Oral management of poorly understood Papillon–Lefèvre syndrome – A case report
Rationale: Papillon-Lefèvre syndrome (PLS) is a rare genodermatosis with autosomal-recessive genetic inheritanceand has features mainly palmoplantar hyperkeratosis and rapidly progressing severe periodontitis leading to early loss of deciduous and permanent dentition. Patient Concerns: The patient i...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2022-01-01
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| Series: | SRM Journal of Research in Dental Sciences |
| Subjects: | |
| Online Access: | http://www.srmjrds.in/article.asp?issn=0976-433X;year=2022;volume=13;issue=3;spage=134;epage=137;aulast=Sharma |
| _version_ | 1811196461729185792 |
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| author | Deepak Sharma Nancy Changra Priyanka Kharbanda Shanta Negi Ankit Mahajan Suresh Kumar Sachdeva |
| author_facet | Deepak Sharma Nancy Changra Priyanka Kharbanda Shanta Negi Ankit Mahajan Suresh Kumar Sachdeva |
| author_sort | Deepak Sharma |
| collection | DOAJ |
| description | Rationale: Papillon-Lefèvre syndrome (PLS) is a rare genodermatosis with autosomal-recessive genetic inheritanceand has features mainly palmoplantar hyperkeratosis and rapidly progressing severe periodontitis leading to early loss of deciduous and permanent dentition. Patient Concerns: The patient in the presented report was concerned with loose teeth, gingival bleeding and oral malodour and wanted to get missing teeth replaced. Diagnosis: The diagnosis was made based on medical history, clinical and radiological findings. Interventions: Periodontal phase I therapy included extraction of hopeless teeth, manual and ultrasonic scaling, mechanical and chemical plaque control and periodic maintenance. Missing teeth were restored by removable and fixed prosthesis. Dermatological lesions were conservatively managed. Outcomes: A comprehensive treatment stabilised periodontal disease of the patient and prosthetic rehabilitation improved oral health related quality of life of PLS patient. Lessons: PLS patients require an early diagnosis and a team approach for dermatological, periodontal complications and prosthetic rehabilitation. |
| first_indexed | 2024-04-12T00:59:16Z |
| format | Article |
| id | doaj.art-a2e7f5f6b03c483b8b83a1cd370f7a36 |
| institution | Directory Open Access Journal |
| issn | 2772-5243 2772-5251 |
| language | English |
| last_indexed | 2024-04-12T00:59:16Z |
| publishDate | 2022-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | SRM Journal of Research in Dental Sciences |
| spelling | doaj.art-a2e7f5f6b03c483b8b83a1cd370f7a362022-12-22T03:54:32ZengWolters Kluwer Medknow PublicationsSRM Journal of Research in Dental Sciences2772-52432772-52512022-01-0113313413710.4103/srmjrds.srmjrds_40_22Oral management of poorly understood Papillon–Lefèvre syndrome – A case reportDeepak SharmaNancy ChangraPriyanka KharbandaShanta NegiAnkit MahajanSuresh Kumar SachdevaRationale: Papillon-Lefèvre syndrome (PLS) is a rare genodermatosis with autosomal-recessive genetic inheritanceand has features mainly palmoplantar hyperkeratosis and rapidly progressing severe periodontitis leading to early loss of deciduous and permanent dentition. Patient Concerns: The patient in the presented report was concerned with loose teeth, gingival bleeding and oral malodour and wanted to get missing teeth replaced. Diagnosis: The diagnosis was made based on medical history, clinical and radiological findings. Interventions: Periodontal phase I therapy included extraction of hopeless teeth, manual and ultrasonic scaling, mechanical and chemical plaque control and periodic maintenance. Missing teeth were restored by removable and fixed prosthesis. Dermatological lesions were conservatively managed. Outcomes: A comprehensive treatment stabilised periodontal disease of the patient and prosthetic rehabilitation improved oral health related quality of life of PLS patient. Lessons: PLS patients require an early diagnosis and a team approach for dermatological, periodontal complications and prosthetic rehabilitation.http://www.srmjrds.in/article.asp?issn=0976-433X;year=2022;volume=13;issue=3;spage=134;epage=137;aulast=Sharmacathepsin cgenodermatosiskeratodermapapillon–lefèvre syndromeperiodontitis |
| spellingShingle | Deepak Sharma Nancy Changra Priyanka Kharbanda Shanta Negi Ankit Mahajan Suresh Kumar Sachdeva Oral management of poorly understood Papillon–Lefèvre syndrome – A case report SRM Journal of Research in Dental Sciences cathepsin c genodermatosis keratoderma papillon–lefèvre syndrome periodontitis |
| title | Oral management of poorly understood Papillon–Lefèvre syndrome – A case report |
| title_full | Oral management of poorly understood Papillon–Lefèvre syndrome – A case report |
| title_fullStr | Oral management of poorly understood Papillon–Lefèvre syndrome – A case report |
| title_full_unstemmed | Oral management of poorly understood Papillon–Lefèvre syndrome – A case report |
| title_short | Oral management of poorly understood Papillon–Lefèvre syndrome – A case report |
| title_sort | oral management of poorly understood papillon lefevre syndrome a case report |
| topic | cathepsin c genodermatosis keratoderma papillon–lefèvre syndrome periodontitis |
| url | http://www.srmjrds.in/article.asp?issn=0976-433X;year=2022;volume=13;issue=3;spage=134;epage=137;aulast=Sharma |
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