Kidney Cysts in Children With Alport Syndrome: A Report of 3 Cases

Kidney Cysts in Children With Alport Syndrome: A Report of 3 Cases

Alport syndrome (AS) is a progressive hereditary kidney disease characterized by hematuria, proteinuria, and progressive kidney dysfunction accompanied by sensorineural hearing loss and ocular abnormalities. Pathogenic COL4A3-5 variants can result in different AS spectra. Further, kidney cysts have...

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Bibliographic Details
Main Authors:	Yeun-Wen Chang, Daw-Yang Hwang, Tung-Ying Chen, Chun-Chen Lin, Min-Hua Tseng, Jeng-Daw Tsai
Format:	Article
Language:	English
Published:	Elsevier 2024-05-01
Series:	Kidney Medicine
Subjects:	Alport syndrome pathogenic COL4A3-COL4A5 variant kidney cysts autosomal-dominant polycystic kidney disease (ADPKD) kidney failure
Online Access:	http://www.sciencedirect.com/science/article/pii/S2590059524000268

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