Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis
Background: Rosai Dorfman Disease (RDD) is histiocytosis associated with lymphadenopathy. Spinal involvement is uncommon and seen in 1%. Most of the spinal lesions are extradural and intradural extramedullary. Intramedullary RDD is extremely rare. Case report: We report a rare case of quadriparesis...
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Format: | Article |
Language: | English |
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Elsevier
2022-03-01
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Series: | Journal of Orthopaedic Reports |
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Online Access: | http://www.sciencedirect.com/science/article/pii/S2773157X22000169 |
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author | Sandeep Velicheti R. Rajakulasingam K. Kalyan G. Rajesh R. Botchu |
author_facet | Sandeep Velicheti R. Rajakulasingam K. Kalyan G. Rajesh R. Botchu |
author_sort | Sandeep Velicheti |
collection | DOAJ |
description | Background: Rosai Dorfman Disease (RDD) is histiocytosis associated with lymphadenopathy. Spinal involvement is uncommon and seen in 1%. Most of the spinal lesions are extradural and intradural extramedullary. Intramedullary RDD is extremely rare. Case report: We report a rare case of quadriparesis in 24 year old male due to intramedullary RDD of cervicothoracic region and review the literature. Conclusion: The rare cases of intramedullary RDD should be included in the differential diagnosis of young patient presenting with quadriparesis or paraparesis. |
first_indexed | 2024-04-12T05:23:45Z |
format | Article |
id | doaj.art-af9dfb12d3aa4a98802c6df17a4e3b51 |
institution | Directory Open Access Journal |
issn | 2773-157X |
language | English |
last_indexed | 2024-04-12T05:23:45Z |
publishDate | 2022-03-01 |
publisher | Elsevier |
record_format | Article |
series | Journal of Orthopaedic Reports |
spelling | doaj.art-af9dfb12d3aa4a98802c6df17a4e3b512022-12-22T03:46:22ZengElsevierJournal of Orthopaedic Reports2773-157X2022-03-01112023Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesisSandeep Velicheti0R. Rajakulasingam1K. Kalyan2G. Rajesh3R. Botchu4Department of Radiology, PSIMS, Vijayawada, IndiaDepartment of Radiology, Royal National Orthopedic Hospital, Stanmore, UKDepartment of Pathology, Orange Diagnostics, Vijayawada, IndiaDepartment of Neurosurgery, Suraksha Hospital, Vijayawada, IndiaDepartment of Radiology, Royal Orthopedic Hospital, Birmingham, UK; Corresponding author. Department of Musculoskeletal Radiology, The Royal Orthopedic Hospital Bristol Road South Northfield, Birmingham, UK.Background: Rosai Dorfman Disease (RDD) is histiocytosis associated with lymphadenopathy. Spinal involvement is uncommon and seen in 1%. Most of the spinal lesions are extradural and intradural extramedullary. Intramedullary RDD is extremely rare. Case report: We report a rare case of quadriparesis in 24 year old male due to intramedullary RDD of cervicothoracic region and review the literature. Conclusion: The rare cases of intramedullary RDD should be included in the differential diagnosis of young patient presenting with quadriparesis or paraparesis.http://www.sciencedirect.com/science/article/pii/S2773157X22000169SpineHistiocytosisParalysisQuadriparesisRosai Dorfman Disease |
spellingShingle | Sandeep Velicheti R. Rajakulasingam K. Kalyan G. Rajesh R. Botchu Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis Journal of Orthopaedic Reports Spine Histiocytosis Paralysis Quadriparesis Rosai Dorfman Disease |
title | Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis |
title_full | Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis |
title_fullStr | Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis |
title_full_unstemmed | Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis |
title_short | Intramedullary Spinal Rosai Dorfman disease- A rare cause of quadriparesis |
title_sort | intramedullary spinal rosai dorfman disease a rare cause of quadriparesis |
topic | Spine Histiocytosis Paralysis Quadriparesis Rosai Dorfman Disease |
url | http://www.sciencedirect.com/science/article/pii/S2773157X22000169 |
work_keys_str_mv | AT sandeepvelicheti intramedullaryspinalrosaidorfmandiseaseararecauseofquadriparesis AT rrajakulasingam intramedullaryspinalrosaidorfmandiseaseararecauseofquadriparesis AT kkalyan intramedullaryspinalrosaidorfmandiseaseararecauseofquadriparesis AT grajesh intramedullaryspinalrosaidorfmandiseaseararecauseofquadriparesis AT rbotchu intramedullaryspinalrosaidorfmandiseaseararecauseofquadriparesis |