Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient
Shone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows: parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete forms with 2 or 3 of these lesions in adult patients have been rarely repor...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Korean Society for Thoracic and Cardiovascular Surgery
2019-04-01
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| Series: | Korean Journal of Thoracic and Cardiovascular Surgery |
| Subjects: |
| _version_ | 1818510912763461632 |
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| author | Beatrice Chia-Hui Shih Jae Hong Lim Jooncheol Min Eung Re Kim Jae Gun Kwak Woong-Han Kim |
| author_facet | Beatrice Chia-Hui Shih Jae Hong Lim Jooncheol Min Eung Re Kim Jae Gun Kwak Woong-Han Kim |
| author_sort | Beatrice Chia-Hui Shih |
| collection | DOAJ |
| description | Shone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows:
parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete
forms with 2 or 3 of these lesions in adult patients have been rarely reported in the literature, meaning
that insufficient general data exist concerning the surgical strategy and clinical follow-up. Herein, we report
the case of a 31-year-old woman with a diagnosis of incomplete form of Shone complex with parachute mitral
valve and coarctation of the aorta who underwent successful single-stage surgical repair. |
| first_indexed | 2024-12-10T23:26:32Z |
| format | Article |
| id | doaj.art-a6b5f3340e2045c9ae6efadda619cfab |
| institution | Directory Open Access Journal |
| issn | 2233-601X 2093-6516 |
| language | English |
| last_indexed | 2024-12-10T23:26:32Z |
| publishDate | 2019-04-01 |
| publisher | Korean Society for Thoracic and Cardiovascular Surgery |
| record_format | Article |
| series | Korean Journal of Thoracic and Cardiovascular Surgery |
| spelling | doaj.art-a6b5f3340e2045c9ae6efadda619cfab2022-12-22T01:29:35ZengKorean Society for Thoracic and Cardiovascular SurgeryKorean Journal of Thoracic and Cardiovascular Surgery2233-601X2093-65162019-04-0152210010410.5090/kjtcs.2019.52.2.100Incomplete Form of Shone Complex in an Adult Congenital Heart Disease PatientBeatrice Chia-Hui Shih0Jae Hong Lim1Jooncheol Min2Eung Re Kim3Jae Gun Kwak4Woong-Han Kim5Seoul National University Children’s Hospital, Seoul National University College of Medicine, Seoul, KoreaSeoul National University Children’s Hospital, Seoul National University College of Medicine, Seoul, KoreaSeoul National University Children’s Hospital, Seoul National University College of Medicine, Seoul, KoreaSeoul National University Children’s Hospital, Seoul National University College of Medicine, Seoul, KoreaSeoul National University Children’s Hospital, Seoul National University College of Medicine, Seoul, KoreaSeoul National University Children’s Hospital, Seoul National University College of Medicine, Seoul, KoreaShone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows: parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete forms with 2 or 3 of these lesions in adult patients have been rarely reported in the literature, meaning that insufficient general data exist concerning the surgical strategy and clinical follow-up. Herein, we report the case of a 31-year-old woman with a diagnosis of incomplete form of Shone complex with parachute mitral valve and coarctation of the aorta who underwent successful single-stage surgical repair.Shone’s complexBicuspid aortic valveParachute mitral valveExtraanatomic bypassAortic coarctation |
| spellingShingle | Beatrice Chia-Hui Shih Jae Hong Lim Jooncheol Min Eung Re Kim Jae Gun Kwak Woong-Han Kim Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient Korean Journal of Thoracic and Cardiovascular Surgery Shone’s complex Bicuspid aortic valve Parachute mitral valve Extraanatomic bypass Aortic coarctation |
| title | Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient |
| title_full | Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient |
| title_fullStr | Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient |
| title_full_unstemmed | Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient |
| title_short | Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient |
| title_sort | incomplete form of shone complex in an adult congenital heart disease patient |
| topic | Shone’s complex Bicuspid aortic valve Parachute mitral valve Extraanatomic bypass Aortic coarctation |
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