Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis

Background: Rosai Dorfman Disease (RDD) is histiocytosis associated with lymphadenopathy. Spinal involvement is uncommon and seen in 1%. Most of the spinal lesions are extradural and intradural extramedullary. Intramedullary RDD is extremely rare. Case report: We report a rare case of quadriparesis...

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Main Authors: Sandeep Velicheti, R. Rajakulasingam, K. Kalyan, G. Rajesh, R. Botchu
Format: Article
Language:English
Published: Elsevier 2022-03-01
Series:Journal of Orthopaedic Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2773157X22000169
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author Sandeep Velicheti
R. Rajakulasingam
K. Kalyan
G. Rajesh
R. Botchu
author_facet Sandeep Velicheti
R. Rajakulasingam
K. Kalyan
G. Rajesh
R. Botchu
author_sort Sandeep Velicheti
collection DOAJ
description Background: Rosai Dorfman Disease (RDD) is histiocytosis associated with lymphadenopathy. Spinal involvement is uncommon and seen in 1%. Most of the spinal lesions are extradural and intradural extramedullary. Intramedullary RDD is extremely rare. Case report: We report a rare case of quadriparesis in 24 year old male due to intramedullary RDD of cervicothoracic region and review the literature. Conclusion: The rare cases of intramedullary RDD should be included in the differential diagnosis of young patient presenting with quadriparesis or paraparesis.
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spelling doaj.art-af9dfb12d3aa4a98802c6df17a4e3b512022-12-22T03:46:22ZengElsevierJournal of Orthopaedic Reports2773-157X2022-03-01112023Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesisSandeep Velicheti0R. Rajakulasingam1K. Kalyan2G. Rajesh3R. Botchu4Department of Radiology, PSIMS, Vijayawada, IndiaDepartment of Radiology, Royal National Orthopedic Hospital, Stanmore, UKDepartment of Pathology, Orange Diagnostics, Vijayawada, IndiaDepartment of Neurosurgery, Suraksha Hospital, Vijayawada, IndiaDepartment of Radiology, Royal Orthopedic Hospital, Birmingham, UK; Corresponding author. Department of Musculoskeletal Radiology, The Royal Orthopedic Hospital Bristol Road South Northfield, Birmingham, UK.Background: Rosai Dorfman Disease (RDD) is histiocytosis associated with lymphadenopathy. Spinal involvement is uncommon and seen in 1%. Most of the spinal lesions are extradural and intradural extramedullary. Intramedullary RDD is extremely rare. Case report: We report a rare case of quadriparesis in 24 year old male due to intramedullary RDD of cervicothoracic region and review the literature. Conclusion: The rare cases of intramedullary RDD should be included in the differential diagnosis of young patient presenting with quadriparesis or paraparesis.http://www.sciencedirect.com/science/article/pii/S2773157X22000169SpineHistiocytosisParalysisQuadriparesisRosai Dorfman Disease
spellingShingle Sandeep Velicheti
R. Rajakulasingam
K. Kalyan
G. Rajesh
R. Botchu
Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis
Journal of Orthopaedic Reports
Spine
Histiocytosis
Paralysis
Quadriparesis
Rosai Dorfman Disease
title Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis
title_full Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis
title_fullStr Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis
title_full_unstemmed Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis
title_short Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis
title_sort intramedullary spinal rosai dorfman disease a rare cause of quadriparesis
topic Spine
Histiocytosis
Paralysis
Quadriparesis
Rosai Dorfman Disease
url http://www.sciencedirect.com/science/article/pii/S2773157X22000169
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AT rrajakulasingam intramedullaryspinalrosaidorfmandiseaseararecauseofquadriparesis
AT kkalyan intramedullaryspinalrosaidorfmandiseaseararecauseofquadriparesis
AT grajesh intramedullaryspinalrosaidorfmandiseaseararecauseofquadriparesis
AT rbotchu intramedullaryspinalrosaidorfmandiseaseararecauseofquadriparesis