

Dermatofibrosarcomas protuberans (DFSP) are rare low-grade tumours with various subtypes and usually occur among middle-aged adults. However, myoid differentiation is very rare. We report a 44-year-old woman who presented to the Lok Nayak Jai Prakash Hospital, New Delhi, India, in 2017 with a recurr...

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Main Authors: Surekha Yadav, Nidhi Verma, Nita Khurana, Sushant Neogi
Format: Article
Language:English
Published: Sultan Qaboos University 2018-09-01
Series:Sultan Qaboos University Medical Journal
Online Access:https://journals.squ.edu.om/index.php/squmj/article/view/2725
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author Surekha Yadav
Nidhi Verma
Nita Khurana
Sushant Neogi
author_facet Surekha Yadav
Nidhi Verma
Nita Khurana
Sushant Neogi
author_sort Surekha Yadav
collection DOAJ
description Dermatofibrosarcomas protuberans (DFSP) are rare low-grade tumours with various subtypes and usually occur among middle-aged adults. However, myoid differentiation is very rare. We report a 44-year-old woman who presented to the Lok Nayak Jai Prakash Hospital, New Delhi, India, in 2017 with a recurrent pigmented DFSP presenting as an arm swelling. Upon histological and immunohistochemical analysis, myoid differentiation was confirmed. A literature review of the clinical and histopathological features of this rare entity is presented. Keywords: Dermatofibrosarcoma Protuberans; Melanocytes; Pigmentation; Cell Differentiation; Case Report; India.
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spelling doaj.art-99c28969ab2648b2805c4819cac50f8e2022-12-22T02:13:19ZengSultan Qaboos UniversitySultan Qaboos University Medical Journal2075-051X2075-05282018-09-0118222823010.18295/squmj.2018.18.02.0192404Recurrent Dermatofibrosarcoma Protuberans with Pigmentation and Myoid DifferentiationSurekha Yadav0Nidhi Verma1Nita Khurana2Sushant Neogi3Department of Pathology, Maulana Azad Medical College, New Delhi, IndiaDepartment of Pathology, Maulana Azad Medical College, New Delhi, IndiaDepartment of Pathology, Maulana Azad Medical College, New Delhi, IndiaDepartment of Surgery, Maulana Azad Medical College, New Delhi, IndiaDermatofibrosarcomas protuberans (DFSP) are rare low-grade tumours with various subtypes and usually occur among middle-aged adults. However, myoid differentiation is very rare. We report a 44-year-old woman who presented to the Lok Nayak Jai Prakash Hospital, New Delhi, India, in 2017 with a recurrent pigmented DFSP presenting as an arm swelling. Upon histological and immunohistochemical analysis, myoid differentiation was confirmed. A literature review of the clinical and histopathological features of this rare entity is presented. Keywords: Dermatofibrosarcoma Protuberans; Melanocytes; Pigmentation; Cell Differentiation; Case Report; India.https://journals.squ.edu.om/index.php/squmj/article/view/2725
spellingShingle Surekha Yadav
Nidhi Verma
Nita Khurana
Sushant Neogi
Recurrent Dermatofibrosarcoma Protuberans with Pigmentation and Myoid Differentiation
Sultan Qaboos University Medical Journal
title Recurrent Dermatofibrosarcoma Protuberans with Pigmentation and Myoid Differentiation
title_full Recurrent Dermatofibrosarcoma Protuberans with Pigmentation and Myoid Differentiation
title_fullStr Recurrent Dermatofibrosarcoma Protuberans with Pigmentation and Myoid Differentiation
title_full_unstemmed Recurrent Dermatofibrosarcoma Protuberans with Pigmentation and Myoid Differentiation
title_short Recurrent Dermatofibrosarcoma Protuberans with Pigmentation and Myoid Differentiation
title_sort recurrent dermatofibrosarcoma protuberans with pigmentation and myoid differentiation
url https://journals.squ.edu.om/index.php/squmj/article/view/2725
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AT nitakhurana recurrentdermatofibrosarcomaprotuberanswithpigmentationandmyoiddifferentiation
AT sushantneogi recurrentdermatofibrosarcomaprotuberanswithpigmentationandmyoiddifferentiation