Senning Procedure for Physiological Atrial Inversion With Left Atrial Isomerism

We present the case of an infant with left atrial isomerism with complex pulmonary and systemic venous connections that resulted in physiological parallel circulation in the setting of ventriculoarterial concordance who was surgically treated using the Senning procedure. This case highlights a rare...

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Main Authors: Bibhuti B. Das, MD, K. Anitha Jayakumar, MD, Ming-Lon Young, MD, Kak-Chen Chan, MD
Format: Article
Language:English
Published: Elsevier 2019-12-01
Series:JACC: Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2666084919304413
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author Bibhuti B. Das, MD
K. Anitha Jayakumar, MD
Ming-Lon Young, MD
Kak-Chen Chan, MD
author_facet Bibhuti B. Das, MD
K. Anitha Jayakumar, MD
Ming-Lon Young, MD
Kak-Chen Chan, MD
author_sort Bibhuti B. Das, MD
collection DOAJ
description We present the case of an infant with left atrial isomerism with complex pulmonary and systemic venous connections that resulted in physiological parallel circulation in the setting of ventriculoarterial concordance who was surgically treated using the Senning procedure. This case highlights a rare cause for cyanosis due to poor mixing from a parallel circulation and an issue with nomenclature. (Level of Difficulty: Advanced.)
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spelling doaj.art-ae5a5fbf221a4758ad48cfd109add2102022-12-21T20:48:25ZengElsevierJACC: Case Reports2666-08492019-12-0114516522Senning Procedure for Physiological Atrial Inversion With Left Atrial IsomerismBibhuti B. Das, MD0K. Anitha Jayakumar, MD1Ming-Lon Young, MD2Kak-Chen Chan, MD3Department of Pediatric Cardiology, Baylor College of Medicine, Texas Children’s Hospital, Austin Specialty Care, Austin, Texas; Address for correspondence: Dr. Bibhuti B. Das, Department of Pediatric Cardiology, Baylor College of Medicine, Texas Children’s Hospital, Austin Specialty Care, Austin, Texas 78759.Joe DiMaggio Children’s Hospital Heart Institute, Memorial Healthcare System, Hollywood, FloridaJoe DiMaggio Children’s Hospital Heart Institute, Memorial Healthcare System, Hollywood, FloridaJoe DiMaggio Children’s Hospital Heart Institute, Memorial Healthcare System, Hollywood, FloridaWe present the case of an infant with left atrial isomerism with complex pulmonary and systemic venous connections that resulted in physiological parallel circulation in the setting of ventriculoarterial concordance who was surgically treated using the Senning procedure. This case highlights a rare cause for cyanosis due to poor mixing from a parallel circulation and an issue with nomenclature. (Level of Difficulty: Advanced.)http://www.sciencedirect.com/science/article/pii/S2666084919304413atrial inversionleft atrial isomerismleft ventricular noncompactionSenning procedure
spellingShingle Bibhuti B. Das, MD
K. Anitha Jayakumar, MD
Ming-Lon Young, MD
Kak-Chen Chan, MD
Senning Procedure for Physiological Atrial Inversion With Left Atrial Isomerism
JACC: Case Reports
atrial inversion
left atrial isomerism
left ventricular noncompaction
Senning procedure
title Senning Procedure for Physiological Atrial Inversion With Left Atrial Isomerism
title_full Senning Procedure for Physiological Atrial Inversion With Left Atrial Isomerism
title_fullStr Senning Procedure for Physiological Atrial Inversion With Left Atrial Isomerism
title_full_unstemmed Senning Procedure for Physiological Atrial Inversion With Left Atrial Isomerism
title_short Senning Procedure for Physiological Atrial Inversion With Left Atrial Isomerism
title_sort senning procedure for physiological atrial inversion with left atrial isomerism
topic atrial inversion
left atrial isomerism
left ventricular noncompaction
Senning procedure
url http://www.sciencedirect.com/science/article/pii/S2666084919304413
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