Idiopathic fibrosing mediastinitis with esophageal varices: A case report
Fibrosing mediastinitis (FM) is a rare cause of lung fibrosis with multiple etiologies ranging from infectious to autoimmune to idiopathic. Common causes of FM include histoplasmosis and a relatively new cause of IgG4-related disease. We present a 55-year-old male with symptoms of esophageal varices...
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| Format: | Article |
| Language: | English |
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Elsevier
2023-05-01
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| Series: | Heliyon |
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| Online Access: | http://www.sciencedirect.com/science/article/pii/S2405844023029870 |
| _version_ | 1797815646888656896 |
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| author | Abid M. Sadiq Faryal M. Raza Yazid R. Abdulrahimu Christian P. Mwacha Adnan M. Sadiq Furaha S. Lyamuya |
| author_facet | Abid M. Sadiq Faryal M. Raza Yazid R. Abdulrahimu Christian P. Mwacha Adnan M. Sadiq Furaha S. Lyamuya |
| author_sort | Abid M. Sadiq |
| collection | DOAJ |
| description | Fibrosing mediastinitis (FM) is a rare cause of lung fibrosis with multiple etiologies ranging from infectious to autoimmune to idiopathic. Common causes of FM include histoplasmosis and a relatively new cause of IgG4-related disease. We present a 55-year-old male with symptoms of esophageal varices, intractable hiccups, and progressive difficulty in breathing. A chest X-ray showed right lung fibrosis with pleural effusion and loss of lung volume, which was originally thought to be the sequelae of SARS-CoV-2 or metastasis, but computed tomography of the chest revealed FM. His variceal bleeding was controlled, and he was discharged home. However, treatment for FM was not pursued because the cause was not identified. Using corticosteroids may not cease the progression of the disease, and surgical options are available when symptoms persist. Idiopathic FM requires laboratory and radiological findings to exclude relevant differential diagnoses. |
| first_indexed | 2024-03-13T08:25:57Z |
| format | Article |
| id | doaj.art-99ca2a82e1984ceaad024f8982795bc6 |
| institution | Directory Open Access Journal |
| issn | 2405-8440 |
| language | English |
| last_indexed | 2024-03-13T08:25:57Z |
| publishDate | 2023-05-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Heliyon |
| spelling | doaj.art-99ca2a82e1984ceaad024f8982795bc62023-05-31T04:45:31ZengElsevierHeliyon2405-84402023-05-0195e15780Idiopathic fibrosing mediastinitis with esophageal varices: A case reportAbid M. Sadiq0Faryal M. Raza1Yazid R. Abdulrahimu2Christian P. Mwacha3Adnan M. Sadiq4Furaha S. Lyamuya5Department of Internal Medicine, Kilimanjaro Christian Medical Centre, Moshi, Tanzania; Kilimanjaro Christian Medical University College, Moshi, Tanzania; Corresponding author. Department of Internal Medicine, Kilimanjaro Christian Medical Centre, Moshi, Tanzania.Department of Internal Medicine, Kilimanjaro Christian Medical Centre, Moshi, Tanzania; Kilimanjaro Christian Medical University College, Moshi, TanzaniaDepartment of Internal Medicine, Kilimanjaro Christian Medical Centre, Moshi, TanzaniaDepartment of Internal Medicine, Kilimanjaro Christian Medical Centre, Moshi, TanzaniaKilimanjaro Christian Medical University College, Moshi, Tanzania; Department of Radiology, Kilimanjaro Christian Medical Centre, Moshi, TanzaniaDepartment of Internal Medicine, Kilimanjaro Christian Medical Centre, Moshi, Tanzania; Kilimanjaro Christian Medical University College, Moshi, TanzaniaFibrosing mediastinitis (FM) is a rare cause of lung fibrosis with multiple etiologies ranging from infectious to autoimmune to idiopathic. Common causes of FM include histoplasmosis and a relatively new cause of IgG4-related disease. We present a 55-year-old male with symptoms of esophageal varices, intractable hiccups, and progressive difficulty in breathing. A chest X-ray showed right lung fibrosis with pleural effusion and loss of lung volume, which was originally thought to be the sequelae of SARS-CoV-2 or metastasis, but computed tomography of the chest revealed FM. His variceal bleeding was controlled, and he was discharged home. However, treatment for FM was not pursued because the cause was not identified. Using corticosteroids may not cease the progression of the disease, and surgical options are available when symptoms persist. Idiopathic FM requires laboratory and radiological findings to exclude relevant differential diagnoses.http://www.sciencedirect.com/science/article/pii/S2405844023029870Fibrosing mediastinitisEsophageal varicesComputed tomographyIdiopathicIgG4Case report |
| spellingShingle | Abid M. Sadiq Faryal M. Raza Yazid R. Abdulrahimu Christian P. Mwacha Adnan M. Sadiq Furaha S. Lyamuya Idiopathic fibrosing mediastinitis with esophageal varices: A case report Heliyon Fibrosing mediastinitis Esophageal varices Computed tomography Idiopathic IgG4 Case report |
| title | Idiopathic fibrosing mediastinitis with esophageal varices: A case report |
| title_full | Idiopathic fibrosing mediastinitis with esophageal varices: A case report |
| title_fullStr | Idiopathic fibrosing mediastinitis with esophageal varices: A case report |
| title_full_unstemmed | Idiopathic fibrosing mediastinitis with esophageal varices: A case report |
| title_short | Idiopathic fibrosing mediastinitis with esophageal varices: A case report |
| title_sort | idiopathic fibrosing mediastinitis with esophageal varices a case report |
| topic | Fibrosing mediastinitis Esophageal varices Computed tomography Idiopathic IgG4 Case report |
| url | http://www.sciencedirect.com/science/article/pii/S2405844023029870 |
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