Large Pelvic Mass in a Female Adolescent: Atypical Presentation and Successful Treatment of Extraskeletal Ewing Sarcoma
Extraskeletal Ewing sarcoma is a rare soft tissue tumor primarily affecting pediatric patients. The treatment is currently based on a multidisciplinary approach which allows, in cases of localized disease, good survival rates. We report the case of a 15-year-old female patient with a rapidly growing...
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| Format: | Article |
| Language: | English |
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MDPI AG
2023-05-01
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| Series: | Healthcare |
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| Online Access: | https://www.mdpi.com/2227-9032/11/10/1373 |
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| author | Federica Perelli Giuseppe Vizzielli Anna Franca Cavaliere Stefano Restaino Giovanni Scambia Gian Franco Zannoni Damiano Arciuolo Valerio Gallotta |
| author_facet | Federica Perelli Giuseppe Vizzielli Anna Franca Cavaliere Stefano Restaino Giovanni Scambia Gian Franco Zannoni Damiano Arciuolo Valerio Gallotta |
| author_sort | Federica Perelli |
| collection | DOAJ |
| description | Extraskeletal Ewing sarcoma is a rare soft tissue tumor primarily affecting pediatric patients. The treatment is currently based on a multidisciplinary approach which allows, in cases of localized disease, good survival rates. We report the case of a 15-year-old female patient with a rapidly growing suspected pelvic mass misdiagnosed following the preliminary radiological exams, which assessed the findings as a mass of ovarian origin. The girl underwent surgery and, thanks to histopathological, immunohistochemical and real-time polymerase chain reaction (RT-PCR) examinations, it was possible to make the right diagnosis and to administer the best treatment in terms of surgery, chemotherapy and radiotherapy, obtaining a long disease-free interval and no recurrence to date. |
| first_indexed | 2024-03-11T03:41:47Z |
| format | Article |
| id | doaj.art-acd195d4f19a46c0baf0477c15caf96d |
| institution | Directory Open Access Journal |
| issn | 2227-9032 |
| language | English |
| last_indexed | 2024-03-11T03:41:47Z |
| publishDate | 2023-05-01 |
| publisher | MDPI AG |
| record_format | Article |
| series | Healthcare |
| spelling | doaj.art-acd195d4f19a46c0baf0477c15caf96d2023-11-18T01:31:21ZengMDPI AGHealthcare2227-90322023-05-011110137310.3390/healthcare11101373Large Pelvic Mass in a Female Adolescent: Atypical Presentation and Successful Treatment of Extraskeletal Ewing SarcomaFederica Perelli0Giuseppe Vizzielli1Anna Franca Cavaliere2Stefano Restaino3Giovanni Scambia4Gian Franco Zannoni5Damiano Arciuolo6Valerio Gallotta7Obstetrics and Gynecology Unit, Ospedale Santa Maria Annunziata, USL Toscana Centro, Bagno a Ripoli, 50012 Firenze, ItalyClinic of Obstetrics and Gynecology, S. Maria della Misericordia University Hospital, Azienda Sanitaria Universitaria Friuli Centrale (ASUFC), 33100 Udine, ItalyObstetrics and Gynaecology Unit, Dipartimento Centro di Eccellenza Donna e Bambino Nascente, Fatebenefratelli Gemelli Isola Tiberina, 00168 Rome, ItalyClinic of Obstetrics and Gynecology, S. Maria della Misericordia University Hospital, Azienda Sanitaria Universitaria Friuli Centrale (ASUFC), 33100 Udine, ItalyDipartimento per le Scienze Della Salute Della Donna, del Bambino e di Sanità Pubblica, UOC Ginecologia Oncologica, Fondazione Policlinico Universitario Agostino Gemelli IRCCS, 00168 Rome, ItalyPathology Unit, Department of Woman and Child’s Health and Public Health Sciences, Fondazione Policlinico Universitario Agostino Gemelli IRCCS, 00168 Rome, ItalyPathology Unit, Department of Woman and Child’s Health and Public Health Sciences, Fondazione Policlinico Universitario Agostino Gemelli IRCCS, 00168 Rome, ItalyDipartimento per le Scienze Della Salute Della Donna, del Bambino e di Sanità Pubblica, UOC Ginecologia Oncologica, Fondazione Policlinico Universitario Agostino Gemelli IRCCS, 00168 Rome, ItalyExtraskeletal Ewing sarcoma is a rare soft tissue tumor primarily affecting pediatric patients. The treatment is currently based on a multidisciplinary approach which allows, in cases of localized disease, good survival rates. We report the case of a 15-year-old female patient with a rapidly growing suspected pelvic mass misdiagnosed following the preliminary radiological exams, which assessed the findings as a mass of ovarian origin. The girl underwent surgery and, thanks to histopathological, immunohistochemical and real-time polymerase chain reaction (RT-PCR) examinations, it was possible to make the right diagnosis and to administer the best treatment in terms of surgery, chemotherapy and radiotherapy, obtaining a long disease-free interval and no recurrence to date.https://www.mdpi.com/2227-9032/11/10/1373gynecologygynecologic surgeryfemale healthcareEwing sarcomapediatric gynecologyfertility sparing |
| spellingShingle | Federica Perelli Giuseppe Vizzielli Anna Franca Cavaliere Stefano Restaino Giovanni Scambia Gian Franco Zannoni Damiano Arciuolo Valerio Gallotta Large Pelvic Mass in a Female Adolescent: Atypical Presentation and Successful Treatment of Extraskeletal Ewing Sarcoma Healthcare gynecology gynecologic surgery female healthcare Ewing sarcoma pediatric gynecology fertility sparing |
| title | Large Pelvic Mass in a Female Adolescent: Atypical Presentation and Successful Treatment of Extraskeletal Ewing Sarcoma |
| title_full | Large Pelvic Mass in a Female Adolescent: Atypical Presentation and Successful Treatment of Extraskeletal Ewing Sarcoma |
| title_fullStr | Large Pelvic Mass in a Female Adolescent: Atypical Presentation and Successful Treatment of Extraskeletal Ewing Sarcoma |
| title_full_unstemmed | Large Pelvic Mass in a Female Adolescent: Atypical Presentation and Successful Treatment of Extraskeletal Ewing Sarcoma |
| title_short | Large Pelvic Mass in a Female Adolescent: Atypical Presentation and Successful Treatment of Extraskeletal Ewing Sarcoma |
| title_sort | large pelvic mass in a female adolescent atypical presentation and successful treatment of extraskeletal ewing sarcoma |
| topic | gynecology gynecologic surgery female healthcare Ewing sarcoma pediatric gynecology fertility sparing |
| url | https://www.mdpi.com/2227-9032/11/10/1373 |
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