Surgical Treatment of Intra-Abdominal Desmoid Tumors Resulting In Short Bowel Syndrome

Advanced intra-abdominal desmoids tumors present with severe symptoms, complications or rapid growth, which lead to adverse outcomes. Our aim was to evaluate the treatment and outcome of patients with advanced intra-abdominal desmoids tumors, and develop guidelines for surgical management of these p...

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Main Authors: Jon Thompson, David Mercer, Wendy Grant, Jean Botha, Alan Langnas, Matthew Wheeler
Format: Article
Language:English
Published: MDPI AG 2012-01-01
Series:Cancers
Subjects:
Online Access:http://www.mdpi.com/2072-6694/4/1/31/
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author Jon Thompson
David Mercer
Wendy Grant
Jean Botha
Alan Langnas
Matthew Wheeler
author_facet Jon Thompson
David Mercer
Wendy Grant
Jean Botha
Alan Langnas
Matthew Wheeler
author_sort Jon Thompson
collection DOAJ
description Advanced intra-abdominal desmoids tumors present with severe symptoms, complications or rapid growth, which lead to adverse outcomes. Our aim was to evaluate the treatment and outcome of patients with advanced intra-abdominal desmoids tumors, and develop guidelines for surgical management of these patients. We reviewed the clinical courses of 21 adult patients with advanced stage intra-abdominal desmoid tumors who presented to an intestinal rehabilitation and transplantation program. Patients with massive intestinal resection presented in two groups. The first group had a short small intestinal remnant after resection ( < 60 cm). These patients were poor rehabilitation candidates and eventually met criteria for transplant. The second had longer intestinal remnants and were more successfully rehabilitated and have not had complications that would lead to transplantation. Advanced intra-abdominal desmoid tumors have outcomes after resection that merit aggressive resection and planned intestinal rehabilitation and intestinal transplantation as indicated.
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spelling doaj.art-af4582b5228f497bb3f067658b09333d2023-09-03T03:25:38ZengMDPI AGCancers2072-66942012-01-0141313810.3390/cancers4010031Surgical Treatment of Intra-Abdominal Desmoid Tumors Resulting In Short Bowel SyndromeJon ThompsonDavid MercerWendy GrantJean BothaAlan LangnasMatthew WheelerAdvanced intra-abdominal desmoids tumors present with severe symptoms, complications or rapid growth, which lead to adverse outcomes. Our aim was to evaluate the treatment and outcome of patients with advanced intra-abdominal desmoids tumors, and develop guidelines for surgical management of these patients. We reviewed the clinical courses of 21 adult patients with advanced stage intra-abdominal desmoid tumors who presented to an intestinal rehabilitation and transplantation program. Patients with massive intestinal resection presented in two groups. The first group had a short small intestinal remnant after resection ( < 60 cm). These patients were poor rehabilitation candidates and eventually met criteria for transplant. The second had longer intestinal remnants and were more successfully rehabilitated and have not had complications that would lead to transplantation. Advanced intra-abdominal desmoid tumors have outcomes after resection that merit aggressive resection and planned intestinal rehabilitation and intestinal transplantation as indicated.http://www.mdpi.com/2072-6694/4/1/31/intra-abdominal desmoid tumorsshort bowel syndromefamilial adenomatous polyposis
spellingShingle Jon Thompson
David Mercer
Wendy Grant
Jean Botha
Alan Langnas
Matthew Wheeler
Surgical Treatment of Intra-Abdominal Desmoid Tumors Resulting In Short Bowel Syndrome
Cancers
intra-abdominal desmoid tumors
short bowel syndrome
familial adenomatous polyposis
title Surgical Treatment of Intra-Abdominal Desmoid Tumors Resulting In Short Bowel Syndrome
title_full Surgical Treatment of Intra-Abdominal Desmoid Tumors Resulting In Short Bowel Syndrome
title_fullStr Surgical Treatment of Intra-Abdominal Desmoid Tumors Resulting In Short Bowel Syndrome
title_full_unstemmed Surgical Treatment of Intra-Abdominal Desmoid Tumors Resulting In Short Bowel Syndrome
title_short Surgical Treatment of Intra-Abdominal Desmoid Tumors Resulting In Short Bowel Syndrome
title_sort surgical treatment of intra abdominal desmoid tumors resulting in short bowel syndrome
topic intra-abdominal desmoid tumors
short bowel syndrome
familial adenomatous polyposis
url http://www.mdpi.com/2072-6694/4/1/31/
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