Desmoplastic small round cell tumor of the lung: A case report and literature review

Desmoplastic small round cell tumor (DSRCT) is a rare, aggressive and malignant tumor that is characterized by nests of small tumor cells surrounded by a cellular and vascular collagenous stroma and predominantly affects young adolescent males. This tumor most commonly originates in the abdomen; how...

Full description

Bibliographic Details
Main Authors: Miguel Angel Ariza-Prota, Ana Pando-Sandoval, David Fole-Vázquez, Pere Casan
Format: Article
Language:English
Published: Elsevier 2015-01-01
Series:Respiratory Medicine Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2213007115300319
_version_ 1811270627260104704
author Miguel Angel Ariza-Prota
Ana Pando-Sandoval
David Fole-Vázquez
Pere Casan
author_facet Miguel Angel Ariza-Prota
Ana Pando-Sandoval
David Fole-Vázquez
Pere Casan
author_sort Miguel Angel Ariza-Prota
collection DOAJ
description Desmoplastic small round cell tumor (DSRCT) is a rare, aggressive and malignant tumor that is characterized by nests of small tumor cells surrounded by a cellular and vascular collagenous stroma and predominantly affects young adolescent males. This tumor most commonly originates in the abdomen; however, in rare cases, DSRCT can originate in other body regions. The main manifestations of DSRCT are chest pain and respiratory symptoms, and patients' average survival after diagnosis is less than two years. In this report, we describe a case involving DSRCT of the lung that proved to be difficult to diagnose, and we conduct a literature review.
first_indexed 2024-04-12T22:05:37Z
format Article
id doaj.art-a62e351729ee47a5ac24341718ddc4eb
institution Directory Open Access Journal
issn 2213-0071
language English
last_indexed 2024-04-12T22:05:37Z
publishDate 2015-01-01
publisher Elsevier
record_format Article
series Respiratory Medicine Case Reports
spelling doaj.art-a62e351729ee47a5ac24341718ddc4eb2022-12-22T03:14:57ZengElsevierRespiratory Medicine Case Reports2213-00712015-01-0116C11211610.1016/j.rmcr.2015.08.010Desmoplastic small round cell tumor of the lung: A case report and literature reviewMiguel Angel Ariza-ProtaAna Pando-SandovalDavid Fole-VázquezPere CasanDesmoplastic small round cell tumor (DSRCT) is a rare, aggressive and malignant tumor that is characterized by nests of small tumor cells surrounded by a cellular and vascular collagenous stroma and predominantly affects young adolescent males. This tumor most commonly originates in the abdomen; however, in rare cases, DSRCT can originate in other body regions. The main manifestations of DSRCT are chest pain and respiratory symptoms, and patients' average survival after diagnosis is less than two years. In this report, we describe a case involving DSRCT of the lung that proved to be difficult to diagnose, and we conduct a literature review.http://www.sciencedirect.com/science/article/pii/S2213007115300319Desmoplastic small round cell tumorLung cancerPleural effusion
spellingShingle Miguel Angel Ariza-Prota
Ana Pando-Sandoval
David Fole-Vázquez
Pere Casan
Desmoplastic small round cell tumor of the lung: A case report and literature review
Respiratory Medicine Case Reports
Desmoplastic small round cell tumor
Lung cancer
Pleural effusion
title Desmoplastic small round cell tumor of the lung: A case report and literature review
title_full Desmoplastic small round cell tumor of the lung: A case report and literature review
title_fullStr Desmoplastic small round cell tumor of the lung: A case report and literature review
title_full_unstemmed Desmoplastic small round cell tumor of the lung: A case report and literature review
title_short Desmoplastic small round cell tumor of the lung: A case report and literature review
title_sort desmoplastic small round cell tumor of the lung a case report and literature review
topic Desmoplastic small round cell tumor
Lung cancer
Pleural effusion
url http://www.sciencedirect.com/science/article/pii/S2213007115300319
work_keys_str_mv AT miguelangelarizaprota desmoplasticsmallroundcelltumorofthelungacasereportandliteraturereview
AT anapandosandoval desmoplasticsmallroundcelltumorofthelungacasereportandliteraturereview
AT davidfolevazquez desmoplasticsmallroundcelltumorofthelungacasereportandliteraturereview
AT perecasan desmoplasticsmallroundcelltumorofthelungacasereportandliteraturereview