Dural ectasia: a manifestation of type 1 neurofibromatosis
Dural ectasia denotes circumferential expansion or dilatation of the dural sac, and has been frequently reported in association with type 1 neurofibromatosis (NF1). The pathogenesis has not been defined, but its correlation with NF1 infers a congenital malformative hypothesis. The neural elements in...
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| Format: | Article |
| Language: | English |
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The Pan African Medical Journal
2018-12-01
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| Series: | The Pan African Medical Journal |
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| Online Access: |
https://www.panafrican-med-journal.com/content/article/31/226/pdf/226.pdf
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| _version_ | 1818916767723945984 |
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| author | Ilyas Derdabi Hajar El Jouadi Meryem Edderai |
| author_facet | Ilyas Derdabi Hajar El Jouadi Meryem Edderai |
| author_sort | Ilyas Derdabi |
| collection | DOAJ |
| description | Dural ectasia denotes circumferential expansion or dilatation of the dural sac, and has been frequently reported in association with type 1 neurofibromatosis (NF1). The pathogenesis has not been defined, but its correlation with NF1 infers a congenital malformative hypothesis. The neural elements in the dilated sleeve typically are not enlarged or abnormal, nevertheless the enlarged area contain an increased amount of cerebrospinal fluid. The dura in the area of ectasia is extremely thin and fragile, and erodes the surrounding bony structures destabilising the spine and permitting spectacular spinal deformities. We present a case: a 40-year-old woman suffering from neurofibromatosis type 1 who developed a thoracic dural ectasia and anterior meningocele. |
| first_indexed | 2024-12-20T00:23:25Z |
| format | Article |
| id | doaj.art-a5cdd6dc4c374d12b7960ff94422116f |
| institution | Directory Open Access Journal |
| issn | 1937-8688 1937-8688 |
| language | English |
| last_indexed | 2024-12-20T00:23:25Z |
| publishDate | 2018-12-01 |
| publisher | The Pan African Medical Journal |
| record_format | Article |
| series | The Pan African Medical Journal |
| spelling | doaj.art-a5cdd6dc4c374d12b7960ff94422116f2022-12-21T20:00:08ZengThe Pan African Medical JournalThe Pan African Medical Journal1937-86881937-86882018-12-013122610.11604/pamj.2018.31.226.97979797Dural ectasia: a manifestation of type 1 neurofibromatosisIlyas Derdabi0Hajar El Jouadi1Meryem Edderai2 Department of Radiology, Hospital Mohammed V, Rabat, Morocco Department of Radiology, Hospital Mohammed V, Rabat, Morocco Department of Radiology, Hospital Mohammed V, Rabat, Morocco Dural ectasia denotes circumferential expansion or dilatation of the dural sac, and has been frequently reported in association with type 1 neurofibromatosis (NF1). The pathogenesis has not been defined, but its correlation with NF1 infers a congenital malformative hypothesis. The neural elements in the dilated sleeve typically are not enlarged or abnormal, nevertheless the enlarged area contain an increased amount of cerebrospinal fluid. The dura in the area of ectasia is extremely thin and fragile, and erodes the surrounding bony structures destabilising the spine and permitting spectacular spinal deformities. We present a case: a 40-year-old woman suffering from neurofibromatosis type 1 who developed a thoracic dural ectasia and anterior meningocele. https://www.panafrican-med-journal.com/content/article/31/226/pdf/226.pdf dural ectasianeurofibromatosis type 1anterior meningocele |
| spellingShingle | Ilyas Derdabi Hajar El Jouadi Meryem Edderai Dural ectasia: a manifestation of type 1 neurofibromatosis The Pan African Medical Journal dural ectasia neurofibromatosis type 1 anterior meningocele |
| title | Dural ectasia: a manifestation of type 1 neurofibromatosis |
| title_full | Dural ectasia: a manifestation of type 1 neurofibromatosis |
| title_fullStr | Dural ectasia: a manifestation of type 1 neurofibromatosis |
| title_full_unstemmed | Dural ectasia: a manifestation of type 1 neurofibromatosis |
| title_short | Dural ectasia: a manifestation of type 1 neurofibromatosis |
| title_sort | dural ectasia a manifestation of type 1 neurofibromatosis |
| topic | dural ectasia neurofibromatosis type 1 anterior meningocele |
| url |
https://www.panafrican-med-journal.com/content/article/31/226/pdf/226.pdf
|
| work_keys_str_mv | AT ilyasderdabi duralectasiaamanifestationoftype1neurofibromatosis AT hajareljouadi duralectasiaamanifestationoftype1neurofibromatosis AT meryemedderai duralectasiaamanifestationoftype1neurofibromatosis |