Anesthetic Management of an Infant with Bilateral Radial Dysplasia and Isolated Patent Ductus Arteriosus: A Case Report and Brief Review of Literature
Bilateral radial dysplasia is a rare condition and usually associated with familial malformation syndromes and spectrum of cardiac anomalies. These patients often require corrective orthopedic surgeries in early age. Radial dysplasia associated with cardiac abnormalities is particularly seen in cer...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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Tehran University of Medical Sciences
2022-11-01
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| Series: | Archives of Anesthesia and Critical Care |
| Subjects: | |
| Online Access: | https://aacc.tums.ac.ir/index.php/aacc/article/view/493 |
| _version_ | 1811216389562695680 |
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| author | Dheeraj Kapoor Harpreet Singh Deepika Gupta Manpreet Singh Parul Sood |
| author_facet | Dheeraj Kapoor Harpreet Singh Deepika Gupta Manpreet Singh Parul Sood |
| author_sort | Dheeraj Kapoor |
| collection | DOAJ |
| description |
Bilateral radial dysplasia is a rare condition and usually associated with familial malformation syndromes and spectrum of cardiac anomalies. These patients often require corrective orthopedic surgeries in early age. Radial dysplasia associated with cardiac abnormalities is particularly seen in certain syndromes such as Holt-Oram (HOS) syndrome and TAR (thrombocytopenia, anemia, and radial aplasia) syndrome. We report a successful management of twelve months old male child with rare combination of bilateral radial dysplasia with isolated patent ductus arteriosus (PDA), for corrective orthopedic surgery. A comprehensive approach, which includes an extensive preoperative evaluation and pre-defined perioperative hemodynamic goals for PDA, plays a pivotal role in its perioperative management.
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| first_indexed | 2024-04-12T06:38:17Z |
| format | Article |
| id | doaj.art-9fb911ba66b74c3da8a69682d41016ee |
| institution | Directory Open Access Journal |
| issn | 2423-5849 |
| language | English |
| last_indexed | 2024-04-12T06:38:17Z |
| publishDate | 2022-11-01 |
| publisher | Tehran University of Medical Sciences |
| record_format | Article |
| series | Archives of Anesthesia and Critical Care |
| spelling | doaj.art-9fb911ba66b74c3da8a69682d41016ee2022-12-22T03:43:48ZengTehran University of Medical SciencesArchives of Anesthesia and Critical Care2423-58492022-11-018SupplementAnesthetic Management of an Infant with Bilateral Radial Dysplasia and Isolated Patent Ductus Arteriosus: A Case Report and Brief Review of LiteratureDheeraj Kapoor0Harpreet Singh1Deepika Gupta2Manpreet Singh3Parul Sood4Department of Anaesthesia and Intensive Care, Government Medical College and Hospital, Chandigarh, India.Department of Critical Care Medicine, Paras Hospital, Panchkula, India.Department of Anaesthesia and Intensive Care, Government Medical College and Hospital, Chandigarh, India.Department of Anaesthesia and Intensive Care, Government Medical College and Hospital, Chandigarh, India.Department of Physiotherapy, Government Medical College and Hospital, Chandigarh, India. Bilateral radial dysplasia is a rare condition and usually associated with familial malformation syndromes and spectrum of cardiac anomalies. These patients often require corrective orthopedic surgeries in early age. Radial dysplasia associated with cardiac abnormalities is particularly seen in certain syndromes such as Holt-Oram (HOS) syndrome and TAR (thrombocytopenia, anemia, and radial aplasia) syndrome. We report a successful management of twelve months old male child with rare combination of bilateral radial dysplasia with isolated patent ductus arteriosus (PDA), for corrective orthopedic surgery. A comprehensive approach, which includes an extensive preoperative evaluation and pre-defined perioperative hemodynamic goals for PDA, plays a pivotal role in its perioperative management. https://aacc.tums.ac.ir/index.php/aacc/article/view/493Radial dysplasiaPatent ductus arteriosusHolt-Oram syndromeTAR syndromeOrthopedic |
| spellingShingle | Dheeraj Kapoor Harpreet Singh Deepika Gupta Manpreet Singh Parul Sood Anesthetic Management of an Infant with Bilateral Radial Dysplasia and Isolated Patent Ductus Arteriosus: A Case Report and Brief Review of Literature Archives of Anesthesia and Critical Care Radial dysplasia Patent ductus arteriosus Holt-Oram syndrome TAR syndrome Orthopedic |
| title | Anesthetic Management of an Infant with Bilateral Radial Dysplasia and Isolated Patent Ductus Arteriosus: A Case Report and Brief Review of Literature |
| title_full | Anesthetic Management of an Infant with Bilateral Radial Dysplasia and Isolated Patent Ductus Arteriosus: A Case Report and Brief Review of Literature |
| title_fullStr | Anesthetic Management of an Infant with Bilateral Radial Dysplasia and Isolated Patent Ductus Arteriosus: A Case Report and Brief Review of Literature |
| title_full_unstemmed | Anesthetic Management of an Infant with Bilateral Radial Dysplasia and Isolated Patent Ductus Arteriosus: A Case Report and Brief Review of Literature |
| title_short | Anesthetic Management of an Infant with Bilateral Radial Dysplasia and Isolated Patent Ductus Arteriosus: A Case Report and Brief Review of Literature |
| title_sort | anesthetic management of an infant with bilateral radial dysplasia and isolated patent ductus arteriosus a case report and brief review of literature |
| topic | Radial dysplasia Patent ductus arteriosus Holt-Oram syndrome TAR syndrome Orthopedic |
| url | https://aacc.tums.ac.ir/index.php/aacc/article/view/493 |
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