Bilateral polyotia: case of a rare and atypical congenital malformation in a three month-old infant

Polyotia is an extremely rare congenital malformation of the external ear, characterised by the development of an accessory auricle. It is more often unilateral. We report the case of a Cameroonian infant whom we received at the age of three months. The infant´s mother had noticed a deformity concer...

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Main Authors: Roger Christian Meva'a Biouélé, Emmanuel Choffor-Nchinda
Format: Article
Language:English
Published: The Pan African Medical Journal 2021-01-01
Series:The Pan African Medical Journal
Subjects:
Online Access: https://www.panafrican-med-journal.com/content/article/38/63/pdf/63.pdf
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author Roger Christian Meva'a Biouélé
Emmanuel Choffor-Nchinda
author_facet Roger Christian Meva'a Biouélé
Emmanuel Choffor-Nchinda
author_sort Roger Christian Meva'a Biouélé
collection DOAJ
description Polyotia is an extremely rare congenital malformation of the external ear, characterised by the development of an accessory auricle. It is more often unilateral. We report the case of a Cameroonian infant whom we received at the age of three months. The infant´s mother had noticed a deformity concerning both ears since birth and did not observe any other associated symptom. On physical examination, we found an additional auricle fusing with the tragus on both sides. This unusual structure consisted of skin and cartilage. Their greater diameters measured 2.5cm and 2cm on the left and right respectively. Otoscopic evaluation and general physical examination were normal. A CT-scan of the temporal bones as well as an abdominal ultrasound scan were requested to explore other possibly associated anomalies. These imaging studies were normal. The diagnosis of isolated bilateral polyotia was made. An ear reconstructive surgery was proposed to the parents. An informed consent was obtained from the parents, pre-operative work-up was requested and the procedure was planned. A bilateral otoplasty was done under general anaesthesia. The procedure was simple, consisting of excision of the excess tissue to give a natural aesthetic result. Post-operative evolution was favourable, with good scarring on day 10, as illustrated on (A, B, C, D, E). Nine months following the procedure, the parents seemed satisfied with the aesthetic result. Polytia is a rare congenital malformation. Management requires adequate and comprehensive investigations to exclude enchondroma or associated malformations, prior to ear reconstructive surgery.
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spelling doaj.art-acbbc412c22743b8acbe08f83d890bfd2022-12-22T00:15:23ZengThe Pan African Medical JournalThe Pan African Medical Journal1937-86881937-86882021-01-01386310.11604/pamj.2021.38.63.2745827458Bilateral polyotia: case of a rare and atypical congenital malformation in a three month-old infantRoger Christian Meva'a Biouélé0Emmanuel Choffor-Nchinda1 Ear, Nose and Throat (ENT) Unit, Yaounde Central Hospital, Yaounde, Cameroon Ear, Nose and Throat (ENT) Unit, Buea Regional Hospital, Buea, Cameroon Polyotia is an extremely rare congenital malformation of the external ear, characterised by the development of an accessory auricle. It is more often unilateral. We report the case of a Cameroonian infant whom we received at the age of three months. The infant´s mother had noticed a deformity concerning both ears since birth and did not observe any other associated symptom. On physical examination, we found an additional auricle fusing with the tragus on both sides. This unusual structure consisted of skin and cartilage. Their greater diameters measured 2.5cm and 2cm on the left and right respectively. Otoscopic evaluation and general physical examination were normal. A CT-scan of the temporal bones as well as an abdominal ultrasound scan were requested to explore other possibly associated anomalies. These imaging studies were normal. The diagnosis of isolated bilateral polyotia was made. An ear reconstructive surgery was proposed to the parents. An informed consent was obtained from the parents, pre-operative work-up was requested and the procedure was planned. A bilateral otoplasty was done under general anaesthesia. The procedure was simple, consisting of excision of the excess tissue to give a natural aesthetic result. Post-operative evolution was favourable, with good scarring on day 10, as illustrated on (A, B, C, D, E). Nine months following the procedure, the parents seemed satisfied with the aesthetic result. Polytia is a rare congenital malformation. Management requires adequate and comprehensive investigations to exclude enchondroma or associated malformations, prior to ear reconstructive surgery. https://www.panafrican-med-journal.com/content/article/38/63/pdf/63.pdf polyotiacongenital malformationplastic surgerycameroon
spellingShingle Roger Christian Meva'a Biouélé
Emmanuel Choffor-Nchinda
Bilateral polyotia: case of a rare and atypical congenital malformation in a three month-old infant
The Pan African Medical Journal
polyotia
congenital malformation
plastic surgery
cameroon
title Bilateral polyotia: case of a rare and atypical congenital malformation in a three month-old infant
title_full Bilateral polyotia: case of a rare and atypical congenital malformation in a three month-old infant
title_fullStr Bilateral polyotia: case of a rare and atypical congenital malformation in a three month-old infant
title_full_unstemmed Bilateral polyotia: case of a rare and atypical congenital malformation in a three month-old infant
title_short Bilateral polyotia: case of a rare and atypical congenital malformation in a three month-old infant
title_sort bilateral polyotia case of a rare and atypical congenital malformation in a three month old infant
topic polyotia
congenital malformation
plastic surgery
cameroon
url https://www.panafrican-med-journal.com/content/article/38/63/pdf/63.pdf
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