Plausible predicament in emergency endodontic rehabilitation of a child with Sturge-Weber syndrome: A case report
Sturge–Weber Syndrome (SWS) is a neuro-oculo-cutaneous vascular disorder that includes leptomeningeal hemangioma and port wine stains, usually ipsilaterally, with ocular manifestations and extended lesions over the oral cavity. It is an embryonic developmental disorder affecting both mesodermal and...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Arbu Academic Publishing
2022-08-01
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| Series: | Contemporary Pediatric Dentistry |
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| _version_ | 1827832864232701952 |
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| author | Amit Khatri Namita Kalra Rishi Tyagi Khadeeja Kulood M Mayank Sharma Drishti Kaushal |
| author_facet | Amit Khatri Namita Kalra Rishi Tyagi Khadeeja Kulood M Mayank Sharma Drishti Kaushal |
| author_sort | Amit Khatri |
| collection | DOAJ |
| description | Sturge–Weber Syndrome (SWS) is a neuro-oculo-cutaneous vascular disorder that includes leptomeningeal hemangioma and port wine stains, usually ipsilaterally, with ocular manifestations and extended lesions over the oral cavity. It is an embryonic developmental disorder affecting both mesodermal and ectodermal germ layers, associated with somatic mutation of gene GNAQ. It has a sporadic occurrence of 1:50,000 and no gender predilection. This case report added to the knowledge and understanding of systematic rehabilitation of a child patient with SWS and its associated risk factors in an emergency scenario. A 3.5-year-old girl child with a known diagnosis of SWS presented abscess over the right lower mandibular deciduous teeth and distinct oral features of SWS, requiring emergency endodontic intervention, followed by full mouth rehabilitation. Thus, an in-depth knowledge of the clinical state that helps in the expert assessment of dental interventions, including emotional co-regulation in those children, is essential. |
| first_indexed | 2024-03-12T05:21:00Z |
| format | Article |
| id | doaj.art-a950f362af4f4dde846b1beb5be8bb4e |
| institution | Directory Open Access Journal |
| issn | 2757-5705 |
| language | English |
| last_indexed | 2024-03-12T05:21:00Z |
| publishDate | 2022-08-01 |
| publisher | Arbu Academic Publishing |
| record_format | Article |
| series | Contemporary Pediatric Dentistry |
| spelling | doaj.art-a950f362af4f4dde846b1beb5be8bb4e2023-09-03T07:43:21ZengArbu Academic PublishingContemporary Pediatric Dentistry2757-57052022-08-0132869110.51463/cpd.2022.97Plausible predicament in emergency endodontic rehabilitation of a child with Sturge-Weber syndrome: A case reportAmit Khatri0https://orcid.org/0000-0001-8071-0501Namita Kalra1https://orcid.org/0000-0001-6216-827XRishi Tyagi2https://orcid.org/0000-0003-4467-961XKhadeeja Kulood M3https://orcid.org/0000-0003-3838-740XMayank Sharma4https://orcid.org/0000-0002-4886-5834Drishti Kaushal5https://orcid.org/0000-0003-4763-3406University College of Medical SciencesUniversity College of Medical SciencesUniversity College of Medical SciencesUniversity College of Medical SciencesUniversity College of Medical SciencesUniversity College of Medical SciencesSturge–Weber Syndrome (SWS) is a neuro-oculo-cutaneous vascular disorder that includes leptomeningeal hemangioma and port wine stains, usually ipsilaterally, with ocular manifestations and extended lesions over the oral cavity. It is an embryonic developmental disorder affecting both mesodermal and ectodermal germ layers, associated with somatic mutation of gene GNAQ. It has a sporadic occurrence of 1:50,000 and no gender predilection. This case report added to the knowledge and understanding of systematic rehabilitation of a child patient with SWS and its associated risk factors in an emergency scenario. A 3.5-year-old girl child with a known diagnosis of SWS presented abscess over the right lower mandibular deciduous teeth and distinct oral features of SWS, requiring emergency endodontic intervention, followed by full mouth rehabilitation. Thus, an in-depth knowledge of the clinical state that helps in the expert assessment of dental interventions, including emotional co-regulation in those children, is essential.angiomatosisendodonticsport wine stainsyndrome |
| spellingShingle | Amit Khatri Namita Kalra Rishi Tyagi Khadeeja Kulood M Mayank Sharma Drishti Kaushal Plausible predicament in emergency endodontic rehabilitation of a child with Sturge-Weber syndrome: A case report Contemporary Pediatric Dentistry angiomatosis endodontics port wine stain syndrome |
| title | Plausible predicament in emergency endodontic rehabilitation of a child with Sturge-Weber syndrome: A case report |
| title_full | Plausible predicament in emergency endodontic rehabilitation of a child with Sturge-Weber syndrome: A case report |
| title_fullStr | Plausible predicament in emergency endodontic rehabilitation of a child with Sturge-Weber syndrome: A case report |
| title_full_unstemmed | Plausible predicament in emergency endodontic rehabilitation of a child with Sturge-Weber syndrome: A case report |
| title_short | Plausible predicament in emergency endodontic rehabilitation of a child with Sturge-Weber syndrome: A case report |
| title_sort | plausible predicament in emergency endodontic rehabilitation of a child with sturge weber syndrome a case report |
| topic | angiomatosis endodontics port wine stain syndrome |
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