Multiple complications of advanced IPF in an individual patient presentation
Abstract We report a patient with advanced idiopathic pulmonary fibrosis (IPF), who in a single presentation experienced three complications of the disease: an acute exacerbation, spontaneous pneumomediastinum, and platypnoea‐orthodeoxia syndrome. Despite there being no definitive evidence‐based tre...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
| Published: |
Wiley
2023-04-01
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| Series: | Respirology Case Reports |
| Subjects: | |
| Online Access: | https://doi.org/10.1002/rcr2.1118 |
| _version_ | 1797857769136586752 |
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| author | Thomas Ledger Stanley Braude |
| author_facet | Thomas Ledger Stanley Braude |
| author_sort | Thomas Ledger |
| collection | DOAJ |
| description | Abstract We report a patient with advanced idiopathic pulmonary fibrosis (IPF), who in a single presentation experienced three complications of the disease: an acute exacerbation, spontaneous pneumomediastinum, and platypnoea‐orthodeoxia syndrome. Despite there being no definitive evidence‐based treatment for an acute exacerbation, we report a marked improvement with high‐dose steroids. This case also highlights the importance in IPF patients of considering pneumomediastinum as a cause of non‐cardiac chest pain, as well as platypnoea‐orthodeoxia in those with positional dyspnoea. |
| first_indexed | 2024-04-09T21:02:09Z |
| format | Article |
| id | doaj.art-b046a1896b784dde8830fb230c8b435b |
| institution | Directory Open Access Journal |
| issn | 2051-3380 |
| language | English |
| last_indexed | 2024-04-09T21:02:09Z |
| publishDate | 2023-04-01 |
| publisher | Wiley |
| record_format | Article |
| series | Respirology Case Reports |
| spelling | doaj.art-b046a1896b784dde8830fb230c8b435b2023-03-29T08:50:29ZengWileyRespirology Case Reports2051-33802023-04-01114n/an/a10.1002/rcr2.1118Multiple complications of advanced IPF in an individual patient presentationThomas Ledger0Stanley Braude1Department of Respiratory Medicine Northern Beaches Hospital Sydney New South Wales AustraliaDepartment of Respiratory Medicine Northern Beaches Hospital Sydney New South Wales AustraliaAbstract We report a patient with advanced idiopathic pulmonary fibrosis (IPF), who in a single presentation experienced three complications of the disease: an acute exacerbation, spontaneous pneumomediastinum, and platypnoea‐orthodeoxia syndrome. Despite there being no definitive evidence‐based treatment for an acute exacerbation, we report a marked improvement with high‐dose steroids. This case also highlights the importance in IPF patients of considering pneumomediastinum as a cause of non‐cardiac chest pain, as well as platypnoea‐orthodeoxia in those with positional dyspnoea.https://doi.org/10.1002/rcr2.1118acute exacerbation of idiopathic pulmonary fibrosisidiopathic pulmonary fibrosisplatypnoea‐orthodeoxia syndromepneumomediastinum |
| spellingShingle | Thomas Ledger Stanley Braude Multiple complications of advanced IPF in an individual patient presentation Respirology Case Reports acute exacerbation of idiopathic pulmonary fibrosis idiopathic pulmonary fibrosis platypnoea‐orthodeoxia syndrome pneumomediastinum |
| title | Multiple complications of advanced IPF in an individual patient presentation |
| title_full | Multiple complications of advanced IPF in an individual patient presentation |
| title_fullStr | Multiple complications of advanced IPF in an individual patient presentation |
| title_full_unstemmed | Multiple complications of advanced IPF in an individual patient presentation |
| title_short | Multiple complications of advanced IPF in an individual patient presentation |
| title_sort | multiple complications of advanced ipf in an individual patient presentation |
| topic | acute exacerbation of idiopathic pulmonary fibrosis idiopathic pulmonary fibrosis platypnoea‐orthodeoxia syndrome pneumomediastinum |
| url | https://doi.org/10.1002/rcr2.1118 |
| work_keys_str_mv | AT thomasledger multiplecomplicationsofadvancedipfinanindividualpatientpresentation AT stanleybraude multiplecomplicationsofadvancedipfinanindividualpatientpresentation |