Obstruction of the Hepatic Venous Flow Caused by Intravenous Leiomyomatosis
Budd–Chiari syndrome (BCS) is a rare intrahepatic vascular disease that is characterized by a hepatic venous outflow obstruction. Intravenous leiomyomatosis (ILs) is a rare complication of a myoma. Here, we report a case of BCS that was caused by intracaval ILs. A woman presented to the emergency de...
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MDPI AG
2020-12-01
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| Series: | Medicina |
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| Online Access: | https://www.mdpi.com/1010-660X/56/12/696 |
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| author | Sin-Youl Park In Hwan Yeo Yun Jeong Kim Jong Kun Kim |
| author_facet | Sin-Youl Park In Hwan Yeo Yun Jeong Kim Jong Kun Kim |
| author_sort | Sin-Youl Park |
| collection | DOAJ |
| description | Budd–Chiari syndrome (BCS) is a rare intrahepatic vascular disease that is characterized by a hepatic venous outflow obstruction. Intravenous leiomyomatosis (ILs) is a rare complication of a myoma. Here, we report a case of BCS that was caused by intracaval ILs. A woman presented to the emergency department (ED) with abdominal distension that had gradually progressed over a period of 3 years. Bedside ultrasonography and contrast-enhanced computed tomography (CECT) showed a large ascites and pelvic mass. The mass continued to the inferior vena cava and the right atrium. The intracaval mass was obstructing the left and middle hepatic veins. We established a tentative diagnosis of BCS caused by intracaval ILs and attempted surgical resection. Complete resection of the intracaval mass failed because of adhesion; however, she was discharged from the hospital without any postoperative complications. After 3 months, a pelvic ultrasonography showed a recurrence of a 4 × 3 cm pelvic mass. The mass size increased to 6 cm after 30 months. ILs can cause secondary BCS and can lead to life-threatening conditions. Owing to its extreme rarity, early detection in the ED is challenging. Bedside ultrasonography and CECT can enable the early recognition of BCS by ILs. |
| first_indexed | 2024-03-12T06:09:58Z |
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| institution | Directory Open Access Journal |
| issn | 1010-660X |
| language | English |
| last_indexed | 2024-03-12T06:09:58Z |
| publishDate | 2020-12-01 |
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| series | Medicina |
| spelling | doaj.art-aff13d8af04f4ef3875978b3e83fb3512023-09-03T03:12:08ZengMDPI AGMedicina1010-660X2020-12-015669669610.3390/medicina56120696Obstruction of the Hepatic Venous Flow Caused by Intravenous LeiomyomatosisSin-Youl Park0In Hwan Yeo1Yun Jeong Kim2Jong Kun Kim3Department of Emergency medicine, College of Medicine, Yeungnam University, Daegu 42415, KoreaDepartment of Emergency Medicine, Kyungpook National University School of Medicine, Daegu 41404, KoreaDepartment of Emergency Medicine, Kyungpook National University School of Medicine, Daegu 41404, KoreaDepartment of Emergency Medicine, Kyungpook National University School of Medicine, Daegu 41404, KoreaBudd–Chiari syndrome (BCS) is a rare intrahepatic vascular disease that is characterized by a hepatic venous outflow obstruction. Intravenous leiomyomatosis (ILs) is a rare complication of a myoma. Here, we report a case of BCS that was caused by intracaval ILs. A woman presented to the emergency department (ED) with abdominal distension that had gradually progressed over a period of 3 years. Bedside ultrasonography and contrast-enhanced computed tomography (CECT) showed a large ascites and pelvic mass. The mass continued to the inferior vena cava and the right atrium. The intracaval mass was obstructing the left and middle hepatic veins. We established a tentative diagnosis of BCS caused by intracaval ILs and attempted surgical resection. Complete resection of the intracaval mass failed because of adhesion; however, she was discharged from the hospital without any postoperative complications. After 3 months, a pelvic ultrasonography showed a recurrence of a 4 × 3 cm pelvic mass. The mass size increased to 6 cm after 30 months. ILs can cause secondary BCS and can lead to life-threatening conditions. Owing to its extreme rarity, early detection in the ED is challenging. Bedside ultrasonography and CECT can enable the early recognition of BCS by ILs.https://www.mdpi.com/1010-660X/56/12/696Budd–Chiari syndromeInferior vena cavaleiomyomaleiomyomatosisultrasonography |
| spellingShingle | Sin-Youl Park In Hwan Yeo Yun Jeong Kim Jong Kun Kim Obstruction of the Hepatic Venous Flow Caused by Intravenous Leiomyomatosis Medicina Budd–Chiari syndrome Inferior vena cava leiomyoma leiomyomatosis ultrasonography |
| title | Obstruction of the Hepatic Venous Flow Caused by Intravenous Leiomyomatosis |
| title_full | Obstruction of the Hepatic Venous Flow Caused by Intravenous Leiomyomatosis |
| title_fullStr | Obstruction of the Hepatic Venous Flow Caused by Intravenous Leiomyomatosis |
| title_full_unstemmed | Obstruction of the Hepatic Venous Flow Caused by Intravenous Leiomyomatosis |
| title_short | Obstruction of the Hepatic Venous Flow Caused by Intravenous Leiomyomatosis |
| title_sort | obstruction of the hepatic venous flow caused by intravenous leiomyomatosis |
| topic | Budd–Chiari syndrome Inferior vena cava leiomyoma leiomyomatosis ultrasonography |
| url | https://www.mdpi.com/1010-660X/56/12/696 |
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