Monolobar Caroli’s disease with renal cysts: Case report
Caroli’s disease is autosomal recessive, non-obstructive dilatation of intrahepatic biliary ducts. The exact etiology is unclear. Two variants of Caroli’s disease are well known-simple; in which bile ducts are dilated without hepatic fibrosis and the second type which is associated with congenital h...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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SpringerOpen
2014-03-01
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| Series: | The Egyptian Journal of Radiology and Nuclear Medicine |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S0378603X13001393 |
| _version_ | 1819076881446600704 |
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| author | Shruti Thakur Sushma Makhaik Arun Chauhan Anupam Jhobta Charu S. Thakur R.G. Sood |
| author_facet | Shruti Thakur Sushma Makhaik Arun Chauhan Anupam Jhobta Charu S. Thakur R.G. Sood |
| author_sort | Shruti Thakur |
| collection | DOAJ |
| description | Caroli’s disease is autosomal recessive, non-obstructive dilatation of intrahepatic biliary ducts. The exact etiology is unclear. Two variants of Caroli’s disease are well known-simple; in which bile ducts are dilated without hepatic fibrosis and the second type which is associated with congenital hepatic fibrosis along with its sequelae, also known as Caroli’s syndrome. Simple Caroli’s disease without hepatic fibrosis is quite rare. The importance of recognizing this disease as a cause of biliary stasis is its frequent association with lithiasis, recurrent cholangitis, liver abscesses, cirrhosis and cholangiocarcinoma. |
| first_indexed | 2024-12-21T18:48:21Z |
| format | Article |
| id | doaj.art-a78312e463b84389a163856bcd3d78cf |
| institution | Directory Open Access Journal |
| issn | 0378-603X |
| language | English |
| last_indexed | 2024-12-21T18:48:21Z |
| publishDate | 2014-03-01 |
| publisher | SpringerOpen |
| record_format | Article |
| series | The Egyptian Journal of Radiology and Nuclear Medicine |
| spelling | doaj.art-a78312e463b84389a163856bcd3d78cf2022-12-21T18:53:49ZengSpringerOpenThe Egyptian Journal of Radiology and Nuclear Medicine0378-603X2014-03-01451495210.1016/j.ejrnm.2013.10.007Monolobar Caroli’s disease with renal cysts: Case reportShruti ThakurSushma MakhaikArun ChauhanAnupam JhobtaCharu S. ThakurR.G. SoodCaroli’s disease is autosomal recessive, non-obstructive dilatation of intrahepatic biliary ducts. The exact etiology is unclear. Two variants of Caroli’s disease are well known-simple; in which bile ducts are dilated without hepatic fibrosis and the second type which is associated with congenital hepatic fibrosis along with its sequelae, also known as Caroli’s syndrome. Simple Caroli’s disease without hepatic fibrosis is quite rare. The importance of recognizing this disease as a cause of biliary stasis is its frequent association with lithiasis, recurrent cholangitis, liver abscesses, cirrhosis and cholangiocarcinoma.http://www.sciencedirect.com/science/article/pii/S0378603X13001393Caroli’s diseaseIntrahepaticCholangitisCholangiocarcinoma |
| spellingShingle | Shruti Thakur Sushma Makhaik Arun Chauhan Anupam Jhobta Charu S. Thakur R.G. Sood Monolobar Caroli’s disease with renal cysts: Case report The Egyptian Journal of Radiology and Nuclear Medicine Caroli’s disease Intrahepatic Cholangitis Cholangiocarcinoma |
| title | Monolobar Caroli’s disease with renal cysts: Case report |
| title_full | Monolobar Caroli’s disease with renal cysts: Case report |
| title_fullStr | Monolobar Caroli’s disease with renal cysts: Case report |
| title_full_unstemmed | Monolobar Caroli’s disease with renal cysts: Case report |
| title_short | Monolobar Caroli’s disease with renal cysts: Case report |
| title_sort | monolobar caroli s disease with renal cysts case report |
| topic | Caroli’s disease Intrahepatic Cholangitis Cholangiocarcinoma |
| url | http://www.sciencedirect.com/science/article/pii/S0378603X13001393 |
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