Signifance of Liver Ductal Plate Malformation in Differential Diagnosis of Autosomal Recessive Polycystic Kidney Disease: An Autopsy Case
Cystic renal diseases are a group of disorders that cause neonatal deaths. Autosomal recessive polycystic kidney disease (ARPKD) is a rare entity which may be associated with liver disorders. Presenting autopsy case was stillbirth in 31 + 1 gestational week. In postmortem autopsy,viewed through the...
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| Format: | Article |
| Language: | English |
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Cukurova University
2015-03-01
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| Series: | Çukurova Üniversitesi Tıp Fakültesi Dergisi |
| Subjects: | |
| Online Access: | http://www.scopemed.org/fulltextpdf.php?mno=187154 |
| _version_ | 1828028148982218752 |
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| author | Kivilcim Eren Erdogan Sevil Karabag seyda Erdogan Figen Doran |
| author_facet | Kivilcim Eren Erdogan Sevil Karabag seyda Erdogan Figen Doran |
| author_sort | Kivilcim Eren Erdogan |
| collection | DOAJ |
| description | Cystic renal diseases are a group of disorders that cause neonatal deaths. Autosomal recessive polycystic kidney disease (ARPKD) is a rare entity which may be associated with liver disorders. Presenting autopsy case was stillbirth in 31 + 1 gestational week. In postmortem autopsy,viewed through the capsule, the renal surface was filled by innumerable miniature cysts about 1 mm in diameter. istopathological examination revealed multiple cysts of variable size in the renal medulla and tortuosity, elongation of ductal plate of liver. The autopsy was evaluated as ARPKD and ductal plate malformation. This disorder is not usually compatible with life. Some of the other cystic kidney diseases have better clinical outcome and must be distinguished from ARPKD. [Cukurova Med J 2015; 40(Suppl 1): 18-21] |
| first_indexed | 2024-04-10T13:48:00Z |
| format | Article |
| id | doaj.art-9c530fca89544e18a55b7e43dc5ebc8c |
| institution | Directory Open Access Journal |
| issn | 0250-5150 |
| language | English |
| last_indexed | 2024-04-10T13:48:00Z |
| publishDate | 2015-03-01 |
| publisher | Cukurova University |
| record_format | Article |
| series | Çukurova Üniversitesi Tıp Fakültesi Dergisi |
| spelling | doaj.art-9c530fca89544e18a55b7e43dc5ebc8c2023-02-15T16:10:54ZengCukurova UniversityÇukurova Üniversitesi Tıp Fakültesi Dergisi0250-51502015-03-014011821187154Signifance of Liver Ductal Plate Malformation in Differential Diagnosis of Autosomal Recessive Polycystic Kidney Disease: An Autopsy CaseKivilcim Eren Erdogan0Sevil Karabag1seyda Erdogan2Figen Doran3Patoloji ABD/ Tip Fakultesi/ Cukurova Universitesi/ Adana/ Turkiye Patoloji ABD/ Tip Fakultesi/ Cukurova Universitesi/ Adana/ Turkiye Patoloji ABD/ Tip Fakultesi/ Cukurova Universitesi/ Adana/ Turkiye Patoloji ABD/ Tip Fakultesi/ Cukurova Universitesi/ Adana/ TurkiyeCystic renal diseases are a group of disorders that cause neonatal deaths. Autosomal recessive polycystic kidney disease (ARPKD) is a rare entity which may be associated with liver disorders. Presenting autopsy case was stillbirth in 31 + 1 gestational week. In postmortem autopsy,viewed through the capsule, the renal surface was filled by innumerable miniature cysts about 1 mm in diameter. istopathological examination revealed multiple cysts of variable size in the renal medulla and tortuosity, elongation of ductal plate of liver. The autopsy was evaluated as ARPKD and ductal plate malformation. This disorder is not usually compatible with life. Some of the other cystic kidney diseases have better clinical outcome and must be distinguished from ARPKD. [Cukurova Med J 2015; 40(Suppl 1): 18-21]http://www.scopemed.org/fulltextpdf.php?mno=187154autosomal recessive polycystic kidney diseaseductal plate malformationautopsy |
| spellingShingle | Kivilcim Eren Erdogan Sevil Karabag seyda Erdogan Figen Doran Signifance of Liver Ductal Plate Malformation in Differential Diagnosis of Autosomal Recessive Polycystic Kidney Disease: An Autopsy Case Çukurova Üniversitesi Tıp Fakültesi Dergisi autosomal recessive polycystic kidney disease ductal plate malformation autopsy |
| title | Signifance of Liver Ductal Plate Malformation in Differential Diagnosis of Autosomal Recessive Polycystic Kidney Disease: An Autopsy Case |
| title_full | Signifance of Liver Ductal Plate Malformation in Differential Diagnosis of Autosomal Recessive Polycystic Kidney Disease: An Autopsy Case |
| title_fullStr | Signifance of Liver Ductal Plate Malformation in Differential Diagnosis of Autosomal Recessive Polycystic Kidney Disease: An Autopsy Case |
| title_full_unstemmed | Signifance of Liver Ductal Plate Malformation in Differential Diagnosis of Autosomal Recessive Polycystic Kidney Disease: An Autopsy Case |
| title_short | Signifance of Liver Ductal Plate Malformation in Differential Diagnosis of Autosomal Recessive Polycystic Kidney Disease: An Autopsy Case |
| title_sort | signifance of liver ductal plate malformation in differential diagnosis of autosomal recessive polycystic kidney disease an autopsy case |
| topic | autosomal recessive polycystic kidney disease ductal plate malformation autopsy |
| url | http://www.scopemed.org/fulltextpdf.php?mno=187154 |
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