Complications of the Low Phenylalanine Diet for Patients with Phenylketonuria and the Benefits of Increased Natural Protein

Complications of the Low Phenylalanine Diet for Patients with Phenylketonuria and the Benefits of Increased Natural Protein

Phenylketonuria (PKU) is an inherited disorder in which phenylalanine (Phe) is not correctly metabolized leading to an abnormally high plasma Phe concentration that causes profound neurologic damage if left untreated. The mainstay of treatment for PKU has centered around limiting natural protein in...

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Bibliographic Details
Main Authors: Nicole McWhorter, Mesaki K. Ndugga-Kabuye, Marja Puurunen, Sharon L. Ernst
Format: Article
Language:English
Published: MDPI AG 2022-11-01
Series:Nutrients
Subjects:
phenylketonuria (PKU)
natural protein intake
medical food
inborn errors of metabolism (IEM)
Online Access:https://www.mdpi.com/2072-6643/14/23/4960

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