Multiple complications of advanced IPF in an individual patient presentation
Abstract We report a patient with advanced idiopathic pulmonary fibrosis (IPF), who in a single presentation experienced three complications of the disease: an acute exacerbation, spontaneous pneumomediastinum, and platypnoea‐orthodeoxia syndrome. Despite there being no definitive evidence‐based tre...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
| Published: |
Wiley
2023-04-01
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| Series: | Respirology Case Reports |
| Subjects: | |
| Online Access: | https://doi.org/10.1002/rcr2.1118 |
| Summary: | Abstract We report a patient with advanced idiopathic pulmonary fibrosis (IPF), who in a single presentation experienced three complications of the disease: an acute exacerbation, spontaneous pneumomediastinum, and platypnoea‐orthodeoxia syndrome. Despite there being no definitive evidence‐based treatment for an acute exacerbation, we report a marked improvement with high‐dose steroids. This case also highlights the importance in IPF patients of considering pneumomediastinum as a cause of non‐cardiac chest pain, as well as platypnoea‐orthodeoxia in those with positional dyspnoea. |
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| ISSN: | 2051-3380 |