Angle closure glaucoma in congenital ectropion uvea
Purpose: Congenital ectropion uvea is a rare anomaly, which is associated with open, but dysplastic iridocorneal angles that cause childhood glaucoma. Herein, we present 3 cases of angle-closure glaucoma in children with congenital ectropion uvea. Observations: Three children were initially diagnose...
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| Format: | Article |
| Language: | English |
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Elsevier
2018-06-01
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| Series: | American Journal of Ophthalmology Case Reports |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2451993617300270 |
| _version_ | 1818657558895788032 |
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| author | Grace M. Wang Daniel Thuente Brenda L. Bohnsack |
| author_facet | Grace M. Wang Daniel Thuente Brenda L. Bohnsack |
| author_sort | Grace M. Wang |
| collection | DOAJ |
| description | Purpose: Congenital ectropion uvea is a rare anomaly, which is associated with open, but dysplastic iridocorneal angles that cause childhood glaucoma. Herein, we present 3 cases of angle-closure glaucoma in children with congenital ectropion uvea. Observations: Three children were initially diagnosed with unilateral glaucoma secondary to congenital ectropion uvea at 7, 8 and 13 years of age. The three cases showed 360° of ectropion uvea and iris stromal atrophy in the affected eye. In one case, we have photographic documentation of progression to complete angle closure, which necessitated placement of a glaucoma drainage device 3 years after combined trabeculotomy and trabeculectomy. The 2 other cases, which presented as complete angle closure, also underwent glaucoma drainage device implantation. All three cases had early glaucoma drainage device encapsulation (within 4 months) and required additional surgery (cycloablation or trabeculectomy). Conclusions and importance: Congenital ectropion uvea can be associated with angle-closure glaucoma, and placement of glaucoma drainage devices in all 3 of our cases showed early failure due to plate encapsulation. Glaucoma in congenital ectropion uvea requires attention to angle configuration and often requires multiple surgeries to obtain intraocular pressure control. Keywords: Congenital ectropion uvea, Juvenile glaucoma, Angle-closure glaucoma, Glaucoma drainage device |
| first_indexed | 2024-12-17T03:43:24Z |
| format | Article |
| id | doaj.art-9ee300fa9d4148c2baeecebccacceab5 |
| institution | Directory Open Access Journal |
| issn | 2451-9936 |
| language | English |
| last_indexed | 2024-12-17T03:43:24Z |
| publishDate | 2018-06-01 |
| publisher | Elsevier |
| record_format | Article |
| series | American Journal of Ophthalmology Case Reports |
| spelling | doaj.art-9ee300fa9d4148c2baeecebccacceab52022-12-21T22:04:57ZengElsevierAmerican Journal of Ophthalmology Case Reports2451-99362018-06-0110215220Angle closure glaucoma in congenital ectropion uveaGrace M. Wang0Daniel Thuente1Brenda L. Bohnsack2Department of Ophthalmology and Visual Sciences, University of Michigan, United StatesGrand Traverse Ophthalmology Clinic, United StatesDepartment of Ophthalmology and Visual Sciences, University of Michigan, United States; Corresponding author. Department of Ophthalmology and Visual Sciences, Kellogg Eye Center, University of Michigan, 1000 Wall Street, Ann Arbor, MI 48105, United States.Purpose: Congenital ectropion uvea is a rare anomaly, which is associated with open, but dysplastic iridocorneal angles that cause childhood glaucoma. Herein, we present 3 cases of angle-closure glaucoma in children with congenital ectropion uvea. Observations: Three children were initially diagnosed with unilateral glaucoma secondary to congenital ectropion uvea at 7, 8 and 13 years of age. The three cases showed 360° of ectropion uvea and iris stromal atrophy in the affected eye. In one case, we have photographic documentation of progression to complete angle closure, which necessitated placement of a glaucoma drainage device 3 years after combined trabeculotomy and trabeculectomy. The 2 other cases, which presented as complete angle closure, also underwent glaucoma drainage device implantation. All three cases had early glaucoma drainage device encapsulation (within 4 months) and required additional surgery (cycloablation or trabeculectomy). Conclusions and importance: Congenital ectropion uvea can be associated with angle-closure glaucoma, and placement of glaucoma drainage devices in all 3 of our cases showed early failure due to plate encapsulation. Glaucoma in congenital ectropion uvea requires attention to angle configuration and often requires multiple surgeries to obtain intraocular pressure control. Keywords: Congenital ectropion uvea, Juvenile glaucoma, Angle-closure glaucoma, Glaucoma drainage devicehttp://www.sciencedirect.com/science/article/pii/S2451993617300270 |
| spellingShingle | Grace M. Wang Daniel Thuente Brenda L. Bohnsack Angle closure glaucoma in congenital ectropion uvea American Journal of Ophthalmology Case Reports |
| title | Angle closure glaucoma in congenital ectropion uvea |
| title_full | Angle closure glaucoma in congenital ectropion uvea |
| title_fullStr | Angle closure glaucoma in congenital ectropion uvea |
| title_full_unstemmed | Angle closure glaucoma in congenital ectropion uvea |
| title_short | Angle closure glaucoma in congenital ectropion uvea |
| title_sort | angle closure glaucoma in congenital ectropion uvea |
| url | http://www.sciencedirect.com/science/article/pii/S2451993617300270 |
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