Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis

Inflammatory myofibroblastic tumor is a neoplasm with uncertain behavior. We describe a case in a 66-year-old female who underwent resection of a left atrial tumor suspected to be a cardiac myxoma which was subsequently diagnosed as an inflammatory myofibroblastic tumor. After three years’ follow-up...

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প্রধান লেখক: Carlos Domínguez-Massa, Lucía Doñate-Bertolín, Óscar R. Blanco-Herrera, Tomás Heredia-Cambra, Manuel Pérez-Guillén, Vicent Martínez-Cózar, Empar Mayordomo-Aranda, Fernando Hornero-Sos
বিন্যাস: প্রবন্ধ
ভাষা:English
প্রকাশিত: Elsevier 2023-02-01
মালা:Revista Portuguesa de Cardiologia
বিষয়গুলি:
অনলাইন ব্যবহার করুন:http://www.sciencedirect.com/science/article/pii/S087025512200525X
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author Carlos Domínguez-Massa
Lucía Doñate-Bertolín
Óscar R. Blanco-Herrera
Tomás Heredia-Cambra
Manuel Pérez-Guillén
Vicent Martínez-Cózar
Empar Mayordomo-Aranda
Fernando Hornero-Sos
author_facet Carlos Domínguez-Massa
Lucía Doñate-Bertolín
Óscar R. Blanco-Herrera
Tomás Heredia-Cambra
Manuel Pérez-Guillén
Vicent Martínez-Cózar
Empar Mayordomo-Aranda
Fernando Hornero-Sos
author_sort Carlos Domínguez-Massa
collection DOAJ
description Inflammatory myofibroblastic tumor is a neoplasm with uncertain behavior. We describe a case in a 66-year-old female who underwent resection of a left atrial tumor suspected to be a cardiac myxoma which was subsequently diagnosed as an inflammatory myofibroblastic tumor. After three years’ follow-up the patient underwent a second operation to remove tumoral occurrence in the right atrium, diagnosed as an intimal sarcoma. It cannot be confirmed whether the tumoral recurrence with a different diagnosis (intimal sarcoma) was a progression from the primary tumor or the metachronous appearance of a spontaneous sarcoma. Resumo: O tumor miofibroblástico inflamatório é uma neoplasia de comportamento incerto. Descrevemos o caso clínico de uma mulher de 66 anos submetida à ressecção de uma massa tumoral na aurícula esquerda com suspeita de mixoma cardíaco, mas diagnosticada como tumor miofibroblástico inflamatório. Após três anos de seguimento, a doente foi operada pela segunda vez para ressecar um novo tumor na aurícula direita, diagnosticado como sarcoma intimal. A recidiva tumoral com um diagnóstico diferente de sarcoma intimal não pôde ser confirmada como progressão do primeiro tumor ou como aparência metacrônica de um sarcoma espontâneo.
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spelling doaj.art-aff64c2d54a34da0a219ea5f4edddb532023-02-09T04:13:36ZengElsevierRevista Portuguesa de Cardiologia0870-25512023-02-01422169.e1169.e4Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosisCarlos Domínguez-Massa0Lucía Doñate-Bertolín1Óscar R. Blanco-Herrera2Tomás Heredia-Cambra3Manuel Pérez-Guillén4Vicent Martínez-Cózar5Empar Mayordomo-Aranda6Fernando Hornero-Sos7Department of Cardiovascular Surgery, Hospital Universitario y Politécnico La Fe, Valencia, Spain; Corresponding author.Department of Cardiovascular Surgery, Hospital Universitario y Politécnico La Fe, Valencia, SpainDepartment of Cardiovascular Surgery, Hospital Universitario y Politécnico La Fe, Valencia, SpainDepartment of Cardiovascular Surgery, Hospital Universitario y Politécnico La Fe, Valencia, SpainDepartment of Cardiovascular Surgery, Hospital Universitario y Politécnico La Fe, Valencia, SpainDepartment of Pathology, Hospital Universitario y Politécnico La Fe, Valencia, SpainDepartment of Pathology, Hospital Universitario y Politécnico La Fe, Valencia, SpainDepartment of Cardiovascular Surgery, Hospital Universitario y Politécnico La Fe, Valencia, SpainInflammatory myofibroblastic tumor is a neoplasm with uncertain behavior. We describe a case in a 66-year-old female who underwent resection of a left atrial tumor suspected to be a cardiac myxoma which was subsequently diagnosed as an inflammatory myofibroblastic tumor. After three years’ follow-up the patient underwent a second operation to remove tumoral occurrence in the right atrium, diagnosed as an intimal sarcoma. It cannot be confirmed whether the tumoral recurrence with a different diagnosis (intimal sarcoma) was a progression from the primary tumor or the metachronous appearance of a spontaneous sarcoma. Resumo: O tumor miofibroblástico inflamatório é uma neoplasia de comportamento incerto. Descrevemos o caso clínico de uma mulher de 66 anos submetida à ressecção de uma massa tumoral na aurícula esquerda com suspeita de mixoma cardíaco, mas diagnosticada como tumor miofibroblástico inflamatório. Após três anos de seguimento, a doente foi operada pela segunda vez para ressecar um novo tumor na aurícula direita, diagnosticado como sarcoma intimal. A recidiva tumoral com um diagnóstico diferente de sarcoma intimal não pôde ser confirmada como progressão do primeiro tumor ou como aparência metacrônica de um sarcoma espontâneo.http://www.sciencedirect.com/science/article/pii/S087025512200525XNeoplasias do coraçãoRecorrência neoplásicaDiagnóstico diferencial
spellingShingle Carlos Domínguez-Massa
Lucía Doñate-Bertolín
Óscar R. Blanco-Herrera
Tomás Heredia-Cambra
Manuel Pérez-Guillén
Vicent Martínez-Cózar
Empar Mayordomo-Aranda
Fernando Hornero-Sos
Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis
Revista Portuguesa de Cardiologia
Neoplasias do coração
Recorrência neoplásica
Diagnóstico diferencial
title Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis
title_full Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis
title_fullStr Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis
title_full_unstemmed Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis
title_short Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis
title_sort inflammatory myofibroblastic tumor a rare entity with a complex diagnosis
topic Neoplasias do coração
Recorrência neoplásica
Diagnóstico diferencial
url http://www.sciencedirect.com/science/article/pii/S087025512200525X
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