Neuromuscular monitoring of a patient with Charcot-Marie-Tooth disease; which monitoring technique is adequate? - A case report and literature review -
Background Charcot-Marie-Tooth disease (CMTD) is a hereditary polyneuropathy associated with a life-threatening risk of pulmonary complications. Case A 61-year-old male with CMTD for 40 years was admitted for the drainage of an abscess in his left ankle. Total intravenous anesthesia was administered...
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| Format: | Article |
| Language: | English |
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Korean Society of Anesthesiologists
2024-01-01
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| Series: | Anesthesia and Pain Medicine |
| Subjects: | |
| Online Access: | http://anesth-pain-med.org/upload/pdf/apm-23111.pdf |
| _version_ | 1827351221981151232 |
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| author | Seung Un Kim Seora Kim Ki Tae Jung |
| author_facet | Seung Un Kim Seora Kim Ki Tae Jung |
| author_sort | Seung Un Kim |
| collection | DOAJ |
| description | Background Charcot-Marie-Tooth disease (CMTD) is a hereditary polyneuropathy associated with a life-threatening risk of pulmonary complications. Case A 61-year-old male with CMTD for 40 years was admitted for the drainage of an abscess in his left ankle. Total intravenous anesthesia was administered, and an electromyography device was attached to the hand for neuromuscular monitoring; however, the response was not measured. Kinemyography and acceleromyography devices were attached to both hands, and responses were obtained. After neuromuscular blockade (NMB) with rocuronium 0.6 mg/kg, the train-of-four (TOF) response on kinemyography was normally measured, but the post-tetanic count on acceleromyography consistently showed 0 during anesthesia. Sugammadex 200 mg was injected to reverse the NMB. After 5 min, the TOF ratios for kinemyography and acceleromyography exceeded 90%. The patient recovered without any complications. Conclusions For CMTD patients, acceleromyography or kinemyography is superior to electromyography, and sugammadex can be used to reverse NMB successfully. |
| first_indexed | 2024-03-08T02:00:02Z |
| format | Article |
| id | doaj.art-a15db4f269b84054addfccbeafbce5ff |
| institution | Directory Open Access Journal |
| issn | 1975-5171 2383-7977 |
| language | English |
| last_indexed | 2024-03-08T02:00:02Z |
| publishDate | 2024-01-01 |
| publisher | Korean Society of Anesthesiologists |
| record_format | Article |
| series | Anesthesia and Pain Medicine |
| spelling | doaj.art-a15db4f269b84054addfccbeafbce5ff2024-02-14T06:30:13ZengKorean Society of AnesthesiologistsAnesthesia and Pain Medicine1975-51712383-79772024-01-01191546110.17085/apm.231111233Neuromuscular monitoring of a patient with Charcot-Marie-Tooth disease; which monitoring technique is adequate? - A case report and literature review -Seung Un Kim0Seora Kim1Ki Tae Jung2 Department of Medicine, Graduate School, Chosun University, Gwangju, Korea Department of Anesthesiology and Pain Medicine, Chosun University Hospital, College of Medicine and Medical School, Chosun University, Gwangju, Korea Department of Medicine, Graduate School, Chosun University, Gwangju, KoreaBackground Charcot-Marie-Tooth disease (CMTD) is a hereditary polyneuropathy associated with a life-threatening risk of pulmonary complications. Case A 61-year-old male with CMTD for 40 years was admitted for the drainage of an abscess in his left ankle. Total intravenous anesthesia was administered, and an electromyography device was attached to the hand for neuromuscular monitoring; however, the response was not measured. Kinemyography and acceleromyography devices were attached to both hands, and responses were obtained. After neuromuscular blockade (NMB) with rocuronium 0.6 mg/kg, the train-of-four (TOF) response on kinemyography was normally measured, but the post-tetanic count on acceleromyography consistently showed 0 during anesthesia. Sugammadex 200 mg was injected to reverse the NMB. After 5 min, the TOF ratios for kinemyography and acceleromyography exceeded 90%. The patient recovered without any complications. Conclusions For CMTD patients, acceleromyography or kinemyography is superior to electromyography, and sugammadex can be used to reverse NMB successfully.http://anesth-pain-med.org/upload/pdf/apm-23111.pdfanesthesiacharcot-marie-tooth diseasemyographyneuromuscular blockadeneuromuscular monitoringsugammadex |
| spellingShingle | Seung Un Kim Seora Kim Ki Tae Jung Neuromuscular monitoring of a patient with Charcot-Marie-Tooth disease; which monitoring technique is adequate? - A case report and literature review - Anesthesia and Pain Medicine anesthesia charcot-marie-tooth disease myography neuromuscular blockade neuromuscular monitoring sugammadex |
| title | Neuromuscular monitoring of a patient with Charcot-Marie-Tooth disease; which monitoring technique is adequate? - A case report and literature review - |
| title_full | Neuromuscular monitoring of a patient with Charcot-Marie-Tooth disease; which monitoring technique is adequate? - A case report and literature review - |
| title_fullStr | Neuromuscular monitoring of a patient with Charcot-Marie-Tooth disease; which monitoring technique is adequate? - A case report and literature review - |
| title_full_unstemmed | Neuromuscular monitoring of a patient with Charcot-Marie-Tooth disease; which monitoring technique is adequate? - A case report and literature review - |
| title_short | Neuromuscular monitoring of a patient with Charcot-Marie-Tooth disease; which monitoring technique is adequate? - A case report and literature review - |
| title_sort | neuromuscular monitoring of a patient with charcot marie tooth disease which monitoring technique is adequate a case report and literature review |
| topic | anesthesia charcot-marie-tooth disease myography neuromuscular blockade neuromuscular monitoring sugammadex |
| url | http://anesth-pain-med.org/upload/pdf/apm-23111.pdf |
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