Functional improvements in patients with lymphangioleiomyomatosis after sirolimus: an observational study

Functional improvements in patients with lymphangioleiomyomatosis after sirolimus: an observational study

Abstract Background Sirolimus has been shown to be effective in patients with lymphangioleiomyomatosis (LAM). We wish to summarize our experience using sirolimus and its effectiveness in LAM patients. Methods We analyzed data from 98 patients who were diagnosed with definite or probable sporadic LAM...

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Bibliographic Details
Main Authors: Yongzhong Zhan, Lisha Shen, Wenshuai Xu, Xiuxiu Wu, Weihong Zhang, Jun Wang, Xue Li, Yanli Yang, Xinlun Tian, Kai-Feng Xu
Format: Article
Language:English
Published: BMC 2018-02-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Lymphangioleiomyomatosis
Sirolimus
Pulmonary function
Chylothorax
Adverse events
Online Access:http://link.springer.com/article/10.1186/s13023-018-0775-9

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