Atlantoaxial dislocation adjacent to kyphotic deformity in a case of adult Larsen syndrome
Kyphotic deformity is often seen in Larsen syndrome. However, its progress in adults is not clear. The adjacent level compression in these patients adds to the difficulty regarding the level that needs to be operated. A 56-year-old male presented with neck pain and spastic quadriplegia. Radiology sh...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
| Published: |
Wolters Kluwer Medknow Publications
2016-01-01
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| Series: | Journal of Craniovertebral Junction and Spine |
| Subjects: | |
| Online Access: | http://www.jcvjs.com/article.asp?issn=0974-8237;year=2016;volume=7;issue=2;spage=109;epage=110;aulast=Sahoo |
| _version_ | 1828422486825369600 |
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| author | Sushanta K Sahoo Arsikere N Deepak Pravin Salunke |
| author_facet | Sushanta K Sahoo Arsikere N Deepak Pravin Salunke |
| author_sort | Sushanta K Sahoo |
| collection | DOAJ |
| description | Kyphotic deformity is often seen in Larsen syndrome. However, its progress in adults is not clear. The adjacent level compression in these patients adds to the difficulty regarding the level that needs to be operated. A 56-year-old male presented with neck pain and spastic quadriplegia. Radiology showed kyphotic deformity (sequelae of Larsen syndrome) with atlantoaxial dislocation. Cord compression was apparent at both levels but careful evaluation showed C1-2 level compression and some compression below the kyphotic deformity. The kyphotic spine was already fused and the canal diameter was adequate. The adjacent level C1-2 was fused and he improved dramatically. Correction of long-standing kyphotic deformity may not be necessary, as it unlikely to progress because of its tendency to fuse naturally. Rather, the adjacent levels are likely to compress the cord due to excessive stress. A proper clinical history and a thorough radiological examination help the surgeon to make an appropriate decision. |
| first_indexed | 2024-12-10T15:48:00Z |
| format | Article |
| id | doaj.art-9d0876aa348e410396669be8226216c3 |
| institution | Directory Open Access Journal |
| issn | 0974-8237 |
| language | English |
| last_indexed | 2024-12-10T15:48:00Z |
| publishDate | 2016-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of Craniovertebral Junction and Spine |
| spelling | doaj.art-9d0876aa348e410396669be8226216c32022-12-22T01:42:54ZengWolters Kluwer Medknow PublicationsJournal of Craniovertebral Junction and Spine0974-82372016-01-017210911010.4103/0974-8237.181869Atlantoaxial dislocation adjacent to kyphotic deformity in a case of adult Larsen syndromeSushanta K SahooArsikere N DeepakPravin SalunkeKyphotic deformity is often seen in Larsen syndrome. However, its progress in adults is not clear. The adjacent level compression in these patients adds to the difficulty regarding the level that needs to be operated. A 56-year-old male presented with neck pain and spastic quadriplegia. Radiology showed kyphotic deformity (sequelae of Larsen syndrome) with atlantoaxial dislocation. Cord compression was apparent at both levels but careful evaluation showed C1-2 level compression and some compression below the kyphotic deformity. The kyphotic spine was already fused and the canal diameter was adequate. The adjacent level C1-2 was fused and he improved dramatically. Correction of long-standing kyphotic deformity may not be necessary, as it unlikely to progress because of its tendency to fuse naturally. Rather, the adjacent levels are likely to compress the cord due to excessive stress. A proper clinical history and a thorough radiological examination help the surgeon to make an appropriate decision.http://www.jcvjs.com/article.asp?issn=0974-8237;year=2016;volume=7;issue=2;spage=109;epage=110;aulast=SahooAtlantoaxial dislocationcervical kyphotic deformityLarsen syndrometwo level compression |
| spellingShingle | Sushanta K Sahoo Arsikere N Deepak Pravin Salunke Atlantoaxial dislocation adjacent to kyphotic deformity in a case of adult Larsen syndrome Journal of Craniovertebral Junction and Spine Atlantoaxial dislocation cervical kyphotic deformity Larsen syndrome two level compression |
| title | Atlantoaxial dislocation adjacent to kyphotic deformity in a case of adult Larsen syndrome |
| title_full | Atlantoaxial dislocation adjacent to kyphotic deformity in a case of adult Larsen syndrome |
| title_fullStr | Atlantoaxial dislocation adjacent to kyphotic deformity in a case of adult Larsen syndrome |
| title_full_unstemmed | Atlantoaxial dislocation adjacent to kyphotic deformity in a case of adult Larsen syndrome |
| title_short | Atlantoaxial dislocation adjacent to kyphotic deformity in a case of adult Larsen syndrome |
| title_sort | atlantoaxial dislocation adjacent to kyphotic deformity in a case of adult larsen syndrome |
| topic | Atlantoaxial dislocation cervical kyphotic deformity Larsen syndrome two level compression |
| url | http://www.jcvjs.com/article.asp?issn=0974-8237;year=2016;volume=7;issue=2;spage=109;epage=110;aulast=Sahoo |
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