Clinical presentation, radiological findings and treatment options in Hughes-Stovin syndrome
Hughes-Stovin syndrome is a rare disease characterized by thrombophlebitis associated with arterial or bronchial aneurysms. Even though it was described first in 1911, it is scarcely reported in the literature. Hughes-Stovin syndrome diagnosis is based on clinical manifestations as well as radiologi...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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Termedia Publishing House
2022-05-01
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| Series: | Rheumatology |
| Subjects: | |
| Online Access: | https://www.termedia.pl/Clinical-presentation-radiological-findings-and-treatment-options-in-Hughes-Stovin-syndrome,18,46890,1,1.html |
| _version_ | 1811302578244288512 |
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| author | Melek Kechida Syrine Daadaa Walid Jomaa |
| author_facet | Melek Kechida Syrine Daadaa Walid Jomaa |
| author_sort | Melek Kechida |
| collection | DOAJ |
| description | Hughes-Stovin syndrome is a rare disease characterized by thrombophlebitis associated with arterial or bronchial aneurysms. Even though it was described first in 1911, it is scarcely reported in the literature. Hughes-Stovin syndrome diagnosis is based on clinical manifestations as well as radiological findings. There are no validated criteria or specific laboratory findings to confirm the diagnosis. Computed tomography pulmonary angiography remains the gold standard for the diagnosis and follow-up of radiological findings, as they were recently described in a critical analysis of the largest cohort in the literature.
The aim of this review is to draw attention to this rare but potentially fatal disease and to discuss its therapeutic options. |
| first_indexed | 2024-04-13T07:31:34Z |
| format | Article |
| id | doaj.art-9ee9fc086c404c658984b80e5cad45d9 |
| institution | Directory Open Access Journal |
| issn | 0034-6233 2084-9834 |
| language | English |
| last_indexed | 2024-04-13T07:31:34Z |
| publishDate | 2022-05-01 |
| publisher | Termedia Publishing House |
| record_format | Article |
| series | Rheumatology |
| spelling | doaj.art-9ee9fc086c404c658984b80e5cad45d92022-12-22T02:56:21ZengTermedia Publishing HouseRheumatology0034-62332084-98342022-05-0160214815210.5114/reum.2022.11566646890Clinical presentation, radiological findings and treatment options in Hughes-Stovin syndromeMelek KechidaSyrine DaadaaWalid JomaaHughes-Stovin syndrome is a rare disease characterized by thrombophlebitis associated with arterial or bronchial aneurysms. Even though it was described first in 1911, it is scarcely reported in the literature. Hughes-Stovin syndrome diagnosis is based on clinical manifestations as well as radiological findings. There are no validated criteria or specific laboratory findings to confirm the diagnosis. Computed tomography pulmonary angiography remains the gold standard for the diagnosis and follow-up of radiological findings, as they were recently described in a critical analysis of the largest cohort in the literature. The aim of this review is to draw attention to this rare but potentially fatal disease and to discuss its therapeutic options.https://www.termedia.pl/Clinical-presentation-radiological-findings-and-treatment-options-in-Hughes-Stovin-syndrome,18,46890,1,1.htmlaneurysm thrombophlebitis hughes-stovin syndrome incomplete behçet’s disease. |
| spellingShingle | Melek Kechida Syrine Daadaa Walid Jomaa Clinical presentation, radiological findings and treatment options in Hughes-Stovin syndrome Rheumatology aneurysm thrombophlebitis hughes-stovin syndrome incomplete behçet’s disease. |
| title | Clinical presentation, radiological findings and treatment options in Hughes-Stovin syndrome |
| title_full | Clinical presentation, radiological findings and treatment options in Hughes-Stovin syndrome |
| title_fullStr | Clinical presentation, radiological findings and treatment options in Hughes-Stovin syndrome |
| title_full_unstemmed | Clinical presentation, radiological findings and treatment options in Hughes-Stovin syndrome |
| title_short | Clinical presentation, radiological findings and treatment options in Hughes-Stovin syndrome |
| title_sort | clinical presentation radiological findings and treatment options in hughes stovin syndrome |
| topic | aneurysm thrombophlebitis hughes-stovin syndrome incomplete behçet’s disease. |
| url | https://www.termedia.pl/Clinical-presentation-radiological-findings-and-treatment-options-in-Hughes-Stovin-syndrome,18,46890,1,1.html |
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