Complete androgen insensitivity syndrome with a large gonadal serous papillary cystadenofibroma
We present a patient with complete androgen insensitivity syndrome (CAIS) diagnosed with a serous papillary cystadenofibroma. A 41-year-old married female with a mass in the left inguinal region and a history of primary amenorrhea. A bulging mass of 13.7 cm × 8 cm × 12.4 cm in the left inguinal regi...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2014-01-01
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| Series: | Journal of Human Reproductive Sciences |
| Subjects: | |
| Online Access: | http://www.jhrsonline.org/article.asp?issn=0974-1208;year=2014;volume=7;issue=2;spage=148;epage=150;aulast=Ozdemir |
| _version_ | 1818553848169496576 |
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| author | Ozhan Ozdemir Mustafa Erkan Sari Evren Akmut Vafa Selimova Tugba Unal Cemal Resat Atalay |
| author_facet | Ozhan Ozdemir Mustafa Erkan Sari Evren Akmut Vafa Selimova Tugba Unal Cemal Resat Atalay |
| author_sort | Ozhan Ozdemir |
| collection | DOAJ |
| description | We present a patient with complete androgen insensitivity syndrome (CAIS) diagnosed with a serous papillary cystadenofibroma. A 41-year-old married female with a mass in the left inguinal region and a history of primary amenorrhea. A bulging mass of 13.7 cm × 8 cm × 12.4 cm in the left inguinal region extending from the hip joint to the level of labia majus, and a 3.2 cm × 2.8 cm mass in her right inguinal region were found by ultrasonography and magnetic resonance imaging. We performed bilateral gonadectomy. The pathology showed testicular tissue in the right inguinal mass and a serous papillary cystadenofibroma in the left one. CAIS is an infrequent clinical entity, occurrence of serous papillary cystadenofibroma is even rarer in this syndrome serous cystadenofibroma should come to mind in patients with a huge inguinal mass. Gonadectomy should be performed right after puberty to prevent the risk of malignancy development in the testes. |
| first_indexed | 2024-12-12T09:31:11Z |
| format | Article |
| id | doaj.art-a55219a3a62d4f22a47660dc2022e5f3 |
| institution | Directory Open Access Journal |
| issn | 0974-1208 1998-4766 |
| language | English |
| last_indexed | 2024-12-12T09:31:11Z |
| publishDate | 2014-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of Human Reproductive Sciences |
| spelling | doaj.art-a55219a3a62d4f22a47660dc2022e5f32022-12-22T00:28:52ZengWolters Kluwer Medknow PublicationsJournal of Human Reproductive Sciences0974-12081998-47662014-01-017214815010.4103/0974-1208.138875Complete androgen insensitivity syndrome with a large gonadal serous papillary cystadenofibromaOzhan OzdemirMustafa Erkan SariEvren AkmutVafa SelimovaTugba UnalCemal Resat AtalayWe present a patient with complete androgen insensitivity syndrome (CAIS) diagnosed with a serous papillary cystadenofibroma. A 41-year-old married female with a mass in the left inguinal region and a history of primary amenorrhea. A bulging mass of 13.7 cm × 8 cm × 12.4 cm in the left inguinal region extending from the hip joint to the level of labia majus, and a 3.2 cm × 2.8 cm mass in her right inguinal region were found by ultrasonography and magnetic resonance imaging. We performed bilateral gonadectomy. The pathology showed testicular tissue in the right inguinal mass and a serous papillary cystadenofibroma in the left one. CAIS is an infrequent clinical entity, occurrence of serous papillary cystadenofibroma is even rarer in this syndrome serous cystadenofibroma should come to mind in patients with a huge inguinal mass. Gonadectomy should be performed right after puberty to prevent the risk of malignancy development in the testes.http://www.jhrsonline.org/article.asp?issn=0974-1208;year=2014;volume=7;issue=2;spage=148;epage=150;aulast=OzdemirComplete androgen insensitivity syndromecystadenofibromagonadal tumoringuinal massprimary amenorrhea |
| spellingShingle | Ozhan Ozdemir Mustafa Erkan Sari Evren Akmut Vafa Selimova Tugba Unal Cemal Resat Atalay Complete androgen insensitivity syndrome with a large gonadal serous papillary cystadenofibroma Journal of Human Reproductive Sciences Complete androgen insensitivity syndrome cystadenofibroma gonadal tumor inguinal mass primary amenorrhea |
| title | Complete androgen insensitivity syndrome with a large gonadal serous papillary cystadenofibroma |
| title_full | Complete androgen insensitivity syndrome with a large gonadal serous papillary cystadenofibroma |
| title_fullStr | Complete androgen insensitivity syndrome with a large gonadal serous papillary cystadenofibroma |
| title_full_unstemmed | Complete androgen insensitivity syndrome with a large gonadal serous papillary cystadenofibroma |
| title_short | Complete androgen insensitivity syndrome with a large gonadal serous papillary cystadenofibroma |
| title_sort | complete androgen insensitivity syndrome with a large gonadal serous papillary cystadenofibroma |
| topic | Complete androgen insensitivity syndrome cystadenofibroma gonadal tumor inguinal mass primary amenorrhea |
| url | http://www.jhrsonline.org/article.asp?issn=0974-1208;year=2014;volume=7;issue=2;spage=148;epage=150;aulast=Ozdemir |
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