Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy
We present a rare case of Stewart-Treves syndrome characterized by a diffuse angiosarcoma of the leg in a 22-year-old man with a history of chronic lymphedema due to Klippel-Trénaunay-Weber syndrome. He underwent limb disarticulation and medical treatment with cycles of doxorubicin, oral thalidomide...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Karger Publishers
2010-04-01
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| Series: | Case Reports in Oncology |
| Subjects: | |
| Online Access: | http://www.karger.com/Article/FullText/313990 |
| _version_ | 1818534943318343680 |
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| author | Ângela Simas Catarina Matos Rodrigo Lopes da Silva Vítor Brotas Eugénio Teófilo José Pereira Albino |
| author_facet | Ângela Simas Catarina Matos Rodrigo Lopes da Silva Vítor Brotas Eugénio Teófilo José Pereira Albino |
| author_sort | Ângela Simas |
| collection | DOAJ |
| description | We present a rare case of Stewart-Treves syndrome characterized by a diffuse angiosarcoma of the leg in a 22-year-old man with a history of chronic lymphedema due to Klippel-Trénaunay-Weber syndrome. He underwent limb disarticulation and medical treatment with cycles of doxorubicin, oral thalidomide and sunitinib with a very good response after 12 months of follow-up. |
| first_indexed | 2024-12-11T18:18:13Z |
| format | Article |
| id | doaj.art-99e53c609c6b4d57b17f2d33bf74b775 |
| institution | Directory Open Access Journal |
| issn | 1662-6575 |
| language | English |
| last_indexed | 2024-12-11T18:18:13Z |
| publishDate | 2010-04-01 |
| publisher | Karger Publishers |
| record_format | Article |
| series | Case Reports in Oncology |
| spelling | doaj.art-99e53c609c6b4d57b17f2d33bf74b7752022-12-22T00:55:22ZengKarger PublishersCase Reports in Oncology1662-65752010-04-013214815310.1159/000313990313990Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to TherapyÂngela SimasCatarina MatosRodrigo Lopes da SilvaVítor BrotasEugénio TeófiloJosé Pereira AlbinoWe present a rare case of Stewart-Treves syndrome characterized by a diffuse angiosarcoma of the leg in a 22-year-old man with a history of chronic lymphedema due to Klippel-Trénaunay-Weber syndrome. He underwent limb disarticulation and medical treatment with cycles of doxorubicin, oral thalidomide and sunitinib with a very good response after 12 months of follow-up.http://www.karger.com/Article/FullText/313990AngiosarcomaChemotherapyChronic lymphedemaKlippel-Trénaunay-Weber syndromeStewart-Treves syndrome |
| spellingShingle | Ângela Simas Catarina Matos Rodrigo Lopes da Silva Vítor Brotas Eugénio Teófilo José Pereira Albino Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy Case Reports in Oncology Angiosarcoma Chemotherapy Chronic lymphedema Klippel-Trénaunay-Weber syndrome Stewart-Treves syndrome |
| title | Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy |
| title_full | Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy |
| title_fullStr | Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy |
| title_full_unstemmed | Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy |
| title_short | Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy |
| title_sort | epithelioid angiosarcoma in a patient with klippel trenaunay weber syndrome an unexpected response to therapy |
| topic | Angiosarcoma Chemotherapy Chronic lymphedema Klippel-Trénaunay-Weber syndrome Stewart-Treves syndrome |
| url | http://www.karger.com/Article/FullText/313990 |
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