Bilateral Total Hip Arthroplasty in the Setting of Developmental Dysplasia of the Hip and Extreme Hip Flexion Requirements due to Phocomelia

Phocomelia is a rare congenital birth defect marked by hypoplastic or markedly absent limbs. Developmental dysplasia of the hip (DDH) is a congenital disorder with a failure of the native acetabulum to provide complete coverage over the femoral head. The secondary osteoarthritis that develops from D...

Full description

Bibliographic Details
Main Authors: Akshar H. Patel, MD, Stefan W. Kreuzer, MD, MSc, William F. Sherman, MD, MBA
Format: Article
Language:English
Published: Elsevier 2021-04-01
Series:Arthroplasty Today
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2352344121000054
_version_ 1818440259155787776
author Akshar H. Patel, MD
Stefan W. Kreuzer, MD, MSc
William F. Sherman, MD, MBA
author_facet Akshar H. Patel, MD
Stefan W. Kreuzer, MD, MSc
William F. Sherman, MD, MBA
author_sort Akshar H. Patel, MD
collection DOAJ
description Phocomelia is a rare congenital birth defect marked by hypoplastic or markedly absent limbs. Developmental dysplasia of the hip (DDH) is a congenital disorder with a failure of the native acetabulum to provide complete coverage over the femoral head. The secondary osteoarthritis that develops from DDH is technically challenging for orthopedic surgeons because of distorted anatomy. The present case describes the diagnosis of Crowe 3 DDH in a phocomelia patient with hyperflexion requirements who successfully underwent staged bilateral total hip arthroplasty via a direct anterior approach. It highlights the utility of preoperative computerized tomography and intraoperative computer navigation to assist in implant placement. Recognizing difficult arthroplasty cases in advance is imperative as these cases may require great expertise and more extensive surgical planning.
first_indexed 2024-12-14T18:09:31Z
format Article
id doaj.art-ac10c58314ba46ad9c95120cc32958c2
institution Directory Open Access Journal
issn 2352-3441
language English
last_indexed 2024-12-14T18:09:31Z
publishDate 2021-04-01
publisher Elsevier
record_format Article
series Arthroplasty Today
spelling doaj.art-ac10c58314ba46ad9c95120cc32958c22022-12-21T22:52:19ZengElsevierArthroplasty Today2352-34412021-04-018262267.e1Bilateral Total Hip Arthroplasty in the Setting of Developmental Dysplasia of the Hip and Extreme Hip Flexion Requirements due to PhocomeliaAkshar H. Patel, MD0Stefan W. Kreuzer, MD, MSc1William F. Sherman, MD, MBA2Department of Orthopaedic Surgery, Tulane University School of Medicine, New Orleans, LA, USAInov8 Orthopedics, Houston, TX, USADepartment of Orthopaedic Surgery, Tulane University School of Medicine, New Orleans, LA, USA; Corresponding author. 1430 Tulane Avenue, New Orleans, LA 70112, USA. Tel.: +1 504 982 0252.Phocomelia is a rare congenital birth defect marked by hypoplastic or markedly absent limbs. Developmental dysplasia of the hip (DDH) is a congenital disorder with a failure of the native acetabulum to provide complete coverage over the femoral head. The secondary osteoarthritis that develops from DDH is technically challenging for orthopedic surgeons because of distorted anatomy. The present case describes the diagnosis of Crowe 3 DDH in a phocomelia patient with hyperflexion requirements who successfully underwent staged bilateral total hip arthroplasty via a direct anterior approach. It highlights the utility of preoperative computerized tomography and intraoperative computer navigation to assist in implant placement. Recognizing difficult arthroplasty cases in advance is imperative as these cases may require great expertise and more extensive surgical planning.http://www.sciencedirect.com/science/article/pii/S2352344121000054Total hip arthroplastyHip dysplasiaPhocomeliaLimb defectContractureComputer navigation
spellingShingle Akshar H. Patel, MD
Stefan W. Kreuzer, MD, MSc
William F. Sherman, MD, MBA
Bilateral Total Hip Arthroplasty in the Setting of Developmental Dysplasia of the Hip and Extreme Hip Flexion Requirements due to Phocomelia
Arthroplasty Today
Total hip arthroplasty
Hip dysplasia
Phocomelia
Limb defect
Contracture
Computer navigation
title Bilateral Total Hip Arthroplasty in the Setting of Developmental Dysplasia of the Hip and Extreme Hip Flexion Requirements due to Phocomelia
title_full Bilateral Total Hip Arthroplasty in the Setting of Developmental Dysplasia of the Hip and Extreme Hip Flexion Requirements due to Phocomelia
title_fullStr Bilateral Total Hip Arthroplasty in the Setting of Developmental Dysplasia of the Hip and Extreme Hip Flexion Requirements due to Phocomelia
title_full_unstemmed Bilateral Total Hip Arthroplasty in the Setting of Developmental Dysplasia of the Hip and Extreme Hip Flexion Requirements due to Phocomelia
title_short Bilateral Total Hip Arthroplasty in the Setting of Developmental Dysplasia of the Hip and Extreme Hip Flexion Requirements due to Phocomelia
title_sort bilateral total hip arthroplasty in the setting of developmental dysplasia of the hip and extreme hip flexion requirements due to phocomelia
topic Total hip arthroplasty
Hip dysplasia
Phocomelia
Limb defect
Contracture
Computer navigation
url http://www.sciencedirect.com/science/article/pii/S2352344121000054
work_keys_str_mv AT aksharhpatelmd bilateraltotalhiparthroplastyinthesettingofdevelopmentaldysplasiaofthehipandextremehipflexionrequirementsduetophocomelia
AT stefanwkreuzermdmsc bilateraltotalhiparthroplastyinthesettingofdevelopmentaldysplasiaofthehipandextremehipflexionrequirementsduetophocomelia
AT williamfshermanmdmba bilateraltotalhiparthroplastyinthesettingofdevelopmentaldysplasiaofthehipandextremehipflexionrequirementsduetophocomelia