Diffuse-Type Caroli Disease with Characteristic Central Dot Sign Complicated by Multiple Intrahepatic and Common Bile Duct Stones
Caroli disease (CD) is a rare congenital malformation of the liver characterized by non-obstructive, segmental, cystic dilatation of the intrahepatic bile ducts (IHDs). The clinical course is usually asymptomatic for the first 5–20 years, and symptoms may seldom occur throughout the patient’s life....
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| Format: | Article |
| Language: | English |
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Korean Society of Gastrointestinal Endoscopy
2017-07-01
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| Series: | Clinical Endoscopy |
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| Online Access: | http://www.e-ce.org/upload/pdf/ce-2016-150.pdf |
| _version_ | 1797425623630610432 |
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| author | Moon Joo Hwang Tae Nyeun Kim |
| author_facet | Moon Joo Hwang Tae Nyeun Kim |
| author_sort | Moon Joo Hwang |
| collection | DOAJ |
| description | Caroli disease (CD) is a rare congenital malformation of the liver characterized by non-obstructive, segmental, cystic dilatation of the intrahepatic bile ducts (IHDs). The clinical course is usually asymptomatic for the first 5–20 years, and symptoms may seldom occur throughout the patient’s life. Bile stagnation leads to recurrent episodes of cholangitis, stone formation, or liver abscesses, and biliary cirrhosis usually occurs years later. Here we report on a 42-year-old man diagnosed with diffuse-type CD with a characteristic central dot sign, who had multiple intrahepatic and common bile duct (CBD) stones. CBD stones were treated successfully with endoscopic retrograde cholangiopancreatography (ERCP). |
| first_indexed | 2024-03-09T08:18:46Z |
| format | Article |
| id | doaj.art-a35186d5ed354485aa32fceadfe2efa1 |
| institution | Directory Open Access Journal |
| issn | 2234-2400 2234-2443 |
| language | English |
| last_indexed | 2024-03-09T08:18:46Z |
| publishDate | 2017-07-01 |
| publisher | Korean Society of Gastrointestinal Endoscopy |
| record_format | Article |
| series | Clinical Endoscopy |
| spelling | doaj.art-a35186d5ed354485aa32fceadfe2efa12023-12-02T21:56:19ZengKorean Society of Gastrointestinal EndoscopyClinical Endoscopy2234-24002234-24432017-07-0150440040310.5946/ce.2016.1507002Diffuse-Type Caroli Disease with Characteristic Central Dot Sign Complicated by Multiple Intrahepatic and Common Bile Duct StonesMoon Joo HwangTae Nyeun KimCaroli disease (CD) is a rare congenital malformation of the liver characterized by non-obstructive, segmental, cystic dilatation of the intrahepatic bile ducts (IHDs). The clinical course is usually asymptomatic for the first 5–20 years, and symptoms may seldom occur throughout the patient’s life. Bile stagnation leads to recurrent episodes of cholangitis, stone formation, or liver abscesses, and biliary cirrhosis usually occurs years later. Here we report on a 42-year-old man diagnosed with diffuse-type CD with a characteristic central dot sign, who had multiple intrahepatic and common bile duct (CBD) stones. CBD stones were treated successfully with endoscopic retrograde cholangiopancreatography (ERCP).http://www.e-ce.org/upload/pdf/ce-2016-150.pdfCaroli diseaseCholedocholithiasisCentral dot signEndoscopic retrograde cholangiopancreatography |
| spellingShingle | Moon Joo Hwang Tae Nyeun Kim Diffuse-Type Caroli Disease with Characteristic Central Dot Sign Complicated by Multiple Intrahepatic and Common Bile Duct Stones Clinical Endoscopy Caroli disease Choledocholithiasis Central dot sign Endoscopic retrograde cholangiopancreatography |
| title | Diffuse-Type Caroli Disease with Characteristic Central Dot Sign Complicated by Multiple Intrahepatic and Common Bile Duct Stones |
| title_full | Diffuse-Type Caroli Disease with Characteristic Central Dot Sign Complicated by Multiple Intrahepatic and Common Bile Duct Stones |
| title_fullStr | Diffuse-Type Caroli Disease with Characteristic Central Dot Sign Complicated by Multiple Intrahepatic and Common Bile Duct Stones |
| title_full_unstemmed | Diffuse-Type Caroli Disease with Characteristic Central Dot Sign Complicated by Multiple Intrahepatic and Common Bile Duct Stones |
| title_short | Diffuse-Type Caroli Disease with Characteristic Central Dot Sign Complicated by Multiple Intrahepatic and Common Bile Duct Stones |
| title_sort | diffuse type caroli disease with characteristic central dot sign complicated by multiple intrahepatic and common bile duct stones |
| topic | Caroli disease Choledocholithiasis Central dot sign Endoscopic retrograde cholangiopancreatography |
| url | http://www.e-ce.org/upload/pdf/ce-2016-150.pdf |
| work_keys_str_mv | AT moonjoohwang diffusetypecarolidiseasewithcharacteristiccentraldotsigncomplicatedbymultipleintrahepaticandcommonbileductstones AT taenyeunkim diffusetypecarolidiseasewithcharacteristiccentraldotsigncomplicatedbymultipleintrahepaticandcommonbileductstones |