Ovarian sarcoma a diagnostic dilemma– A case report
Primary sarcoma of the ovary is extremely rare. There are inadequate data in the literature regarding ovarian sarcoma in the pediatric age group. We report a case of an 8-year-old girl presenting with large abdominal mass and cachexia. Raised alpha-fetoprotein levels suggested germ cell tumor. Tru-c...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Wolters Kluwer Medknow Publications
2023-01-01
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| Series: | Journal of Indian Association of Pediatric Surgeons |
| Subjects: | |
| Online Access: | http://www.jiaps.com/article.asp?issn=0971-9261;year=2023;volume=28;issue=5;spage=436;epage=438;aulast=Zulpi |
| _version_ | 1797645586438029312 |
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| author | Prashant K Zulpi Akshay B Kalavant Anil B Halgeri P Priyanka |
| author_facet | Prashant K Zulpi Akshay B Kalavant Anil B Halgeri P Priyanka |
| author_sort | Prashant K Zulpi |
| collection | DOAJ |
| description | Primary sarcoma of the ovary is extremely rare. There are inadequate data in the literature regarding ovarian sarcoma in the pediatric age group. We report a case of an 8-year-old girl presenting with large abdominal mass and cachexia. Raised alpha-fetoprotein levels suggested germ cell tumor. Tru-cut biopsy histopathological report suggested a spindle cell tumor. The IHC staining suggested non rhabdomyosarcoma. As tumour was large and ovarian pediatric non rhabdomyosarcoma was not reported in the literature, we started on rhabdomyosarcoma neoadjuant regimen. Good response was noted for neoadjuvant chemotherapy, which was followed by complete surgical excision of the tumor and radiotherapy. At present, the overall outcome of the disease is dismal. Increased available data and gaining more evidence may help in improvising the treatment option. |
| first_indexed | 2024-03-11T14:49:59Z |
| format | Article |
| id | doaj.art-9f05ae0a200946c0b351a7bcb28fb5a6 |
| institution | Directory Open Access Journal |
| issn | 0971-9261 1998-3891 |
| language | English |
| last_indexed | 2024-03-11T14:49:59Z |
| publishDate | 2023-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of Indian Association of Pediatric Surgeons |
| spelling | doaj.art-9f05ae0a200946c0b351a7bcb28fb5a62023-10-30T10:03:35ZengWolters Kluwer Medknow PublicationsJournal of Indian Association of Pediatric Surgeons0971-92611998-38912023-01-0128543643810.4103/jiaps.jiaps_15_23Ovarian sarcoma a diagnostic dilemma– A case reportPrashant K ZulpiAkshay B KalavantAnil B HalgeriP PriyankaPrimary sarcoma of the ovary is extremely rare. There are inadequate data in the literature regarding ovarian sarcoma in the pediatric age group. We report a case of an 8-year-old girl presenting with large abdominal mass and cachexia. Raised alpha-fetoprotein levels suggested germ cell tumor. Tru-cut biopsy histopathological report suggested a spindle cell tumor. The IHC staining suggested non rhabdomyosarcoma. As tumour was large and ovarian pediatric non rhabdomyosarcoma was not reported in the literature, we started on rhabdomyosarcoma neoadjuant regimen. Good response was noted for neoadjuvant chemotherapy, which was followed by complete surgical excision of the tumor and radiotherapy. At present, the overall outcome of the disease is dismal. Increased available data and gaining more evidence may help in improvising the treatment option.http://www.jiaps.com/article.asp?issn=0971-9261;year=2023;volume=28;issue=5;spage=436;epage=438;aulast=Zulpinon-rhabdomyosarcoma of ovaryovarian sarcomapediatric ovarian sarcomapediatric ovarian tumorprimary ovarian sarcoma |
| spellingShingle | Prashant K Zulpi Akshay B Kalavant Anil B Halgeri P Priyanka Ovarian sarcoma a diagnostic dilemma– A case report Journal of Indian Association of Pediatric Surgeons non-rhabdomyosarcoma of ovary ovarian sarcoma pediatric ovarian sarcoma pediatric ovarian tumor primary ovarian sarcoma |
| title | Ovarian sarcoma a diagnostic dilemma– A case report |
| title_full | Ovarian sarcoma a diagnostic dilemma– A case report |
| title_fullStr | Ovarian sarcoma a diagnostic dilemma– A case report |
| title_full_unstemmed | Ovarian sarcoma a diagnostic dilemma– A case report |
| title_short | Ovarian sarcoma a diagnostic dilemma– A case report |
| title_sort | ovarian sarcoma a diagnostic dilemma a case report |
| topic | non-rhabdomyosarcoma of ovary ovarian sarcoma pediatric ovarian sarcoma pediatric ovarian tumor primary ovarian sarcoma |
| url | http://www.jiaps.com/article.asp?issn=0971-9261;year=2023;volume=28;issue=5;spage=436;epage=438;aulast=Zulpi |
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