Airway Abnormalities in Adult Mucopolysaccharidosis and Development of Salford Mucopolysaccharidosis Airway Score

Airway Abnormalities in Adult Mucopolysaccharidosis and Development of Salford Mucopolysaccharidosis Airway Score

(1) Background: Mucopolysaccharidoses (MPS) are a heterogeneous group of lysosomal storage disorders caused by the absence of enzymes required for degradation of glycosaminoglycans (GAGs). GAGs deposition in tissues leads to progressive airway narrowing and/or tortuosity. Increased longevity of pati...

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Bibliographic Details
Main Authors: Chaitanya Gadepalli, Karolina M. Stepien, Reena Sharma, Ana Jovanovic, Govind Tol, Andrew Bentley
Format: Article
Language:English
Published: MDPI AG 2021-07-01
Series:Journal of Clinical Medicine
Subjects:
mucopolysaccharidoses
airway
obstruction
management
Online Access:https://www.mdpi.com/2077-0383/10/15/3275

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