A Case Series of Metastatic Malignant Gastrointestinal Neuroectodermal Tumors and Comprehensive Genomic Profiling Analysis of 20 Cases

A Case Series of Metastatic Malignant Gastrointestinal Neuroectodermal Tumors and Comprehensive Genomic Profiling Analysis of 20 Cases

Malignant gastrointestinal neuroectodermal tumor (GNET) is an ultra-rare soft tissue sarcoma, therefore often misdiagnosed and has no available standard treatment. Here, we report 3 cases of metastatic GNET with variable clinical courses. Our small case series as well as extensive literature review,...

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Bibliographic Details
Main Authors:	Taylor Kandler, Eliane Cortez, Lani Clinton, Amanda Hemmerich, Osama Ahmed, Ralph Wong, Taylor Forns, Andrea J. MacNeill, Trevor D. Hamilton, Mohammadali Khorasani, Xiaolan Feng
Format:	Article
Language:	English
Published:	MDPI AG 2022-02-01
Series:	Current Oncology
Subjects:	malignant gastrointestinal neuroectodermal tumors (GNET) clear cell sarcoma (CCS) clear cell sarcoma-like tumor of the gastrointestinal tract (CCSTGT) EWSR1-ATF1 fusion EWSR1-CREB1 fusion comprehensive genomic profiling (CGP)
Online Access:	https://www.mdpi.com/1718-7729/29/2/109

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