An Astonishing Extrarenal Wilms Localisation; Spinal Cord

Wilms’ tumour is a renal tumour mostly seen during the first 5 years of life and it accounts for 95% of renal malignancies during childhood. Its origin is primitive metanephric cells and, very rarely, it may occur in places other than the kidneys. The estimated rate of nephroblastoma outside the kid...

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Main Authors: Ayşe Gülnur Tokuç, Nurşah Eker, Burcu Tufan Taş, Süheyla Uyar Bozkurt, Mustafa Sakar, Seda Aras, Kadriye Ebru Akar
Format: Article
Language:English
Published: Galenos Yayinevi 2022-06-01
Series:Journal of Pediatric Research
Subjects:
Online Access: http://jpedres.org/archives/archive-detail/article-preview/an-astonishing-extrarenal-wilms-localisation-spina/52011
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author Ayşe Gülnur Tokuç
Nurşah Eker
Burcu Tufan Taş
Süheyla Uyar Bozkurt
Mustafa Sakar
Seda Aras
Kadriye Ebru Akar
author_facet Ayşe Gülnur Tokuç
Nurşah Eker
Burcu Tufan Taş
Süheyla Uyar Bozkurt
Mustafa Sakar
Seda Aras
Kadriye Ebru Akar
author_sort Ayşe Gülnur Tokuç
collection DOAJ
description Wilms’ tumour is a renal tumour mostly seen during the first 5 years of life and it accounts for 95% of renal malignancies during childhood. Its origin is primitive metanephric cells and, very rarely, it may occur in places other than the kidneys. The estimated rate of nephroblastoma outside the kidneys is approximately 0.5 to 1% of Wilms’ tumour cases. In this article, we report on a 3-year-old female patient who first presented with spinal dysraphism and a mass in the lumbar spinal cord with a histopathological diagnosis of nephrogenic rest, and after one year, a Wilms tumour arose in this location. This is a very rare extrarenal Wilms’ tumour location. Here, we report on a case with immature renal cells located in the lumber spinal cord associated with spinal dysraphism and the development of Wilms’ tumour there after one year.
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spelling doaj.art-a27a7b15790441e8bb751563314e6e092023-02-15T16:19:46ZengGalenos YayineviJournal of Pediatric Research2147-94452587-24782022-06-019218819110.4274/jpr.galenos.2021.3444513049054An Astonishing Extrarenal Wilms Localisation; Spinal CordAyşe Gülnur Tokuç0Nurşah Eker1Burcu Tufan Taş2Süheyla Uyar Bozkurt3Mustafa Sakar4Seda Aras5Kadriye Ebru Akar6 Marmara University Faculty of Medicine, Department of Pediatric Hematology and Oncology, İstanbul, Turkey Marmara University Faculty of Medicine, Department of Pediatric Hematology and Oncology, İstanbul, Turkey Marmara University Pendik Training and Research Hospital, Clinic of Pediatric Hematology and Oncology, İstanbul, Turkey Marmara University Faculty of Medicine, Department of Pathology, İstanbul, Turkey Marmara University Faculty of Medicine, Department of Brain and Neurosurgery, İstanbul, Turkey Marmara University Faculty of Medicine, Department of Pediatric Hematology and Oncology, İstanbul, Turkey Marmara University Faculty of Medicine, Department of Pathology, İstanbul, Turkey Wilms’ tumour is a renal tumour mostly seen during the first 5 years of life and it accounts for 95% of renal malignancies during childhood. Its origin is primitive metanephric cells and, very rarely, it may occur in places other than the kidneys. The estimated rate of nephroblastoma outside the kidneys is approximately 0.5 to 1% of Wilms’ tumour cases. In this article, we report on a 3-year-old female patient who first presented with spinal dysraphism and a mass in the lumbar spinal cord with a histopathological diagnosis of nephrogenic rest, and after one year, a Wilms tumour arose in this location. This is a very rare extrarenal Wilms’ tumour location. Here, we report on a case with immature renal cells located in the lumber spinal cord associated with spinal dysraphism and the development of Wilms’ tumour there after one year. http://jpedres.org/archives/archive-detail/article-preview/an-astonishing-extrarenal-wilms-localisation-spina/52011 childrenextrarenalwilms
spellingShingle Ayşe Gülnur Tokuç
Nurşah Eker
Burcu Tufan Taş
Süheyla Uyar Bozkurt
Mustafa Sakar
Seda Aras
Kadriye Ebru Akar
An Astonishing Extrarenal Wilms Localisation; Spinal Cord
Journal of Pediatric Research
children
extrarenal
wilms
title An Astonishing Extrarenal Wilms Localisation; Spinal Cord
title_full An Astonishing Extrarenal Wilms Localisation; Spinal Cord
title_fullStr An Astonishing Extrarenal Wilms Localisation; Spinal Cord
title_full_unstemmed An Astonishing Extrarenal Wilms Localisation; Spinal Cord
title_short An Astonishing Extrarenal Wilms Localisation; Spinal Cord
title_sort astonishing extrarenal wilms localisation spinal cord
topic children
extrarenal
wilms
url http://jpedres.org/archives/archive-detail/article-preview/an-astonishing-extrarenal-wilms-localisation-spina/52011
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