Congenitally corrected transposition of great vessels with infundibular pulmonary stenosis with ventricular septal defect, presenting with atypical atrioventricular nodal reentrant tachycardia: a rare association

Ashwin Kodliwadmath Department of Medicine, Belgaum Institute of Medical Sciences, Belgaum, Karnataka, India Abstract: Congenitally corrected transposition of great vessels (CCTGV) is a rare congenital heart disease (CHD) accounting for <1% of CHDs. CCTGV with infundibular pulmonary stenosis...

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Main Author: Kodliwadmath A
Format: Article
Language:English
Published: Dove Medical Press 2017-09-01
Series:International Medical Case Reports Journal
Subjects:
Online Access:https://www.dovepress.com/congenitally-corrected-transposition-of-great-vessels-with-infundibula-peer-reviewed-article-IMCRJ
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author Kodliwadmath A
author_facet Kodliwadmath A
author_sort Kodliwadmath A
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description Ashwin Kodliwadmath Department of Medicine, Belgaum Institute of Medical Sciences, Belgaum, Karnataka, India Abstract: Congenitally corrected transposition of great vessels (CCTGV) is a rare congenital heart disease (CHD) accounting for <1% of CHDs. CCTGV with infundibular pulmonary stenosis (PS) with ventricular septal defect (VSD) is part of Fallot’s physiology. It is known to be associated with bradyarrhythmias like atrioventricular (AV) blocks, and acquired complete AV block occurs at a rate of 2% per year. Patients can have left-sided accessory pathways, which may cause atrioventricular reentrant tachycardia (AVRT). Tachyarrhythmias like atrioventricular nodal reentrant tachycardia (AVNRT) are very rare in such patients. A 30-year-old woman, a known case of CCTGV with PS with VSD, not corrected surgically and not on any drugs, presented with the syndrome of paroxysmal supraventricular tachycardia without hemodynamic compromise. Electrocardiogram showed atypical AVNRT. She was pharmacologically cardioverted to normal sinus rhythm with adenosine. CTGV with PS with VSD known to be associated with AV blocks, and preexcitation can sometimes present with atypical AVNRT. Keywords: supraventricular tachycardia, Fallot’s physiology, congenitally corrected transposition of great vessels
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spelling doaj.art-aa7a075524314c1ab77675274b59c5f12022-12-22T00:03:47ZengDove Medical PressInternational Medical Case Reports Journal1179-142X2017-09-01Volume 1031932234849Congenitally corrected transposition of great vessels with infundibular pulmonary stenosis with ventricular septal defect, presenting with atypical atrioventricular nodal reentrant tachycardia: a rare associationKodliwadmath AAshwin Kodliwadmath Department of Medicine, Belgaum Institute of Medical Sciences, Belgaum, Karnataka, India Abstract: Congenitally corrected transposition of great vessels (CCTGV) is a rare congenital heart disease (CHD) accounting for <1% of CHDs. CCTGV with infundibular pulmonary stenosis (PS) with ventricular septal defect (VSD) is part of Fallot’s physiology. It is known to be associated with bradyarrhythmias like atrioventricular (AV) blocks, and acquired complete AV block occurs at a rate of 2% per year. Patients can have left-sided accessory pathways, which may cause atrioventricular reentrant tachycardia (AVRT). Tachyarrhythmias like atrioventricular nodal reentrant tachycardia (AVNRT) are very rare in such patients. A 30-year-old woman, a known case of CCTGV with PS with VSD, not corrected surgically and not on any drugs, presented with the syndrome of paroxysmal supraventricular tachycardia without hemodynamic compromise. Electrocardiogram showed atypical AVNRT. She was pharmacologically cardioverted to normal sinus rhythm with adenosine. CTGV with PS with VSD known to be associated with AV blocks, and preexcitation can sometimes present with atypical AVNRT. Keywords: supraventricular tachycardia, Fallot’s physiology, congenitally corrected transposition of great vesselshttps://www.dovepress.com/congenitally-corrected-transposition-of-great-vessels-with-infundibula-peer-reviewed-article-IMCRJSupraventricular tachycardiaFallot’s physiology
spellingShingle Kodliwadmath A
Congenitally corrected transposition of great vessels with infundibular pulmonary stenosis with ventricular septal defect, presenting with atypical atrioventricular nodal reentrant tachycardia: a rare association
International Medical Case Reports Journal
Supraventricular tachycardia
Fallot’s physiology
title Congenitally corrected transposition of great vessels with infundibular pulmonary stenosis with ventricular septal defect, presenting with atypical atrioventricular nodal reentrant tachycardia: a rare association
title_full Congenitally corrected transposition of great vessels with infundibular pulmonary stenosis with ventricular septal defect, presenting with atypical atrioventricular nodal reentrant tachycardia: a rare association
title_fullStr Congenitally corrected transposition of great vessels with infundibular pulmonary stenosis with ventricular septal defect, presenting with atypical atrioventricular nodal reentrant tachycardia: a rare association
title_full_unstemmed Congenitally corrected transposition of great vessels with infundibular pulmonary stenosis with ventricular septal defect, presenting with atypical atrioventricular nodal reentrant tachycardia: a rare association
title_short Congenitally corrected transposition of great vessels with infundibular pulmonary stenosis with ventricular septal defect, presenting with atypical atrioventricular nodal reentrant tachycardia: a rare association
title_sort congenitally corrected transposition of great vessels with infundibular pulmonary stenosis with ventricular septal defect presenting with atypical atrioventricular nodal reentrant tachycardia a rare association
topic Supraventricular tachycardia
Fallot’s physiology
url https://www.dovepress.com/congenitally-corrected-transposition-of-great-vessels-with-infundibula-peer-reviewed-article-IMCRJ
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