Kyphoscoliosis caused by lymphangiogenic form of Gorham – Stout disease with axial skeletal lesion

The paper presents a clinical observation of a child with lymphangiogenic form of spontaneous osteolysis (Gorham – Stout disease) associated with massive destruction of the rib cage and progressive kyphoscoliotic deformity. Staged surgical treatment under the therapy with osteoclast inhibitors r...

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Bibliographic Details
Main Authors: Aleksandr Yu. Mushkin, Igor A. Komolkin, Mikhail M. Kostik, Denis B. Malamashin
Format: Article
Language:English
Published: Ministry of Health of Russian Federation, Federal State Budgetary Institution "Novosibirsk Research Institute of Traumatology and Orthopaedics n.a. Ya.L. Tsivyan" 2017-06-01
Series:Хирургия позвоночника
Subjects:
Online Access:https://www.spinesurgery.ru/jour/article/view/119/425
Description
Summary:The paper presents a clinical observation of a child with lymphangiogenic form of spontaneous osteolysis (Gorham – Stout disease) associated with massive destruction of the rib cage and progressive kyphoscoliotic deformity. Staged surgical treatment under the therapy with osteoclast inhibitors resulted in the deformity correction and significant improvement in the quality of life. The prognosis remains unclear due to the risk of osteolysis progression.
ISSN:1810-8997
2313-1497