Data on phenylalanine-to-tyrosine ratios in assessment of tetrahydrobiopterin (BH4)-responsiveness in patients with hyperphenylalaninemia

Data on phenylalanine-to-tyrosine ratios in assessment of tetrahydrobiopterin (BH4)-responsiveness in patients with hyperphenylalaninemia

Blood phenylalanine-to-tyrosine (Phe/Tyr) ratio is an important indicator of metabolic control in phenylketonuria patients. We present the data that highlights the role of Phe/Tyr-ratio in the evaluation of tetrahydrobiopterin (BH4)-responsiveness in patients with hyperphenylalaninemia. Our data com...

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Bibliographic Details
Main Authors:	Barbka Repic Lampret, Mojca Zerjav Tansek, Blaz Groselj, Jaka Sikonja, Tadej Battelino, Urh Groselj
Format:	Article
Language:	English
Published:	Elsevier 2022-04-01
Series:	Data in Brief
Subjects:	Phenylketonuria Phenylalanine-to-tyrosine ratio Tetrahydrobiopterin BH4-responsiveness Hyperphenylalaninemia Tandem mass spectrometry
Online Access:	http://www.sciencedirect.com/science/article/pii/S235234092200138X

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