Cystic Fibrosis Bone Disease: The Interplay between CFTR Dysfunction and Chronic Inflammation

Cystic Fibrosis Bone Disease: The Interplay between CFTR Dysfunction and Chronic Inflammation

Cystic fibrosis is a monogenic disease with a multisystemic phenotype, ranging from predisposition to chronic lung infection and inflammation to reduced bone mass. The exact mechanisms unbalancing the maintenance of an optimal bone mass in cystic fibrosis patients remain unknown. Multiple factors ma...

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Bibliographic Details
Main Authors:	Óscar Fonseca, Maria Salomé Gomes, Maria Adelina Amorim, Ana Cordeiro Gomes
Format:	Article
Language:	English
Published:	MDPI AG 2023-02-01
Series:	Biomolecules
Subjects:	cystic fibrosis related bone disease osteoporosis CFTR bone
Online Access:	https://www.mdpi.com/2218-273X/13/3/425

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