Treatment considerations in total anomalous pulmonary venous connection
Background Total anomalous pulmonary venous connection (TAPVC) is a rare cyanotic abnormality that accounts for about 1%–3% of congenital heart disease malformations. TAPVC is a condition in which there is no direct connection between all four pulmonary veins and the left atrium but makes abnormal c...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
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SAGE Publishing
2023-07-01
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| Series: | Proceedings of Singapore Healthcare |
| Online Access: | https://doi.org/10.1177/20101058231188865 |
| _version_ | 1797785122561327104 |
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| author | Eka Prasetya Budi Mulia Mahrus A. Rahman |
| author_facet | Eka Prasetya Budi Mulia Mahrus A. Rahman |
| author_sort | Eka Prasetya Budi Mulia |
| collection | DOAJ |
| description | Background Total anomalous pulmonary venous connection (TAPVC) is a rare cyanotic abnormality that accounts for about 1%–3% of congenital heart disease malformations. TAPVC is a condition in which there is no direct connection between all four pulmonary veins and the left atrium but makes abnormal connections to the right atrium or systemic venous system. TAPVC caused a high mortality rate of 80% in the first year of life, and 50% of them die within 3 months after birth without intervention. Objectives The aim of this review is to elucidate the various treatment considerations of TAPVC. Methods A literature search was conducted on PubMed, ScienceDirect and Google Scholar using various combinations of keywords related to treatment of TAPVC. The citations from all selected articles were reviewed for additional studies. Results and Conclusion TAPVC intervention, including medical and surgical, is tailored to each type of TAPVC. Catheter-based interventions are frequently used to temporize neonates and provide time to optimize patients medically prior to definite repair. Corrective surgery is required for all patients with this condition. Several latest catheter-based or surgical intervention technique modifications have also been reported. |
| first_indexed | 2024-03-13T00:49:35Z |
| format | Article |
| id | doaj.art-a29014b83ae44cc68512694e999aa371 |
| institution | Directory Open Access Journal |
| issn | 2059-2329 |
| language | English |
| last_indexed | 2024-03-13T00:49:35Z |
| publishDate | 2023-07-01 |
| publisher | SAGE Publishing |
| record_format | Article |
| series | Proceedings of Singapore Healthcare |
| spelling | doaj.art-a29014b83ae44cc68512694e999aa3712023-07-08T04:33:19ZengSAGE PublishingProceedings of Singapore Healthcare2059-23292023-07-013210.1177/20101058231188865Treatment considerations in total anomalous pulmonary venous connectionEka Prasetya Budi MuliaMahrus A. RahmanBackground Total anomalous pulmonary venous connection (TAPVC) is a rare cyanotic abnormality that accounts for about 1%–3% of congenital heart disease malformations. TAPVC is a condition in which there is no direct connection between all four pulmonary veins and the left atrium but makes abnormal connections to the right atrium or systemic venous system. TAPVC caused a high mortality rate of 80% in the first year of life, and 50% of them die within 3 months after birth without intervention. Objectives The aim of this review is to elucidate the various treatment considerations of TAPVC. Methods A literature search was conducted on PubMed, ScienceDirect and Google Scholar using various combinations of keywords related to treatment of TAPVC. The citations from all selected articles were reviewed for additional studies. Results and Conclusion TAPVC intervention, including medical and surgical, is tailored to each type of TAPVC. Catheter-based interventions are frequently used to temporize neonates and provide time to optimize patients medically prior to definite repair. Corrective surgery is required for all patients with this condition. Several latest catheter-based or surgical intervention technique modifications have also been reported.https://doi.org/10.1177/20101058231188865 |
| spellingShingle | Eka Prasetya Budi Mulia Mahrus A. Rahman Treatment considerations in total anomalous pulmonary venous connection Proceedings of Singapore Healthcare |
| title | Treatment considerations in total anomalous pulmonary venous connection |
| title_full | Treatment considerations in total anomalous pulmonary venous connection |
| title_fullStr | Treatment considerations in total anomalous pulmonary venous connection |
| title_full_unstemmed | Treatment considerations in total anomalous pulmonary venous connection |
| title_short | Treatment considerations in total anomalous pulmonary venous connection |
| title_sort | treatment considerations in total anomalous pulmonary venous connection |
| url | https://doi.org/10.1177/20101058231188865 |
| work_keys_str_mv | AT ekaprasetyabudimulia treatmentconsiderationsintotalanomalouspulmonaryvenousconnection AT mahrusarahman treatmentconsiderationsintotalanomalouspulmonaryvenousconnection |