Barraquer-Simons syndrome: literature review and case report
Barraquer-Simons syndrome is a type of lipodystrophy characterized by progressive atrophy of the subcutaneous tissue limited to the upper body. Its involvement is usually symmetrical with craniocaudal evolution, reaching down to the thighs. This syndrome is also known as cephalo-thoracic lipodystrop...
| Main Authors: | , , , , , , , , |
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| Format: | Article |
| Language: | English |
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Sociedade Brasileira de Cirurgia Plástica
2016-06-01
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| Series: | Revista Brasileira de Cirurgia Plástica |
| Subjects: | |
| Online Access: | http://www.rbcp.org.br/export-pdf/1749/en_v31n2a24.pdf |
| _version_ | 1797419447487561728 |
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| author | André Luiz de Araujo França Luís Alberto de Souza Leite Jeanine Maria Tejo Caminha Carlos Lacerda de Andrade Almeida Ênio Gomes de Araújo Ernani Coelho Alencar Rafael Neves de Souza Jonathan Augusto Vidal de Oliveira Pedro Flávio de Oliveira Batista |
| author_facet | André Luiz de Araujo França Luís Alberto de Souza Leite Jeanine Maria Tejo Caminha Carlos Lacerda de Andrade Almeida Ênio Gomes de Araújo Ernani Coelho Alencar Rafael Neves de Souza Jonathan Augusto Vidal de Oliveira Pedro Flávio de Oliveira Batista |
| author_sort | André Luiz de Araujo França |
| collection | DOAJ |
| description | Barraquer-Simons syndrome is a type of lipodystrophy characterized by progressive atrophy of the subcutaneous tissue limited to the upper body. Its involvement is usually symmetrical with craniocaudal evolution, reaching down to the thighs. This syndrome is also known as cephalo-thoracic lipodystrophy or progressive partial lipodystrophy. It is a rare disease of unknown origin that usually manifests at the beginning of the second decade of life and has predominance among women. We report a case and literature review of this rare disease, its therapeutic management, and a comparison with other treatment modalities currently available. During one year and three months follow-up, four sessions of facial fat grafting were performed following the principles of structural fat grafting. The use of this therapeutic modality, improved significantly facial contour, and almost complete disappearance of depressions and irregularities, and preservation were achieved during follow-up time. A number of treatments have been described as effective for lipodystrophy, such as: use of alloplastic materials, autologous grafts, local and microsurgical flaps. Each treatment has advantages and disadvantages. Decision depends on the surgeon's experience, availability of resources, specific materials in each center. |
| first_indexed | 2024-03-09T06:47:26Z |
| format | Article |
| id | doaj.art-9e0f0e29a02947e5b8281033725a9c19 |
| institution | Directory Open Access Journal |
| issn | 1983-5175 2177-1235 |
| language | English |
| last_indexed | 2024-03-09T06:47:26Z |
| publishDate | 2016-06-01 |
| publisher | Sociedade Brasileira de Cirurgia Plástica |
| record_format | Article |
| series | Revista Brasileira de Cirurgia Plástica |
| spelling | doaj.art-9e0f0e29a02947e5b8281033725a9c192023-12-03T10:33:43ZengSociedade Brasileira de Cirurgia PlásticaRevista Brasileira de Cirurgia Plástica1983-51752177-12352016-06-01310228128610.5935/2177-1235.2016RBCP0046Barraquer-Simons syndrome: literature review and case reportAndré Luiz de Araujo França0Luís Alberto de Souza Leite1Jeanine Maria Tejo Caminha2Carlos Lacerda de Andrade Almeida3Ênio Gomes de Araújo4Ernani Coelho Alencar5Rafael Neves de Souza6Jonathan Augusto Vidal de Oliveira7Pedro Flávio de Oliveira Batista8Hospital Agamenon Magalhães, Recife, PE, BrazilHospital Agamenon Magalhães, Recife, PE, BrazilHospital Agamenon Magalhães, Recife, PE, BrazilHospital Agamenon Magalhães, Recife, PE, BrazilHospital Agamenon Magalhães, Recife, PE, BrazilHospital Agamenon Magalhães, Recife, PE, BrazilHospital Agamenon Magalhães, Recife, PE, BrazilHospital Agamenon Magalhães, Recife, PE, BrazilHospital Agamenon Magalhães, Recife, PE, BrazilBarraquer-Simons syndrome is a type of lipodystrophy characterized by progressive atrophy of the subcutaneous tissue limited to the upper body. Its involvement is usually symmetrical with craniocaudal evolution, reaching down to the thighs. This syndrome is also known as cephalo-thoracic lipodystrophy or progressive partial lipodystrophy. It is a rare disease of unknown origin that usually manifests at the beginning of the second decade of life and has predominance among women. We report a case and literature review of this rare disease, its therapeutic management, and a comparison with other treatment modalities currently available. During one year and three months follow-up, four sessions of facial fat grafting were performed following the principles of structural fat grafting. The use of this therapeutic modality, improved significantly facial contour, and almost complete disappearance of depressions and irregularities, and preservation were achieved during follow-up time. A number of treatments have been described as effective for lipodystrophy, such as: use of alloplastic materials, autologous grafts, local and microsurgical flaps. Each treatment has advantages and disadvantages. Decision depends on the surgeon's experience, availability of resources, specific materials in each center.http://www.rbcp.org.br/export-pdf/1749/en_v31n2a24.pdflipodistrophyrare diseasessurgical flapsface |
| spellingShingle | André Luiz de Araujo França Luís Alberto de Souza Leite Jeanine Maria Tejo Caminha Carlos Lacerda de Andrade Almeida Ênio Gomes de Araújo Ernani Coelho Alencar Rafael Neves de Souza Jonathan Augusto Vidal de Oliveira Pedro Flávio de Oliveira Batista Barraquer-Simons syndrome: literature review and case report Revista Brasileira de Cirurgia Plástica lipodistrophy rare diseases surgical flaps face |
| title | Barraquer-Simons syndrome: literature
review and case report |
| title_full | Barraquer-Simons syndrome: literature
review and case report |
| title_fullStr | Barraquer-Simons syndrome: literature
review and case report |
| title_full_unstemmed | Barraquer-Simons syndrome: literature
review and case report |
| title_short | Barraquer-Simons syndrome: literature
review and case report |
| title_sort | barraquer simons syndrome literature review and case report |
| topic | lipodistrophy rare diseases surgical flaps face |
| url | http://www.rbcp.org.br/export-pdf/1749/en_v31n2a24.pdf |
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