Ormond’s Disease – IgG4-related Disease

Ormond’s disease is a relatively rare disease with unclear etiology, characterized by chronic periaortitis and retroperitoneal fibrosis. The inflammatory process affects the infrarenal part of the abdominal aorta and the iliac arteries, and the presence of infiltrates encasing the ureters and inferi...

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Main Authors: Miroslav Průcha, Ivan Kolombo, Petr Štádler
Format: Article
Language:English
Published: Karolinum Press 2015-01-01
Series:Prague Medical Report
Subjects:
Online Access:https://pmr.lf1.cuni.cz/116/3/0181/
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author Miroslav Průcha
Ivan Kolombo
Petr Štádler
author_facet Miroslav Průcha
Ivan Kolombo
Petr Štádler
author_sort Miroslav Průcha
collection DOAJ
description Ormond’s disease is a relatively rare disease with unclear etiology, characterized by chronic periaortitis and retroperitoneal fibrosis. The inflammatory process affects the infrarenal part of the abdominal aorta and the iliac arteries, and the presence of infiltrates encasing the ureters and inferior vena cava. This disease is currently classed as an IgG4-related disease. In our review we analyse the clinical history, diagnostic approaches, surgical and immunosuppressive therapies.
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spelling doaj.art-a0a36033bd63425e890cc4a25afba42e2022-12-22T01:49:05ZengKarolinum PressPrague Medical Report1214-69942336-29362015-01-01116318119210.14712/23362936.2015.57Ormond’s Disease – IgG4-related DiseaseMiroslav Průcha0Ivan Kolombo1Petr Štádler2Department of Clinical Biochemistry, Haematology and Immunology, Na Homolce Hospital, Prague, Czech RepublicDepartment of Urology, Third Faculty of Medicine, Charles University in Prague and University Hospital Královské Vinohrady, Prague, Czech RepublicDepartment of Vascular Surgery, Na Homolce Hospital, Prague, Czech RepublicOrmond’s disease is a relatively rare disease with unclear etiology, characterized by chronic periaortitis and retroperitoneal fibrosis. The inflammatory process affects the infrarenal part of the abdominal aorta and the iliac arteries, and the presence of infiltrates encasing the ureters and inferior vena cava. This disease is currently classed as an IgG4-related disease. In our review we analyse the clinical history, diagnostic approaches, surgical and immunosuppressive therapies.https://pmr.lf1.cuni.cz/116/3/0181/Ormond’s diseasePeriaortitisHydronefrosisSurgical treatmentImmunosuppression
spellingShingle Miroslav Průcha
Ivan Kolombo
Petr Štádler
Ormond’s Disease – IgG4-related Disease
Prague Medical Report
Ormond’s disease
Periaortitis
Hydronefrosis
Surgical treatment
Immunosuppression
title Ormond’s Disease – IgG4-related Disease
title_full Ormond’s Disease – IgG4-related Disease
title_fullStr Ormond’s Disease – IgG4-related Disease
title_full_unstemmed Ormond’s Disease – IgG4-related Disease
title_short Ormond’s Disease – IgG4-related Disease
title_sort ormond s disease igg4 related disease
topic Ormond’s disease
Periaortitis
Hydronefrosis
Surgical treatment
Immunosuppression
url https://pmr.lf1.cuni.cz/116/3/0181/
work_keys_str_mv AT miroslavprucha ormondsdiseaseigg4relateddisease
AT ivankolombo ormondsdiseaseigg4relateddisease
AT petrstadler ormondsdiseaseigg4relateddisease