A Case of Senile Langerhans Cell Histiocytosis with Soft Tissue Mass as the Main Manifestation

Langerhans cell histiocytosis (LCH) is a rare disease characterized by the proliferation of Langerhans cells and the destruction of local tissue. LCH large occurs in children, whilst incidence of the elderly population is extremely low, and there are few related studies. LCH lesions can involve mult...

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Bibliographic Details
Main Authors: XING Mingquan, WU Weixia, SUN Xiaoxing, WANG Qikai, HAN Hao, GE Hongfeng
Format: Article
Language:zho
Published: Editorial Office of Journal of Rare Diseases 2023-07-01
Series:罕见病研究
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Online Access:https://jrd.chard.org.cn/article/doi/10.12376/j.issn.2097-0501.2023.03.015
Description
Summary:Langerhans cell histiocytosis (LCH) is a rare disease characterized by the proliferation of Langerhans cells and the destruction of local tissue. LCH large occurs in children, whilst incidence of the elderly population is extremely low, and there are few related studies. LCH lesions can involve multiple organs and systems, including bone tissue, lymph nodes, skin, liver, and spleen. However, it is rare that multiple soft tissues are implicated for eldly patients with LCH and present with soft tissue mass as the main manifestation. Here is a report on the clinical features, treatment and prognosis of an elderly LCH with multiple soft tissue masses as the main manifestation, in order to provide clinical reference.
ISSN:2097-0501