Successful repair of a spontaneous scleral rupture in a patient with type VI Ehlers-Danlos syndrome
Purpose: To describe ocular findings in a patient with Type VI Ehlers-Danlos syndrome (EDS) and make ophthalmologists aware of the potential ophthalmic complications of this particular type of EDS. To briefly report the surgical technique utilized for the repair of spontaneous scleral rupture that m...
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| Format: | Article |
| Language: | English |
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Elsevier
2020-12-01
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| Series: | American Journal of Ophthalmology Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2451993620302760 |
| _version_ | 1818392699784396800 |
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| author | Rosa Lozada, MD Claudia Amaral, B.S. Samuel Alvarez-Falcón, B.S. Natalio J. Izquierdo, MD Armando L. Oliver, MD |
| author_facet | Rosa Lozada, MD Claudia Amaral, B.S. Samuel Alvarez-Falcón, B.S. Natalio J. Izquierdo, MD Armando L. Oliver, MD |
| author_sort | Rosa Lozada, MD |
| collection | DOAJ |
| description | Purpose: To describe ocular findings in a patient with Type VI Ehlers-Danlos syndrome (EDS) and make ophthalmologists aware of the potential ophthalmic complications of this particular type of EDS. To briefly report the surgical technique utilized for the repair of spontaneous scleral rupture that may be associated with Type VI Ehlers-Danlos syndrome. Observations: A 36-year-old female visited the Emergency Room due to sudden vision loss, edema, and redness of the right eye consistent with spontaneous scleral rupture secondary to scleral thinning due to Type VI EDS. Repair with scleral patch graft resulted in improvement in visual acuity, a decrease in hyphema, and discomfort resolution. Conclusions and Importance: Spontaneous scleral perforation may occur in patients with Type VI EDS. A scleral patch graft may serve as a viable surgical repair alternative for such patients. |
| first_indexed | 2024-12-14T05:33:34Z |
| format | Article |
| id | doaj.art-aa27694f2df84886b935369d9b4ec906 |
| institution | Directory Open Access Journal |
| issn | 2451-9936 |
| language | English |
| last_indexed | 2024-12-14T05:33:34Z |
| publishDate | 2020-12-01 |
| publisher | Elsevier |
| record_format | Article |
| series | American Journal of Ophthalmology Case Reports |
| spelling | doaj.art-aa27694f2df84886b935369d9b4ec9062022-12-21T23:15:16ZengElsevierAmerican Journal of Ophthalmology Case Reports2451-99362020-12-0120100961Successful repair of a spontaneous scleral rupture in a patient with type VI Ehlers-Danlos syndromeRosa Lozada, MD0Claudia Amaral, B.S.1Samuel Alvarez-Falcón, B.S.2Natalio J. Izquierdo, MD3Armando L. Oliver, MD4University of Puerto Rico, Department of Ophthalmology, Medical Sciences Campus, San Juan, PR, USAUniversity of Puerto Rico School of Medicine, Medical Sciences Campus, San Juan, PR, USAUniversity of Puerto Rico School of Medicine, Medical Sciences Campus, San Juan, PR, USAUniversity of Puerto Rico, Department of Surgery, School of Medicine, Medical Sciences Campus, San Juan, PR, USAUniversity of Puerto Rico, Department of Ophthalmology, Medical Sciences Campus, San Juan, PR, USA; Corresponding author. UPR Department of Ophthalmology, PO BOX 3650689, San Juan, PR, 00936, USA.Purpose: To describe ocular findings in a patient with Type VI Ehlers-Danlos syndrome (EDS) and make ophthalmologists aware of the potential ophthalmic complications of this particular type of EDS. To briefly report the surgical technique utilized for the repair of spontaneous scleral rupture that may be associated with Type VI Ehlers-Danlos syndrome. Observations: A 36-year-old female visited the Emergency Room due to sudden vision loss, edema, and redness of the right eye consistent with spontaneous scleral rupture secondary to scleral thinning due to Type VI EDS. Repair with scleral patch graft resulted in improvement in visual acuity, a decrease in hyphema, and discomfort resolution. Conclusions and Importance: Spontaneous scleral perforation may occur in patients with Type VI EDS. A scleral patch graft may serve as a viable surgical repair alternative for such patients.http://www.sciencedirect.com/science/article/pii/S2451993620302760Ehlers danlos syndromeScleral ruptureScleral patch graft |
| spellingShingle | Rosa Lozada, MD Claudia Amaral, B.S. Samuel Alvarez-Falcón, B.S. Natalio J. Izquierdo, MD Armando L. Oliver, MD Successful repair of a spontaneous scleral rupture in a patient with type VI Ehlers-Danlos syndrome American Journal of Ophthalmology Case Reports Ehlers danlos syndrome Scleral rupture Scleral patch graft |
| title | Successful repair of a spontaneous scleral rupture in a patient with type VI Ehlers-Danlos syndrome |
| title_full | Successful repair of a spontaneous scleral rupture in a patient with type VI Ehlers-Danlos syndrome |
| title_fullStr | Successful repair of a spontaneous scleral rupture in a patient with type VI Ehlers-Danlos syndrome |
| title_full_unstemmed | Successful repair of a spontaneous scleral rupture in a patient with type VI Ehlers-Danlos syndrome |
| title_short | Successful repair of a spontaneous scleral rupture in a patient with type VI Ehlers-Danlos syndrome |
| title_sort | successful repair of a spontaneous scleral rupture in a patient with type vi ehlers danlos syndrome |
| topic | Ehlers danlos syndrome Scleral rupture Scleral patch graft |
| url | http://www.sciencedirect.com/science/article/pii/S2451993620302760 |
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