Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature
Tonsillar synovial sarcoma is an extremely rare entity and only 9 adult patients have been reported up to now. Here, we describe the first pediatric tonsillar synovial sarcoma of the literature in a patient who presented with a 2-month history of dysphagia and snoring. Clinical and radiological exam...
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Format: | Article |
Language: | English |
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Federation of Turkish Pathology Societies
2020-01-01
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Series: | Türk Patoloji Dergisi |
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http://www.turkjpath.org/pdf.php3?id=1886
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author | Koray YALÇIN Gülen TÜYSÜZ Mine GENÇ İrem Hicran ÖZBUDAK Alper Tunga DERİN Kamil KARAALİ Alphan KÜPESİZ Elif GÜLER |
author_facet | Koray YALÇIN Gülen TÜYSÜZ Mine GENÇ İrem Hicran ÖZBUDAK Alper Tunga DERİN Kamil KARAALİ Alphan KÜPESİZ Elif GÜLER |
author_sort | Koray YALÇIN |
collection | DOAJ |
description | Tonsillar synovial sarcoma is an extremely rare entity and only 9 adult patients have been reported up to now. Here, we describe the first pediatric tonsillar synovial sarcoma of the literature in a patient who presented with a 2-month history of dysphagia and snoring. Clinical and radiological examinations showed that the tumor arose from the right palatine tonsil and narrowed the parapharyngeal space. An incisional biopsy from the palatine tonsil revealed the diagnosis of synovial sarcoma. The patient has underwent total tonsillectomy and received radiotherapy and chemotherapy because of the positive surgical margins. The patient is clinically in good condition and free of tumor 30 months after the initial diagnosis. We achieved a long-term complete remission with a combination of surgery, radiotherapy and chemotherapy in our case. Tonsillar synovial sarcoma should be kept in mind while dealing with tonsillar masses. We can conclude that a multidisciplinary approach is warranted while treating synovial sarcoma with this localization. |
first_indexed | 2024-04-10T13:33:48Z |
format | Article |
id | doaj.art-9bf5b9848f1144be8ddda22537ddb8ae |
institution | Directory Open Access Journal |
issn | 1018-5615 1309-5730 |
language | English |
last_indexed | 2024-04-10T13:33:48Z |
publishDate | 2020-01-01 |
publisher | Federation of Turkish Pathology Societies |
record_format | Article |
series | Türk Patoloji Dergisi |
spelling | doaj.art-9bf5b9848f1144be8ddda22537ddb8ae2023-02-15T16:11:28ZengFederation of Turkish Pathology SocietiesTürk Patoloji Dergisi1018-56151309-57302020-01-0136108208610.5146/tjpath.2018.01449Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the LiteratureKoray YALÇINGülen TÜYSÜZMine GENÇİrem Hicran ÖZBUDAKAlper Tunga DERİNKamil KARAALİAlphan KÜPESİZElif GÜLERTonsillar synovial sarcoma is an extremely rare entity and only 9 adult patients have been reported up to now. Here, we describe the first pediatric tonsillar synovial sarcoma of the literature in a patient who presented with a 2-month history of dysphagia and snoring. Clinical and radiological examinations showed that the tumor arose from the right palatine tonsil and narrowed the parapharyngeal space. An incisional biopsy from the palatine tonsil revealed the diagnosis of synovial sarcoma. The patient has underwent total tonsillectomy and received radiotherapy and chemotherapy because of the positive surgical margins. The patient is clinically in good condition and free of tumor 30 months after the initial diagnosis. We achieved a long-term complete remission with a combination of surgery, radiotherapy and chemotherapy in our case. Tonsillar synovial sarcoma should be kept in mind while dealing with tonsillar masses. We can conclude that a multidisciplinary approach is warranted while treating synovial sarcoma with this localization. http://www.turkjpath.org/pdf.php3?id=1886 synovial sarcomatonsillar neoplasmpediatric tumor dysphagiasnoring |
spellingShingle | Koray YALÇIN Gülen TÜYSÜZ Mine GENÇ İrem Hicran ÖZBUDAK Alper Tunga DERİN Kamil KARAALİ Alphan KÜPESİZ Elif GÜLER Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature Türk Patoloji Dergisi synovial sarcoma tonsillar neoplasm pediatric tumor dysphagia snoring |
title | Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature |
title_full | Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature |
title_fullStr | Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature |
title_full_unstemmed | Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature |
title_short | Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature |
title_sort | pediatric tonsillar synovial sarcoma very rare localization a case report and review of the literature |
topic | synovial sarcoma tonsillar neoplasm pediatric tumor dysphagia snoring |
url |
http://www.turkjpath.org/pdf.php3?id=1886
|
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