Current dietary recommendations for patients with cystic fibrosis
Cystic fibrosis (CF) is classified as metabolic and multisystem disease with autosomal recessive inheritance caused by mutations in the gene located on chromosome 7 encoding cystic fibrosis transmembrane conductance regulator (CFTR) protein. CFTR is a transmembrane chloride channel of epithelial cel...
| Main Authors: | , , , , , , , , , , |
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| Format: | Article |
| Language: | English |
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Kazimierz Wielki University
2019-04-01
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| Series: | Journal of Education, Health and Sport |
| Subjects: | |
| Online Access: | https://apcz.umk.pl/JEHS/article/view/25700 |
| _version_ | 1828366151635173376 |
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| author | Katarzyna Stefańska Monika Jakimiec-Komisarczyk Paulina Terlecka Marcelina Makuch Joanna Jakimiec Magdalena Igras-Kołdyj Michał Szczyrek Robert Kieszko Agnieszka Zwolak Janusz Milanowski Robert Jan Łuczyk |
| author_facet | Katarzyna Stefańska Monika Jakimiec-Komisarczyk Paulina Terlecka Marcelina Makuch Joanna Jakimiec Magdalena Igras-Kołdyj Michał Szczyrek Robert Kieszko Agnieszka Zwolak Janusz Milanowski Robert Jan Łuczyk |
| author_sort | Katarzyna Stefańska |
| collection | DOAJ |
| description | Cystic fibrosis (CF) is classified as metabolic and multisystem disease with autosomal recessive inheritance caused by mutations in the gene located on chromosome 7 encoding cystic fibrosis transmembrane conductance regulator (CFTR) protein. CFTR is a transmembrane chloride channel of epithelial cells and affects the activity of the mucous membrane of the sweat glands, airway epithelium, pancreatic ducts, vas deferens, bile ducts and intestines. In CF, increased concentration of chlorides in the sweat, pancreatic insufficiency and impaired absorption are observed as well as changes in the respiratory system related to, among others, impaired airway patency, weakening of the mucociliary clearance mechanism and the development of bacterial infections. CF is a chronic condition requiring comprehensive therapy. Nutritional treatment is an essential element of CF therapy. Malnutrition is a common complication in patient with CF and eating disorders. The majority of patients with CF have higher energy, protein and fat needs. In addition, supplementation with enzyme preparations, vitamins, sodium chloride, as well as the use of high-energy nutrients is recommended. The aim of the study was to evaluate current nutritional recommendations of patients with CF. |
| first_indexed | 2024-04-14T05:41:28Z |
| format | Article |
| id | doaj.art-af336cee47a9477bbb438712666962c5 |
| institution | Directory Open Access Journal |
| issn | 2391-8306 |
| language | English |
| last_indexed | 2024-04-14T05:41:28Z |
| publishDate | 2019-04-01 |
| publisher | Kazimierz Wielki University |
| record_format | Article |
| series | Journal of Education, Health and Sport |
| spelling | doaj.art-af336cee47a9477bbb438712666962c52022-12-22T02:09:26ZengKazimierz Wielki UniversityJournal of Education, Health and Sport2391-83062019-04-0194Current dietary recommendations for patients with cystic fibrosisKatarzyna Stefańska0Monika Jakimiec-Komisarczyk1Paulina Terlecka2Marcelina Makuch3Joanna Jakimiec4Magdalena Igras-Kołdyj5Michał Szczyrek6Robert Kieszko7Agnieszka Zwolak8Janusz Milanowski9Robert Jan Łuczyk10Department of Pneumonology, Oncology and Allergology, Medical University of LublinDepartment of Pneumonology, Oncology and Allergology, Medical University of LublinDepartment of Pneumonology, Oncology and Allergology, Medical University of LublinDepartment of Pneumonology, Oncology and Allergology, Medical University of LublinDepartment of Pneumonology, Oncology and Allergology, Medical University of LublinChair of Internal Medicine with Department of Internal Nursing, Medical University of LublinDepartment of Pneumonology, Oncology and Allergology, Medical University of LublinDepartment of Pneumonology, Oncology and Allergology, Medical University of LublinChair of Internal Medicine with Department of Internal Nursing, Medical University of LublinDepartment of Pneumonology, Oncology and Allergology, Medical University of LublinChair of Internal Medicine with Department of Internal Nursing, Medical University of LublinCystic fibrosis (CF) is classified as metabolic and multisystem disease with autosomal recessive inheritance caused by mutations in the gene located on chromosome 7 encoding cystic fibrosis transmembrane conductance regulator (CFTR) protein. CFTR is a transmembrane chloride channel of epithelial cells and affects the activity of the mucous membrane of the sweat glands, airway epithelium, pancreatic ducts, vas deferens, bile ducts and intestines. In CF, increased concentration of chlorides in the sweat, pancreatic insufficiency and impaired absorption are observed as well as changes in the respiratory system related to, among others, impaired airway patency, weakening of the mucociliary clearance mechanism and the development of bacterial infections. CF is a chronic condition requiring comprehensive therapy. Nutritional treatment is an essential element of CF therapy. Malnutrition is a common complication in patient with CF and eating disorders. The majority of patients with CF have higher energy, protein and fat needs. In addition, supplementation with enzyme preparations, vitamins, sodium chloride, as well as the use of high-energy nutrients is recommended. The aim of the study was to evaluate current nutritional recommendations of patients with CF.https://apcz.umk.pl/JEHS/article/view/25700cystic fibrosisnutritional treatmentsupplementation |
| spellingShingle | Katarzyna Stefańska Monika Jakimiec-Komisarczyk Paulina Terlecka Marcelina Makuch Joanna Jakimiec Magdalena Igras-Kołdyj Michał Szczyrek Robert Kieszko Agnieszka Zwolak Janusz Milanowski Robert Jan Łuczyk Current dietary recommendations for patients with cystic fibrosis Journal of Education, Health and Sport cystic fibrosis nutritional treatment supplementation |
| title | Current dietary recommendations for patients with cystic fibrosis |
| title_full | Current dietary recommendations for patients with cystic fibrosis |
| title_fullStr | Current dietary recommendations for patients with cystic fibrosis |
| title_full_unstemmed | Current dietary recommendations for patients with cystic fibrosis |
| title_short | Current dietary recommendations for patients with cystic fibrosis |
| title_sort | current dietary recommendations for patients with cystic fibrosis |
| topic | cystic fibrosis nutritional treatment supplementation |
| url | https://apcz.umk.pl/JEHS/article/view/25700 |
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