A case report of phakomatosis pigmentovascularis
The Sturge-Weber syndrome consists of unilateral port wine hemangioma of skin along the trigeminal distribution associated with an ipsilateral leptomeningeal angioma. Nevus of Ota (oculodermal melanosis) is a hamartoma of dermal melanocytes which presents as a blue or gray patch on the face and conj...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2017-01-01
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| Series: | Journal of Clinical Ophthalmology and Research |
| Subjects: | |
| Online Access: | http://www.jcor.in/article.asp?issn=2320-3897;year=2017;volume=5;issue=2;spage=91;epage=93;aulast=Trivedi |
| _version_ | 1811266599597899776 |
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| author | Nitin V Trivedi Ravindra A Vhankade Rushik B Patel |
| author_facet | Nitin V Trivedi Ravindra A Vhankade Rushik B Patel |
| author_sort | Nitin V Trivedi |
| collection | DOAJ |
| description | The Sturge-Weber syndrome consists of unilateral port wine hemangioma of skin along the trigeminal distribution associated with an ipsilateral leptomeningeal angioma. Nevus of Ota (oculodermal melanosis) is a hamartoma of dermal melanocytes which presents as a blue or gray patch on the face and conjunctiva, which is congenital or acquired and is within the distribution of the branches of the trigeminal nerve. The coexistence of cutaneous hemangioma and pigmentary naevi is known as phakomatosis pigmentovascularis. We report the first case of phakomatosis pigmentovascularis in the Indian literature. |
| first_indexed | 2024-04-12T20:46:07Z |
| format | Article |
| id | doaj.art-9c9ace5c8ee844949ad1936d004c3e94 |
| institution | Directory Open Access Journal |
| issn | 2320-3897 |
| language | English |
| last_indexed | 2024-04-12T20:46:07Z |
| publishDate | 2017-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of Clinical Ophthalmology and Research |
| spelling | doaj.art-9c9ace5c8ee844949ad1936d004c3e942022-12-22T03:17:16ZengWolters Kluwer Medknow PublicationsJournal of Clinical Ophthalmology and Research2320-38972017-01-0152919310.4103/2320-3897.205183A case report of phakomatosis pigmentovascularisNitin V TrivediRavindra A VhankadeRushik B PatelThe Sturge-Weber syndrome consists of unilateral port wine hemangioma of skin along the trigeminal distribution associated with an ipsilateral leptomeningeal angioma. Nevus of Ota (oculodermal melanosis) is a hamartoma of dermal melanocytes which presents as a blue or gray patch on the face and conjunctiva, which is congenital or acquired and is within the distribution of the branches of the trigeminal nerve. The coexistence of cutaneous hemangioma and pigmentary naevi is known as phakomatosis pigmentovascularis. We report the first case of phakomatosis pigmentovascularis in the Indian literature.http://www.jcor.in/article.asp?issn=2320-3897;year=2017;volume=5;issue=2;spage=91;epage=93;aulast=TrivediNevus of Otaphakomatosis pigmentovascularisSturge-Weber syndrome |
| spellingShingle | Nitin V Trivedi Ravindra A Vhankade Rushik B Patel A case report of phakomatosis pigmentovascularis Journal of Clinical Ophthalmology and Research Nevus of Ota phakomatosis pigmentovascularis Sturge-Weber syndrome |
| title | A case report of phakomatosis pigmentovascularis |
| title_full | A case report of phakomatosis pigmentovascularis |
| title_fullStr | A case report of phakomatosis pigmentovascularis |
| title_full_unstemmed | A case report of phakomatosis pigmentovascularis |
| title_short | A case report of phakomatosis pigmentovascularis |
| title_sort | case report of phakomatosis pigmentovascularis |
| topic | Nevus of Ota phakomatosis pigmentovascularis Sturge-Weber syndrome |
| url | http://www.jcor.in/article.asp?issn=2320-3897;year=2017;volume=5;issue=2;spage=91;epage=93;aulast=Trivedi |
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