Cardiac Imaging in Patients After Fontan Palliation: Which Test and When?
The Fontan operation represents the final stage of a series of palliative surgical procedures for children born with complex congenital heart disease, where a “usual” biventricular physiology cannot be restored. The palliation results in the direct connection of the systemic venous returns to the pu...
| Main Authors: | , , , , , , , , , , |
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| Format: | Article |
| Language: | English |
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Frontiers Media S.A.
2022-05-01
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| Series: | Frontiers in Pediatrics |
| Subjects: | |
| Online Access: | https://www.frontiersin.org/articles/10.3389/fped.2022.876742/full |
| _version_ | 1828796190078009344 |
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| author | Paolo Ciliberti Paolo Ciancarella Pasqualina Bruno Davide Curione Veronica Bordonaro Veronica Lisignoli Mario Panebianco Marcello Chinali Aurelio Secinaro Lorenzo Galletti Paolo Guccione |
| author_facet | Paolo Ciliberti Paolo Ciancarella Pasqualina Bruno Davide Curione Veronica Bordonaro Veronica Lisignoli Mario Panebianco Marcello Chinali Aurelio Secinaro Lorenzo Galletti Paolo Guccione |
| author_sort | Paolo Ciliberti |
| collection | DOAJ |
| description | The Fontan operation represents the final stage of a series of palliative surgical procedures for children born with complex congenital heart disease, where a “usual” biventricular physiology cannot be restored. The palliation results in the direct connection of the systemic venous returns to the pulmonary arterial circulation without an interposed ventricle. In this unique physiology, systemic venous hypertension and intrathoracic pressures changes due to respiratory mechanics play the main role for propelling blood through the pulmonary vasculature. Although the Fontan operation has dramatically improved survival in patients with a single ventricle congenital heart disease, significant morbidity is still a concern. Patients with Fontan physiology are in fact suffering from a multitude of complications mainly due to the increased systemic venous pressure. Consequently, these patients need close clinical and imaging monitoring, where cardiac exams play a key role. In this article, we review the main cardiac imaging modalities available, summarizing their main strengths and limitations in this peculiar setting. The main purpose is to provide a practical approach for all clinicians involved in the care of these patients, even for those less experienced in cardiac imaging. |
| first_indexed | 2024-12-12T04:17:18Z |
| format | Article |
| id | doaj.art-a2201fb630c44e80a03317215c986389 |
| institution | Directory Open Access Journal |
| issn | 2296-2360 |
| language | English |
| last_indexed | 2024-12-12T04:17:18Z |
| publishDate | 2022-05-01 |
| publisher | Frontiers Media S.A. |
| record_format | Article |
| series | Frontiers in Pediatrics |
| spelling | doaj.art-a2201fb630c44e80a03317215c9863892022-12-22T00:38:24ZengFrontiers Media S.A.Frontiers in Pediatrics2296-23602022-05-011010.3389/fped.2022.876742876742Cardiac Imaging in Patients After Fontan Palliation: Which Test and When?Paolo Ciliberti0Paolo Ciancarella1Pasqualina Bruno2Davide Curione3Veronica Bordonaro4Veronica Lisignoli5Mario Panebianco6Marcello Chinali7Aurelio Secinaro8Lorenzo Galletti9Paolo Guccione10Department of Cardiac Surgery, Cardiology, Heart and Lung Transplantation Bambino Gesu' Children's Hospital, IRCCS, Rome, ItalyAdvanced Cardiothoracic Imaging Unit, Bambino Gesù Children's Hospital, IRCCS, Rome, ItalyDepartment of Cardiac Surgery, Cardiology, Heart and Lung Transplantation Bambino Gesu' Children's Hospital, IRCCS, Rome, ItalyAdvanced Cardiothoracic Imaging Unit, Bambino Gesù Children's Hospital, IRCCS, Rome, ItalyAdvanced Cardiothoracic Imaging Unit, Bambino Gesù Children's Hospital, IRCCS, Rome, ItalyDepartment of Cardiac Surgery, Cardiology, Heart and Lung Transplantation Bambino Gesu' Children's Hospital, IRCCS, Rome, ItalyDepartment of Cardiac Surgery, Cardiology, Heart and Lung Transplantation Bambino Gesu' Children's Hospital, IRCCS, Rome, ItalyDepartment of Cardiac Surgery, Cardiology, Heart and Lung Transplantation Bambino Gesu' Children's Hospital, IRCCS, Rome, ItalyAdvanced Cardiothoracic Imaging Unit, Bambino Gesù Children's Hospital, IRCCS, Rome, ItalyDepartment of Cardiac Surgery, Cardiology, Heart and Lung Transplantation Bambino Gesu' Children's Hospital, IRCCS, Rome, ItalyDepartment of Cardiac Surgery, Cardiology, Heart and Lung Transplantation Bambino Gesu' Children's Hospital, IRCCS, Rome, ItalyThe Fontan operation represents the final stage of a series of palliative surgical procedures for children born with complex congenital heart disease, where a “usual” biventricular physiology cannot be restored. The palliation results in the direct connection of the systemic venous returns to the pulmonary arterial circulation without an interposed ventricle. In this unique physiology, systemic venous hypertension and intrathoracic pressures changes due to respiratory mechanics play the main role for propelling blood through the pulmonary vasculature. Although the Fontan operation has dramatically improved survival in patients with a single ventricle congenital heart disease, significant morbidity is still a concern. Patients with Fontan physiology are in fact suffering from a multitude of complications mainly due to the increased systemic venous pressure. Consequently, these patients need close clinical and imaging monitoring, where cardiac exams play a key role. In this article, we review the main cardiac imaging modalities available, summarizing their main strengths and limitations in this peculiar setting. The main purpose is to provide a practical approach for all clinicians involved in the care of these patients, even for those less experienced in cardiac imaging.https://www.frontiersin.org/articles/10.3389/fped.2022.876742/fullcongenital heart diseaseFontan operationechocardiographycardiac CTcardiac MRI |
| spellingShingle | Paolo Ciliberti Paolo Ciancarella Pasqualina Bruno Davide Curione Veronica Bordonaro Veronica Lisignoli Mario Panebianco Marcello Chinali Aurelio Secinaro Lorenzo Galletti Paolo Guccione Cardiac Imaging in Patients After Fontan Palliation: Which Test and When? Frontiers in Pediatrics congenital heart disease Fontan operation echocardiography cardiac CT cardiac MRI |
| title | Cardiac Imaging in Patients After Fontan Palliation: Which Test and When? |
| title_full | Cardiac Imaging in Patients After Fontan Palliation: Which Test and When? |
| title_fullStr | Cardiac Imaging in Patients After Fontan Palliation: Which Test and When? |
| title_full_unstemmed | Cardiac Imaging in Patients After Fontan Palliation: Which Test and When? |
| title_short | Cardiac Imaging in Patients After Fontan Palliation: Which Test and When? |
| title_sort | cardiac imaging in patients after fontan palliation which test and when |
| topic | congenital heart disease Fontan operation echocardiography cardiac CT cardiac MRI |
| url | https://www.frontiersin.org/articles/10.3389/fped.2022.876742/full |
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