Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis
Inflammatory myofibroblastic tumor is a neoplasm with uncertain behavior. We describe a case in a 66-year-old female who underwent resection of a left atrial tumor suspected to be a cardiac myxoma which was subsequently diagnosed as an inflammatory myofibroblastic tumor. After three years’ follow-up...
প্রধান লেখক: | , , , , , , , |
---|---|
বিন্যাস: | প্রবন্ধ |
ভাষা: | English |
প্রকাশিত: |
Elsevier
2023-02-01
|
মালা: | Revista Portuguesa de Cardiologia |
বিষয়গুলি: | |
অনলাইন ব্যবহার করুন: | http://www.sciencedirect.com/science/article/pii/S087025512200525X |
_version_ | 1828038446680113152 |
---|---|
author | Carlos Domínguez-Massa Lucía Doñate-Bertolín Óscar R. Blanco-Herrera Tomás Heredia-Cambra Manuel Pérez-Guillén Vicent Martínez-Cózar Empar Mayordomo-Aranda Fernando Hornero-Sos |
author_facet | Carlos Domínguez-Massa Lucía Doñate-Bertolín Óscar R. Blanco-Herrera Tomás Heredia-Cambra Manuel Pérez-Guillén Vicent Martínez-Cózar Empar Mayordomo-Aranda Fernando Hornero-Sos |
author_sort | Carlos Domínguez-Massa |
collection | DOAJ |
description | Inflammatory myofibroblastic tumor is a neoplasm with uncertain behavior. We describe a case in a 66-year-old female who underwent resection of a left atrial tumor suspected to be a cardiac myxoma which was subsequently diagnosed as an inflammatory myofibroblastic tumor. After three years’ follow-up the patient underwent a second operation to remove tumoral occurrence in the right atrium, diagnosed as an intimal sarcoma. It cannot be confirmed whether the tumoral recurrence with a different diagnosis (intimal sarcoma) was a progression from the primary tumor or the metachronous appearance of a spontaneous sarcoma. Resumo: O tumor miofibroblástico inflamatório é uma neoplasia de comportamento incerto. Descrevemos o caso clínico de uma mulher de 66 anos submetida à ressecção de uma massa tumoral na aurícula esquerda com suspeita de mixoma cardíaco, mas diagnosticada como tumor miofibroblástico inflamatório. Após três anos de seguimento, a doente foi operada pela segunda vez para ressecar um novo tumor na aurícula direita, diagnosticado como sarcoma intimal. A recidiva tumoral com um diagnóstico diferente de sarcoma intimal não pôde ser confirmada como progressão do primeiro tumor ou como aparência metacrônica de um sarcoma espontâneo. |
first_indexed | 2024-04-10T16:27:12Z |
format | Article |
id | doaj.art-aff64c2d54a34da0a219ea5f4edddb53 |
institution | Directory Open Access Journal |
issn | 0870-2551 |
language | English |
last_indexed | 2024-04-10T16:27:12Z |
publishDate | 2023-02-01 |
publisher | Elsevier |
record_format | Article |
series | Revista Portuguesa de Cardiologia |
spelling | doaj.art-aff64c2d54a34da0a219ea5f4edddb532023-02-09T04:13:36ZengElsevierRevista Portuguesa de Cardiologia0870-25512023-02-01422169.e1169.e4Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosisCarlos Domínguez-Massa0Lucía Doñate-Bertolín1Óscar R. Blanco-Herrera2Tomás Heredia-Cambra3Manuel Pérez-Guillén4Vicent Martínez-Cózar5Empar Mayordomo-Aranda6Fernando Hornero-Sos7Department of Cardiovascular Surgery, Hospital Universitario y Politécnico La Fe, Valencia, Spain; Corresponding author.Department of Cardiovascular Surgery, Hospital Universitario y Politécnico La Fe, Valencia, SpainDepartment of Cardiovascular Surgery, Hospital Universitario y Politécnico La Fe, Valencia, SpainDepartment of Cardiovascular Surgery, Hospital Universitario y Politécnico La Fe, Valencia, SpainDepartment of Cardiovascular Surgery, Hospital Universitario y Politécnico La Fe, Valencia, SpainDepartment of Pathology, Hospital Universitario y Politécnico La Fe, Valencia, SpainDepartment of Pathology, Hospital Universitario y Politécnico La Fe, Valencia, SpainDepartment of Cardiovascular Surgery, Hospital Universitario y Politécnico La Fe, Valencia, SpainInflammatory myofibroblastic tumor is a neoplasm with uncertain behavior. We describe a case in a 66-year-old female who underwent resection of a left atrial tumor suspected to be a cardiac myxoma which was subsequently diagnosed as an inflammatory myofibroblastic tumor. After three years’ follow-up the patient underwent a second operation to remove tumoral occurrence in the right atrium, diagnosed as an intimal sarcoma. It cannot be confirmed whether the tumoral recurrence with a different diagnosis (intimal sarcoma) was a progression from the primary tumor or the metachronous appearance of a spontaneous sarcoma. Resumo: O tumor miofibroblástico inflamatório é uma neoplasia de comportamento incerto. Descrevemos o caso clínico de uma mulher de 66 anos submetida à ressecção de uma massa tumoral na aurícula esquerda com suspeita de mixoma cardíaco, mas diagnosticada como tumor miofibroblástico inflamatório. Após três anos de seguimento, a doente foi operada pela segunda vez para ressecar um novo tumor na aurícula direita, diagnosticado como sarcoma intimal. A recidiva tumoral com um diagnóstico diferente de sarcoma intimal não pôde ser confirmada como progressão do primeiro tumor ou como aparência metacrônica de um sarcoma espontâneo.http://www.sciencedirect.com/science/article/pii/S087025512200525XNeoplasias do coraçãoRecorrência neoplásicaDiagnóstico diferencial |
spellingShingle | Carlos Domínguez-Massa Lucía Doñate-Bertolín Óscar R. Blanco-Herrera Tomás Heredia-Cambra Manuel Pérez-Guillén Vicent Martínez-Cózar Empar Mayordomo-Aranda Fernando Hornero-Sos Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis Revista Portuguesa de Cardiologia Neoplasias do coração Recorrência neoplásica Diagnóstico diferencial |
title | Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis |
title_full | Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis |
title_fullStr | Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis |
title_full_unstemmed | Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis |
title_short | Inflammatory myofibroblastic tumor: A rare entity with a complex diagnosis |
title_sort | inflammatory myofibroblastic tumor a rare entity with a complex diagnosis |
topic | Neoplasias do coração Recorrência neoplásica Diagnóstico diferencial |
url | http://www.sciencedirect.com/science/article/pii/S087025512200525X |
work_keys_str_mv | AT carlosdominguezmassa inflammatorymyofibroblastictumorarareentitywithacomplexdiagnosis AT luciadonatebertolin inflammatorymyofibroblastictumorarareentitywithacomplexdiagnosis AT oscarrblancoherrera inflammatorymyofibroblastictumorarareentitywithacomplexdiagnosis AT tomasherediacambra inflammatorymyofibroblastictumorarareentitywithacomplexdiagnosis AT manuelperezguillen inflammatorymyofibroblastictumorarareentitywithacomplexdiagnosis AT vicentmartinezcozar inflammatorymyofibroblastictumorarareentitywithacomplexdiagnosis AT emparmayordomoaranda inflammatorymyofibroblastictumorarareentitywithacomplexdiagnosis AT fernandohornerosos inflammatorymyofibroblastictumorarareentitywithacomplexdiagnosis |