Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature

Tonsillar synovial sarcoma is an extremely rare entity and only 9 adult patients have been reported up to now. Here, we describe the first pediatric tonsillar synovial sarcoma of the literature in a patient who presented with a 2-month history of dysphagia and snoring. Clinical and radiological exam...

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Main Authors: Koray YALÇIN, Gülen TÜYSÜZ, Mine GENÇ, İrem Hicran ÖZBUDAK, Alper Tunga DERİN, Kamil KARAALİ, Alphan KÜPESİZ, Elif GÜLER
Format: Article
Language:English
Published: Federation of Turkish Pathology Societies 2020-01-01
Series:Türk Patoloji Dergisi
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Online Access: http://www.turkjpath.org/pdf.php3?id=1886
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author Koray YALÇIN
Gülen TÜYSÜZ
Mine GENÇ
İrem Hicran ÖZBUDAK
Alper Tunga DERİN
Kamil KARAALİ
Alphan KÜPESİZ
Elif GÜLER
author_facet Koray YALÇIN
Gülen TÜYSÜZ
Mine GENÇ
İrem Hicran ÖZBUDAK
Alper Tunga DERİN
Kamil KARAALİ
Alphan KÜPESİZ
Elif GÜLER
author_sort Koray YALÇIN
collection DOAJ
description Tonsillar synovial sarcoma is an extremely rare entity and only 9 adult patients have been reported up to now. Here, we describe the first pediatric tonsillar synovial sarcoma of the literature in a patient who presented with a 2-month history of dysphagia and snoring. Clinical and radiological examinations showed that the tumor arose from the right palatine tonsil and narrowed the parapharyngeal space. An incisional biopsy from the palatine tonsil revealed the diagnosis of synovial sarcoma. The patient has underwent total tonsillectomy and received radiotherapy and chemotherapy because of the positive surgical margins. The patient is clinically in good condition and free of tumor 30 months after the initial diagnosis. We achieved a long-term complete remission with a combination of surgery, radiotherapy and chemotherapy in our case. Tonsillar synovial sarcoma should be kept in mind while dealing with tonsillar masses. We can conclude that a multidisciplinary approach is warranted while treating synovial sarcoma with this localization.
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spelling doaj.art-9bf5b9848f1144be8ddda22537ddb8ae2023-02-15T16:11:28ZengFederation of Turkish Pathology SocietiesTürk Patoloji Dergisi1018-56151309-57302020-01-0136108208610.5146/tjpath.2018.01449Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the LiteratureKoray YALÇINGülen TÜYSÜZMine GENÇİrem Hicran ÖZBUDAKAlper Tunga DERİNKamil KARAALİAlphan KÜPESİZElif GÜLERTonsillar synovial sarcoma is an extremely rare entity and only 9 adult patients have been reported up to now. Here, we describe the first pediatric tonsillar synovial sarcoma of the literature in a patient who presented with a 2-month history of dysphagia and snoring. Clinical and radiological examinations showed that the tumor arose from the right palatine tonsil and narrowed the parapharyngeal space. An incisional biopsy from the palatine tonsil revealed the diagnosis of synovial sarcoma. The patient has underwent total tonsillectomy and received radiotherapy and chemotherapy because of the positive surgical margins. The patient is clinically in good condition and free of tumor 30 months after the initial diagnosis. We achieved a long-term complete remission with a combination of surgery, radiotherapy and chemotherapy in our case. Tonsillar synovial sarcoma should be kept in mind while dealing with tonsillar masses. We can conclude that a multidisciplinary approach is warranted while treating synovial sarcoma with this localization. http://www.turkjpath.org/pdf.php3?id=1886 synovial sarcomatonsillar neoplasmpediatric tumor dysphagiasnoring
spellingShingle Koray YALÇIN
Gülen TÜYSÜZ
Mine GENÇ
İrem Hicran ÖZBUDAK
Alper Tunga DERİN
Kamil KARAALİ
Alphan KÜPESİZ
Elif GÜLER
Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature
Türk Patoloji Dergisi
synovial sarcoma
tonsillar neoplasm
pediatric tumor
dysphagia
snoring
title Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature
title_full Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature
title_fullStr Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature
title_full_unstemmed Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature
title_short Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature
title_sort pediatric tonsillar synovial sarcoma very rare localization a case report and review of the literature
topic synovial sarcoma
tonsillar neoplasm
pediatric tumor
dysphagia
snoring
url http://www.turkjpath.org/pdf.php3?id=1886
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