Rosai-Dorfman disease of the oral cavity
First described by J Rosai and R F Dorfman in 1969, Rosai-Dorfman disease (RDD) is a benign, self-limiting histiocytosis of unknown etiology. It is usually seen in the first two decades of life. The most frequent clinical presentation is painless, bilateral cervical lymphadenopathy accompanied by f...
| Main Authors: | , , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
University of São Paulo
2023-12-01
|
| Series: | Autopsy and Case Reports |
| Subjects: | |
| Online Access: | https://www.revistas.usp.br/autopsy/article/view/219697 |
| _version_ | 1827595076115628032 |
|---|---|
| author | Abir Charfeddine Mounir Omami Marwa Garma Ahlem Bellalah Sameh Sioud Jamil Selmi |
| author_facet | Abir Charfeddine Mounir Omami Marwa Garma Ahlem Bellalah Sameh Sioud Jamil Selmi |
| author_sort | Abir Charfeddine |
| collection | DOAJ |
| description |
First described by J Rosai and R F Dorfman in 1969, Rosai-Dorfman disease (RDD) is a benign, self-limiting histiocytosis of unknown etiology. It is usually seen in the first two decades of life. The most frequent clinical presentation is painless, bilateral cervical lymphadenopathy accompanied by fever, weight loss, and an elevated ESR. However, RDD without nodal involvement is extremely rare, and the most common extranodal location is the head and neck region, mainly affecting the nasal cavity, pharynx, and paranasal sinuses. Oral location of RDD is occasional; according to our knowledge, only 17 cases of oral Rosai-Dorfman disease without lymph node involvement have been found in the literature. Because of the rarity of these isolated oral presentations, the clinical and radiological aspects need to be more studied. This article aims to present a rare case of oral Rosai-Dorfman disease without nodal involvement, detail the clinical and radiological signs, and the treatment strategy used in our patient.
|
| first_indexed | 2024-03-09T02:46:33Z |
| format | Article |
| id | doaj.art-b07419b23f6942d0931803b34002f310 |
| institution | Directory Open Access Journal |
| issn | 2236-1960 |
| language | English |
| last_indexed | 2024-03-09T02:46:33Z |
| publishDate | 2023-12-01 |
| publisher | University of São Paulo |
| record_format | Article |
| series | Autopsy and Case Reports |
| spelling | doaj.art-b07419b23f6942d0931803b34002f3102023-12-05T16:13:38ZengUniversity of São PauloAutopsy and Case Reports2236-19602023-12-0113Rosai-Dorfman disease of the oral cavityAbir Charfeddine0 Mounir Omami1Marwa Garma2Ahlem Bellalah3Sameh Sioud4Jamil Selmi5University Clinic of Dental Medicine, Oral Surgery Department, Oral Medicine, Monastir, TunisiaUniversity Clinic of Dental Medicine, Oral Surgery Department, Oral Medicine, Monastir, TunisiaUniversity Clinic of Dental Medicine, Oral Surgery Department, Oral Medicine, Monastir, TunisiaFattouma Bourguiba University Hospital, Anatomical Pathology and Cytology Department, Monastir, TunisiaUniversity Clinic of Dental Medicine, Oral Surgery Department, Oral Medicine, Monastir, TunisiaUniversity Clinic of Dental Medicine, Oral Surgery Department, Oral Medicine, Monastir, Tunisia First described by J Rosai and R F Dorfman in 1969, Rosai-Dorfman disease (RDD) is a benign, self-limiting histiocytosis of unknown etiology. It is usually seen in the first two decades of life. The most frequent clinical presentation is painless, bilateral cervical lymphadenopathy accompanied by fever, weight loss, and an elevated ESR. However, RDD without nodal involvement is extremely rare, and the most common extranodal location is the head and neck region, mainly affecting the nasal cavity, pharynx, and paranasal sinuses. Oral location of RDD is occasional; according to our knowledge, only 17 cases of oral Rosai-Dorfman disease without lymph node involvement have been found in the literature. Because of the rarity of these isolated oral presentations, the clinical and radiological aspects need to be more studied. This article aims to present a rare case of oral Rosai-Dorfman disease without nodal involvement, detail the clinical and radiological signs, and the treatment strategy used in our patient. https://www.revistas.usp.br/autopsy/article/view/219697EmperipolesisHistiocytosis, SinusLymph NodesMaxilla |
| spellingShingle | Abir Charfeddine Mounir Omami Marwa Garma Ahlem Bellalah Sameh Sioud Jamil Selmi Rosai-Dorfman disease of the oral cavity Autopsy and Case Reports Emperipolesis Histiocytosis, Sinus Lymph Nodes Maxilla |
| title | Rosai-Dorfman disease of the oral cavity |
| title_full | Rosai-Dorfman disease of the oral cavity |
| title_fullStr | Rosai-Dorfman disease of the oral cavity |
| title_full_unstemmed | Rosai-Dorfman disease of the oral cavity |
| title_short | Rosai-Dorfman disease of the oral cavity |
| title_sort | rosai dorfman disease of the oral cavity |
| topic | Emperipolesis Histiocytosis, Sinus Lymph Nodes Maxilla |
| url | https://www.revistas.usp.br/autopsy/article/view/219697 |
| work_keys_str_mv | AT abircharfeddine rosaidorfmandiseaseoftheoralcavity AT mouniromami rosaidorfmandiseaseoftheoralcavity AT marwagarma rosaidorfmandiseaseoftheoralcavity AT ahlembellalah rosaidorfmandiseaseoftheoralcavity AT samehsioud rosaidorfmandiseaseoftheoralcavity AT jamilselmi rosaidorfmandiseaseoftheoralcavity |